Kuongorora kwezviratidzo, kuongororwa, nekurapa
Tsanangudzo
Immune thrombocytopenia (ITP), yaimboti idiopathic thrombocytopenic purpura, ndiyo mamiriro apo masimba emumuviri wako anorwisa uye anoparadza maplatelet ako achikonzera pasi peplatelet zviyero ( thrombocytopenia ). Platelets inodiwa kuti ivhare ropa uye kana iwe usina chakanaka, unogona kubuda ropa.
Zviratidzo zveTP
Zviratidzo zveTP zvakabatana nehuwandu hwehutachiona hwekubuda ropa pamusana peplate platelet yako yakawanda.
Zvisinei, vanhu vazhinji vane ITP havana zviratidzo.
Nosebleeds
Kubvumira kubva mumadzimai
Ropa mumugini kana chigaro
Kuwedzerwa kudarika kumwedzi kunobuda ropa rinozivikanwa semamorrhagia
Petechiae - maduku maduku maduku matsvuku angangodaro akafanana nekuputika asi chaizvoizvo ari shoma rekubuda ropa pasi peganda
Kuramba kuputika - marwadzo angave makuru uye anokwanisa kunzwa pasi peganda
Ropa blister mukati memuromo unozivikanwa se purpura
Zvinokonzera ITP
Nenzira yakawanda, platelet yako yakawanda inodonha muItP nokuti muviri wako unogadzira zvirwere zvinosungirirana pama platelet uye zvinoratidzira kuti zviparadzwe. Apo maplatelet aya anotenderera kuburikidza nesimbi (nhengo muchero iyo inosvipa ropa), inobvuma ma antibodies aya uye inoparadza maplatelets. Uyewo kugadzirwa kweplatelets kunogona kuderedzwa. ITP inowanzotanga mushure mekuita chimwe chiitiko chinokurudzira, dzimwe nguva chiremba wako angasakwanise kuziva kuti chiitiko ichi chaiva chii.
Virusi: Muvana, ITP inowanzokonzerwa nehutachiona hwehutachiona. Utachiona hutachiona hunowanzoitika mavhiki mashomanana zvisati zvaitika kukura kweItP. Kunyange zvazvo zvirwere zvemuviri zvinokonzera zvirwere zvekurwisa zvirwere zvehutachiona zvinokonzerwa nehutachiona zvinoitawo zvirwere zvinosungirirana pama platelet.
Majekiseni: ITP yakabatanidzwa nekutungamirirwa kwemukoko weMMR (masero, mumps, rubella). Inowanzoitika mukati memavhiki matanhatu ekugamuchira chirwere. Zvakakosha kuziva kuti ichi ndicho chiitiko chisingashamisi uye 2.6 matambudziko emakwenzi ose emamiriyoni 100 000 anopiwa. Iyi njodzi iduku kudarika dambudziko rekuita ITP kana iwe uine utachiona kana rubella. Kubuda ropa kwakanyanya kunowanikwa mumatambudziko aya uye vanopfuura 90% yevanhu vachave nekugadzirisa kweICT mukati memwedzi mitanhatu.
Zvirwere zvekuzvidzivirira: ITP inofungidzirwa kuti inorwara uye inobatanidzwa nedzimwe zvirwere zvinokonzerwa nemapirus uye rheumatoid arthritis. ITP inogona kutanga kutaura kweimwe yezvirapa izvi.
Kuongororwa kweTP
Kufanana nedzimwe dambudziko reropa seanemia uye neutropenia , ITP inoratidzirwa pahuwandu hwekuverenga ropa (CBC). Hakuchina kuongororwa kweTP. Iko kuongororwa kwekuregererwa, kureva kuti zvimwe zvikonzero zvakarongwa kunze. Muzhinji, chete platelet count inoderera muItP; iyo white cell cell count uye hemoglobin yakajairika. Mutapi wako wehutano angave ane maplatelets anoongororwa pasi pe microscope (inonzi peripheral blood smear) kuti ave nechokwadi chokuti maplatelet anoderedza nhamba asi anoonekwa akaenzana. Pakati pekugadzirisa, iwe unogona kuva nedzimwe kuedza kuti uone kunze kwekenza kana zvimwe zvikonzero zveplateletlet kuverenga, asi izvi hazvidi nguva dzose. Kana iyo ITP inofungidzirwa kuva yechipiri kune chirwere chemoto, unogona kuongorora zvakananga izvi.
Kurapa kweTP
Parizvino, kurapwa kweTP kunobva pauripo hwezviratidzo zvekubuda ropa panzvimbo peplatelet count. Chinangwa chekurapa ndechekurega kubuda ropa kana kuunza platelet kuverenga kusvika kune "yakachengeteka".
Kunyange zvazvo zvisiri izvo "kwete" kurapa, vanhu vane ITP havafanire kutora aspirin kana ibuprofen-ine mishonga sezvo mishonga iyi inoderedza basa remaplatelet.
Kucherechedza: Kana iwe usina zviratidzo zvekubuda ropa ikozvino, chiremba wako angasarudza kukuchengetedza pasina kupa mishonga.
Steroids: Steroid yakadai semethylprednisolone kana prednisone ndiyo inowanzoshandiswa kurapa ITP pasi rese. Steroid dzinoderedza kuparadzwa kweplatelet mu spleen. Steroids inoshanda zvikuru asi inogona kutora nguva inopfuura vhiki kuti uwedzere platelet yako yakawanda.
IVIG: Intravenous immune globulin (IVIG) inowanzoshandiswa kweLTP. Inowanzoshandiswa kune varwere vane ropa rinoda kuwedzera nokukurumidza mu platelet count. Inoshandiswa seine intravenous (IV) kukanganiswa kwemaawa akawanda.
WinRho: WinRho imishonga yeVIV inogona kushandiswa kuwedzera platelet kuverengwa kune vanhu vane dzimwe ropa. Iyo inokurumidza kukurumidza kupfuura IVIG.
Platelet transfusion: Kuwedzerwa kweplatelet hakusi nguva dzose kunobatsira kune vanhu vane ITP asi inogona kushandiswa mune mamwe mamiriro ezvinhu akadai kana iwe uchida kushanda.
Kana iyo ITP yako ichiramba uye isingapindi mishonga yokutanga iwe chiremba angakurudzira mamwe mishonga akadai se:
Splenectomy : MuItP maplatelet anoparadzwa mu spleen. Nokubvisa chirwere, tarisiro yehupenyu yeplatelets inogona kuwedzerwa. Mabatsiro uye njodzi dzinofanira kuyerwa vasati vachisarudza kubvisa chirwere chacho.
Rituximab : Rituximab imishonga inonzi monoclonal antibody. Iyi mishonga inobatsira kuparadza masero emachena eropa ayo anogadzira zvirwere zvinopikisa maplatelet, anonzi B-seli. Tariro ndeyokuti kana muviri wako unobereka B-masero matsva, haazogadziri kupesana neaplatelet.
Thrombopoietin agonists: Zvimwe zvezvechirwere zvitsva ndeye thrombopoietin (TPO) agonists. Iyi mishonga iyi eltrombopag (muromo) kana romiplostim (subcutaneous); zvinomutsa mapfupa ako emapfupa kuita maplatelet akawanda.
Kusiyana kwevana nevakuru
Zvakakosha kucherechedza kuti nhoroondo yemasikirwo eIt inowanzosiyana nevana kuvana nevanhu vakuru. Vanopfuura 80% vevana vanoonekwa kuti vane ITP vachava nekugadzirisa kwakakwana. Vachiri kuyaruka uye vanhu vakuru vanowanzoita kuti vave neHIV isingaperi iyo inova chirwere chehupenyu hwehupenyu hwose chinogona kana chisingadi kurapwa.
> Kwakabva:
> CE Neunert, DL Yee. Kushungurudza kwePlateti. Muna: CD Rudolph, AM Rudolph, GE Lister, LR Kutanga uye AA Gershon eds. Rudolph's Pediatrics . 22nd ed. New York: McGraw Hill Mushonga, 2011.