Rimwe Rakagara Rakagadzikana Dambudziko Rinokonzera Matambudziko Okuputika
Kartagener syndrome, chirwere chisingawanzobereki chizvarwa chinokonzerwa nekuremara kwemajeni . Icho chinyorwa chekuzvidzivirira , zvinoreva kuti zvinongoitika chete kana vabereki vose vakatakura geni. Kartagener syndrome inokanganisa vanhu vanenge 30 000, kusanganisira vakomana.
Iyo inozivikanwa nokuda kwezvinhu zviviri zvisingakanganisi zvikuru: primary ciliary dyskinesia uye inversus inogara.
Ciliary Dyskinesia
Iyo nzira yekupumadza inosanganisira mhino, sinus, nzeve yepakati, eustachian tubes , huro, uye kufema tubes ( trachea , bronchi , uye bronchioles ). Iyo yose iyo yakagadzirwa nemasero anokosha ane maitiro akafanana nevhudzi pamusoro pavo, anonzi cilia. Iyo cilia inopisa inopinza makomikoro eguruva, utsi, uye mabhakitiriya kumusoro uye kunze kwegwara rekupema.
Mumamiriro ekutanga ciliary dyskinesia ane kartagener syndrome, cilia haina kukwana uye haishande zvakanaka. Izvi zvinoreva kuti masikiti uye mabhakitiriya mumapapu haakwanisi kudzingwa, uye semugumisiro, nguva dzose zvirwere zvepapu, zvakadai sepineumonia, inobudirira.
Cilia inowanikwawo mumhepo yeuropi uye muhutano hwekubereka. Vanhu vane Kartagener syndrome vanogona kuva nemusoro uye matambudziko nekubereka.
Situs Inversus
Situs inversus inoitika apo fetus iri mudumbu. Inokonzera nhengo kuti dzikure pane rumwe rutivi rwakashata rwemuviri, kushandura chimiro chakanaka.
Mune zvimwe zviitiko, nhengo dzose dzinogona kuva chiratidziro chegiratiro chekugara muchigaro, asi mune dzimwe nguva, nhengo dzomumwechete dzinoshandiswa.
Zviratidzo
Zvizhinji zvezviratidzo zveKartagener Syndrome zvinokonzerwa nokusakwanisa kwekupempa cilia kushanda zvakanaka, zvakadai se:
- Chirwere chechirwere chisingaperi
- Vanowanzopora maperembudzi, zvakadai sepneumonia uye bronchitis
- Bronchiectasis - kukanganisa kwemapapu kubva kune dzimwe nguva zvirwere
- Kakawanda kunzwa nzeve
Chiratidzo chinokosha chinosiyanisa Kartagener syndrome kubva kune dzimwe mhando dzepamusoro ciliary dyskinesia kuiswa kwezvikamu zvemukati kune rumwe rutivi rwakatarisana nechekare (inonzi instus inversus). Somuenzaniso, mwoyo uri kurudyi rwebhokisi pane kuruboshwe.
Kuziva
Kartagener syndrome inozivikanwa nezviratidzo zvitatu zvikuru zvechirwere sinusitis, bronchiectasis uye inversus. Bofu x-rays kana kuti computed tomography (CT) zvinotaridzika zvinogona kuona kuchinja kwemapapu zvinoratidza zvechirwere. Kutora biopsy yedanda re trachea, mapapu kana zvitema zvinogona kubvumira kuongororwa kwemasero emasero anokonzera nzira yekufema, iyo inogona kuona kusakosha cilia.
Kurapa
Kuchengetedzwa kwechiremba kune munhu ane Kartagener syndrome inotarisa kudzivirira kwezvirwere zvekufema uye nokukurumidza kurapwa kwezvingazoitika. Mishonga inorwisa mabhakitiriya inogona kubvisa sinusitis, uye kuvhara mishonga uye kurapa kupora kunogona kubatsira kana chirwere chisingaperi chemapapu chinowedzera. Zviduku zviduku zvinogona kuiswa kuburikidza neeardrums kubvumira kutapukisa uye mvura inonaya ichibuda mukati mekunze. Vakuru, kunyanya varume, vangave vakaomerwa nekubereka uye vanogona kubatsirwa nekutsvaga kune nyanzvi yekubereka. Mumiedzo yakakomba, vamwe vanhu vanogona kuda kutora mapapu akazara.
Muvanhu vakawanda, nhamba yehutachiona hwekutapukira inotanga kuderera neanenge makore makumi maviri, uye somugumisiro, vanhu vakawanda vane Kartagener syndrome vava pedyo nekugara vanhu vakuru.
Kunobva:
"Chii Chinokosha Ciliary Dyskinesia?" PCD Foundation . 24 Nov 2008
Rice, S. "Kartagener Syndrome". Healthline , 2013.