Mixed Cellularity Hodgkin Lymphoma

Zviratidzo, Zvinokonzera, uye Zvirwere Mixed Cellularity Classic Hodgkin Disease

Ndezvipi zvakasanganiswa nemafuta Hodgkin lymphoma, zvakasviba zvakadini, chii chinokonzera, uye chinoshandiswa sei?

Overview

Mixed cellularity Hodgkin's lymphoma chirwere cheHodgkin chirwere , kenza yemarikisi masero. Iyo ndiyo yechipiri inowanzosiyana nehutachiona hweHodgkin , uye anenge 15 kusvika ku30 muzana yevanhu vose vanotambura neHodgkin lymphoma munyika yekumadokero vane rudzi urwu.

Nhamba yevarwere vane rudzi urwu rweHodgkin yakakwirira kune dzimwe nzvimbo dzenyika kunze kweUnited States, kusanganisira Asia. Mune dzimwe nzvimbo, ndiyo inowanzosiyana neHodgkin lymphoma.

Mamiriro

Mixed cellularity Hodgkin inogona kuitika panguva ipi zvayo, kunyange iri yakajairika kune vanhu vakuru pakati pemakore 55 ne74, pamwe nevana vari pasi pezera remakore 14. Izvo zvakafananawo kune varume nevakadzi. Mutengo werudzi urwu lymphoma unoratidzika kuti wakaderera mumatambudziko pakati pa1992 na2011, asi izvi zvingave zvichienderana nenzira iyo lymphomas inorondedzerwa panzvimbo yekuderera kwechokwadi muzviitiko.

Izvo zvinowanzoonekwa kune vanhu vane maitiro ezvirwere zvekuzvidzivirira ari kushanda zvisina kunaka, somuenzaniso, kune vanhu vane HIV.

Zvinokonzera

Hazvizivikanwe chinokonzera chirwere cheHodgkin , kunyange zvazvo zvimwe zvinhu zvinowanzoisa njodzi. Nekavhenganiswa nemhando yerudzi rwemarimine lymphoma pane zviitiko zvakanyanya zveEppstein-Barr zviripo mumasero ekenza, asi masayendisiti vasati vava nechokwadi cheukama chaiyo pakati pemakirini uye chirwere ichi chinokonzera kutapukisa mononucleosis.

Zviratidzo

Zviratidzo zvemasanganiswa ehutachiona hwechirwere zvinowedzera lymph nodes mumutsipa, makumbo uye mudumbu.

Zvimwe nhengo dzisingakwanisi kubatanidzwa nemhando iyi ye lymphoma kupfuura dzimwe mhando dze lymphoma. Nehutachiona hwehutachiona hutatu 30 muzana yevanhu vanobatanidzwa nepleen yavo, 10 muzana yavo bone marora, 3 muzana yavo chiropa, uye chete 1 kusvika ku3 muzana yevanhu vanobatanidzwa kune dzimwe nhengo.

Kuziva

Kuongororwa kwe lymphoma kunoitwa ne lymph node biopsy .

Kurapa

Vanhu vazhinji vane lymphoma iyi vanoonekwa kuti vane chirwere chepamusoro, chinosanganisira lymph nodes kumativi ose ari kumusoro kwemuviri uye mudumbu.

Kune vanhu vane chirwere chekutanga , chirwere chinowanzobatanidza kusanganiswa kwemakemikrasi uye remishonga inonzi radiation.

Nechirwere chepamusoro , chirwere chinowanzomirira chemotherapy kwenguva yakareba, uye hazvikwanisi kusanganisira kushandiswa kwemishonga inonzi radiation. Chemotherapy zvinyorwa zvinokurukurwa munyaya ino pamusoro pokurapa kweHodgkin lymphoma .

Kune avo vanodzokorora zvakare musanganiswa wesero Hodgkin lymphoma, kana kana kutanga kurapwa kuchikundikana, pane zvimwe zvingasarudzwa. Chimwe ndechokushandisa salvage chemotherapy (chemotherapy inoshandiswa kuderedza kuwanda kwechirwere asi kwete kuporesa kenza) inoteverwa nepamusoro-kati chemotherapy uye autologous stem cell transplant. Zvimwe zvingasarudzwa zvinogona kusanganisira kushandiswa kwe monoclonal antibody Blincyto (brentuximab, ) immunotherapy ne checkpoint inhibitor, a nonmyeloablative stem cell transplant, kana kliniki yekuedzwa.

Prognosis

Kunyange zvazvo yakavhenganiswa nemafuta Hodgkin lymphoma chirwere chinotyisa, kufungidzira kwakanaka chaizvo . Izvo zvakafanana zvakafanana nevanhu vane nodular sclerosing Hodgkin lymphoma , uye zviri nani kudarika vanhu vane lymphocyte kuparadza Hodgkin chirwere.

Kutsungirira

Hazvina mhosva kuti kufungidzira, kunotyisa kuonekwa nekenza, Mukuwedzera kune izvozvo, kurapwa kwekuisa rudzi urwu rweHodgkin chirwere mukuregererwa kunogona kunge kwakaoma zvikuru uye kukwereta, uye tiri kudzidza kuti kudzvinyirira haisi pfungwa yakanaka yevanhu vane lymphomas . Svika kumhuri neshamwari. Funga kubatana neboka rinotsigira munharaunda yako kana paIndaneti. Uye chengetedza mazano aya ekurwisana ne lymphoma

Sources:

Ansell, S. Hodgkin Lymphoma: Kuziva nekurapa. Mayo Clinic Proceedings . 2015. 90 (11): 1574-83.

Bienemann, K., Borkhardt, A., Klapper, W., uye I. Oschies. Nzvimbo yakakwirira ye Epstein-Barr virus (EBV) -iyo inofadza Hodgkin lymphoma uye Hodgkin lymphoma-yakadai se-B-cell marapiritsiro neEBV latency profile 2 muvana vane interleukin-2-inducible T-cell kinase inoshaya. Histopathology . 2015. 67 (5): 607-16.

Kanzira: Mazano uye Maitiro eOnology 7th Edition. Vakuru: VT DeVita, S Hellman uye SA Rosenberg. Yakabudiswa naLippincott Williams naWilkins, 2005.

Glaser, S., Clarke, C., Keegan, T., Shanduko, E., uye D. Weisenburger. Nguva Inotenderera muHatari yeHodgkin Lymphoma Histologic Subtypes: Kuitika Kwechokwadi Kuchinja kana Kuvandudza Maitiro Okuongorora? Cancer Epidemiology Biomarkers uye Kudzivirira . 2015. 24 (10): 1474-88.

National Cancer Institute. Kuongororwa, Epidemiology, uye Kuguma Zvabuda Purogiramu. Mixed cellularity classic Hodgkin lymphoma. Yakasvika 02/11/16. http://seer.cancer.gov/seertools/hemelymph/51f6cf57e3e27c3994bd5342/