Pakati pekuongorora kwemakore ekuberekwa kwemwana wako, hazvisi zvisizvo kuti vana vako vekuda vana vatumire ropa rakazara (CBC) . Iyi CBC inoshandiswa kuratidzira kushayikwa kwesimbi kusagadzikana sevana sekushandura kubva mukaka wamazamu kana mazai kusvika mukaka wose. Iwe unogona kushamiswa apo hofisi yevana vako yakadana kukuudza kuti mwana wako haasi chirwere chepachiremera asi kuti ropa ravo rega rega rega, kunyanya mabhakitiriya anorwisa masero anonzi neutrophils, akaderera.
Panguva ino, iwe unganzwa uchitya zvishoma uye unetseka kuti chii chakaipa.
Nenzira yakanaka, chikonzero chinowanzovhiringidza neutropenia (pasi neutrophil kuverengeka) kune vana chirwere chetachiona. Munguva yehutachiona hwehutachiwana, kubudiswa kweeutrophils kunoderedzwa, izvo zvingaguma neutropenia. Kana hutachiona hwachoka, nhamba ye neutrophil inodzokera kune yakajairika, saka chiremba wevana vako anogona kukurudzira kudzokorora CBC mumavhiki kana maviri. Kana iyo neutropenia ichiramba ichida, mwana wako anogona kutumirwa kune hematologist kuti aone chinokonzera neutropenia.
Chii Chinonzi chirwere Chekuita Neutropenia?
Chirwere chemoto autoimmune neutropenia chinogonawo kunzi chisingarapiki bhenign neutropenia yehuduku. Iyi mamiriro akafanana neaya immune thrombocytopenia (ITP) uye autoimmune hemolytic anemia (AIHA) . Pasinei nechokwadi chokuti marora emapfupa anoita kuti neutrophils zvive zvakanaka, muviri hauna kuita kuti zvirwere zvive neutrophils zvinoratidzirira kuparadzwa, zvichiita kuti neutropenia.
Chirwere chemoto autoimmune neutropenia inowanzopa mucheche 6 - 15 mwedzi yemakore asi inogona kuitika chero ipi zvayo, kunyange kuva munhu mukuru. Kuzvigadzirisa neutropenia pamwe chete neTP kana AIHA inonzi Evans Syndrome .
Zviratidzo
Vana vazhinji vane autoimmune neutropenia havana zviratidzo. Izvozvo ndechokuti, pasinei nehuwandu hwakanyanya pasi neutrophil kuverengwa, zvirwere zvakakomba hazviwanzoitiki.
Iyo neutropenia inogona kuwanika paCBC yakatangira kusvika kune nzeve kana kuputika kwehutachiona. Vamwe vana vangaona zvironda mumuromo kana zvirwere zveganda.
Kuziva
Sezvo nedzimwe maitiro e-neutropenia, yekutanga kuongororwa kwekuongorora ndiyo CBC. Mhedzisiro yakakwana yeutrophil (ANC) inowanikwa pasi pe1000 masero ne microliter uye inogona kuva pasi pe 500. Kazhinji, hemoglobin uye platelet yakawanda inowanikwa. A peripheral blood smear, kuongororwa kwemasero eropa pasi pekroscope, inogonawo kutorwa. Kunyange zvazvo nhamba yeeutrophils yakaderera, inenge yakaonekwa.
Zvadaro, chiremba wako angangowana maCBCs kaviri kwevhiki kwemavhiki masere matanhatu kuti ave nechokwadi chokuti mwana wako haana cyclic neutropenia (mamiriro apo neutrophils ari pasi pemazuva mashoma mazuva ose 21).
Chiremba wako angatumira kutengesa kuti aone kana kune ma antibodies kune neutrophils, achivaisa kubva pakuparadzwa. Kana iyi miedzo yakanaka, inosimbisa kuongororwa. Zvinosuruvarisa, kana kuedza kusina kunaka hakuiti kutora autoimmune neutropenia. Mune vamwe varwere, anti-neutrophil antibodies haatombozivikanwi. Muzviitiko izvi, kana nguva nehurukuro zvakagadzirisa mufananidzo we autoimmune neutropenia, kufungidzirwa kunofungidzirwa.
Muzviitiko zvisingawanzoitiki, kuongorora kwemafupa kunogona kudikanwa kutonga zvimwe zvinokonzera neutropenia. Izvi zvinowanzoitika kune vana vane mharidzo uye zvirwere zvisingakodzeri mufananidzo wezvirwere zvevanhu vanozvimirira neutropenia.
Kurapa
Hakuchina kurapa kwakanangana ne autoimmune neutropenia yehuduku. Ma anti-neutrophil antibodies achaparara pakarepo uye neutrophil nhamba ichadzoka kune yakajairika. Kuzvidzivirira kunowanzoitika kune makore mashanu, uye neutropenia inogara kwenguva yakareba kwemwedzi 20.
Nokuti neutropenia inowedzera njodzi yehutachiona, dzose fever dzinoda kurapwa kwechiremba.
Izvi zvinowanzobatwa neCBC, tsika yeropa (kuisa ropa muhombodo mabhodhoro kutsva mabhakitiriya), uye pamwe neyero imwe yemishonga inorwisa mabhakitiriya. Kana iyo ANC iri pasi pemasero mazana mashanu / mL, mwana wako angangozobvumirwa kupinda kuchipatara pamishonga inorwisa mabhakitiriya e IV. Kana mwana wako akatarisa zvakanaka uye ANC ikuru kune 1000 cell / mL, iwe uchave wakasunungurwa kumba kuti uite kunze kwekutevera.
Mishonga inoshandiswa kune dzimwe zvirwere zvehutachiona zvehutachiona (ITP, AIHA) steroids uye intravenous immune globulin (IVIG) haisi kubudirira mu autoimmune neutropenia. Dzimwe nguva filgrastim (G-CSF) inogona kushandiswa panguva dzehutachiona hunoshandiswa kuita kuti kusunungurwa kweeutrophils kubva mumuviri wemasora kusvika kuropa rega.
Sources
Coates TD. Immune neutropenia. MuchiTeDate, Post TW (Ed), UpToDate, Waltham, MA.