Stevens-Johnson Syndrome (SJS) isati iripo asi inogona kunge iri kutyisa upenyu hweganda mukati mekunze kweganda (epidermis) inoparadzanisa kubva pakadzika pakati pe (dermis) epidermis, zvichiita kuti munhu ave nekukurumidza kufa.
Kunyange zvazvo SJS inogona kukonzerwa nehuwandu hwehutachiona, kusanganisira mumps uye typhoid, ivo vanowanzobatanidzwa nehutachiona hwehutachiona.
Hypersensitivity inowanikwa apo kubuda kune imwe mishonga inokonzera mhinduro dzisina kukwana dzomuviri umo muviri unoshungurudza mawo masero nemasukisi.
Mimwe mishonga inorwisa mabhakitiriya inoshandiswa kurapa HIV inobatanidzwa nehuwandu hwehuwandu hweSJS kusanganisira Viramune (nevirapine), Ziagen (abacavir), uye Isentress (raltegravir).
Mishonga inorwisa mabhakitiriya, zvikurukuru sulfa mishonga, inowanzobatanidzwa mune zviitiko zveSJS. Kutaura zvazviri, kushandiswa kweripampin ye anti-tuberculosis kunogona kuwedzera ngozi ye SJS kune vanhu vane HIV nevanenge 400 muzana.
Zviratidzo
SJS inowanzotanga nezviratidzo zvinyoro zvakadai sekuneta zvakakwana, fever, uye kurwadziwa kwehuro. Izvi zvinowanzoteverwa nekutaridzika kwezvipembenene zvinorwadza pamusoro pemakumbo emumuromo wemiromo, miromo, rurimi, uye mawere emukati (uye pane dzimwe nguva anus uye marudzi). Iyo inogonawo kusanganisira zvikamu zvakakura zvechiso, trunk, migumo, uye netsoka dzemakumbo, kuratidzira ne blisters yeanenge inch in size.
Zviratidzo zvinowanzoonekwa mukati memavhiki maviri ekutanga kutanga chirongwa chitsva. Kana isina kusiyiwa uye mishonga isati yamira, mungozi yomuviri inogona kuitika uye inotungamirira kukuvadzwa kweziso, kupofu, kana kunyange rufu. Sepsis , kufambira mberi nokukurumidza, hupenyu hunotyisa, hunogona kuguma apo mabhakitiriya anobva muhutachiona hweSJS anopinda muropa uye anopararira mumuviri wose, zvichikonzera kushungurudzwa kunotyisa uye kusakundika kwechimiro.
SJS dzimwe nguva inokanganiswa neyerythema multiforme, chirwere chemishonga inoratidzira inoratidzika nekusimudza, piniki kana kuti tsvuku tsvuku. SJS, nenzira yakasiyana, inosanganiswa nekuputika kwemvura kunogona kuwirirana kugadzira mahwendefa makuru eganda rakasvibiswa. Kunyange mukutanga kwekutaura, vanachiremba vakawanda vachatsanangura SJS inoshandura se "kutsamwa" nekuda kwekuonekwa kwavo kunorwadza, kunopisa.
Kurapa
Kuregererwa kwekufungidzirwa kwechirwere ichi ndicho chinhu chekutanga kana SJS ichifungidzirwa. Muzviitiko zvakakomba, kurapwa kweSJS kwakafanana neyayo kune varwere vane kupisa kwakakomba, kusanganisira kuchengetedzwa kwemvura, kushandiswa kwekusagadzikana, kushandiswa kwekushisa, uye kurapa kunotsigira kupedza kurwadziwa nekudya.
Kana imwe nguva mushonga wakamira nekuda kweSJS, haifaniri kutongotangazve
Njodzi
Kunyange zvazvo SJS inogona kukanganisa chero ani zvake, pane vamwe vanoita sokuti vanofanirwa kugadziriswa kusvika pamamiriro ezvinhu. Kutsvakurudza kunoratidza kuti vanhu vane geni HLA-B 1502 vanowanzogadzirisa kukura SJS nehuwandu huwandu hwehuwandu hunoonekwa pakati pevanhu veChina, Indian, uye South East Asia vanobva.
Pamusoro pemishonga yakanyorwa pamusoro apa, mishonga yakawanda inowanzonzi yakanyorerwa inobatanidzwawo kune SJS. Dzinosanganisira:
- Nonsteroidal anti-inflammatory drugs (NSAIDs) zvakadai seacetaminophen, ibuprofen, uye sodium naproxen
- Penicillin
- Anti-gout mishonga yakadai seallopurinol
- Anticonvulsants vaishandiswa kurapa kamufa
- Antipsychotics vanoshandisa kurapa zvirwere zvepfungwa
- Radiation therapy
> Sources:
> Knight, L .; Muloiwa, R .; Dlamini, S. et al. "Zviitiko Zvinosanganiswa Nokuwedzera Kufa Munharaunda Inonyanya Kubatwa neHIV neStevens-Johnson Syndrome uye Toxic Epidermal Necrolysis." PLoS ONE. 2014; 9 (4): e93543. DOI: 10.1371 / magazini.pone.0093543.
> Dhipatimendi reUnited Health of Health and Human Services (DHHS). "Mirayiridzo yeKushandiswa kweAntiretroviral Agents muHIV-1-Vakaberekwa Vakuru Nevana Vari Kuyaruka: Kukanganisa Kurapa uye Kuchengeteka - Maitiro Akaipa Emishonga Inorwisa Maitiro Anotapukisa Utachiona." Washington, DC; yakasvika muna June 7, 2015.