Ichi Chinyorwa chePraterotemporal Degeneration Chinozivikanwawo se Pick's Disease
Maitiro akasiyana-siyana ekutungamira mberi kwemaodzanyemba (bvFTD) ndeimwe yemhando dzakasiyana siyana dzekushaya chimiro chinowira mu "frontotemporal degeneration". Ichi chikamu chinobata vanenge 50,000 kusvika 60,000 veAmerica. Sezvinoratidzwa nezita racho, rudzi urwu rwemtentia hunonyanya kukanganisa ruzivo rwemukati uye rwemakore rweuropi. Chirwere chekutengesa kwepamberi yepototemporal ndeyemhando yekuzvibata-yakasiyana-siyana.
Kuita-maitiro akasiyana-siyana pamberi pezvematongerwo enyika anonzi dementia dzimwe nguva anonzi chirwere chePikk .
Chii Chinokonzera Kusarudza Zvirwere?
Chirwere che Pick chinofungidzirwa chinokonzerwa nekusanganiswa kusina kushandiswa kwemapuroteni emadziro muzhepfenyuro nepamakore ekuropi. Aya mapuroteni anozivikanwa anozivikanwa seMuviri wemiti. Sezvavanounganidza mumatanda aya, masero europi anotanga kufa, zvichikonzera manzwiro, manzwiro uye maitiro ekugogodza mukushanda kwako.
Zviratidzo
Zviratidzo zvinowanzoonekwa zveBVFTD zvinetso zvekuzvibata kana zvepfungwa , zvinosanganisira kunyanya kudya, kuva nemafungiro ezvinyengeri, kuita mhinduro dzisina kukodzera, uye kuratidza hutano hwehupombwe uye zviito, pamwe nekutsamwa, kushungurudzika , kusafarira uye udyire.
Vanhu vane bvFTD vangave vachinetseka kuchengeta basa, kuratidza kuderera kwehutsanana hwavo, kuchengetedza zvimwe zvinhu, kuita zvisarudzo zvemari zvisina kunaka, uye nhengo dzemhuri dziri kure uye neshamwari kuburikidza nemashoko avo asingazivi uye maitiro.
Vamwe vanhu vane bvFTD vanoonawo matambudziko akafanana nehosha yaPasinson , kusanganisira kuderera kwechitarisiko chemaziso, kusindimara kwemisimba, kusimba uye kusagadzikana.
Kusiyana neAlzheimer's , kurasikirwa nekuyeuka hakuwanzoitiki muBVFTD, uye kana ikadaro, hazvisi kusvikira chirwere chacho chiri zvishoma nezvishoma.
Somutarisiri, iwe ungazoona zvimwe zvinetso zvekuyeuka, pamwe nematambudziko nekugadzirira kana kutarisa (zvine chokuita nehutungamiri hunoita ).
Mukudarika bvFTD, mutauro unobatawo, zvichiita kuti kukurukurirana kuve kwakaoma.
Zvirwere zvePikk zvakasiyana sei neAlzheimer's?
Kusiyana kwehutano hwepamberi (foreotemporal dementia) (Pick's disease) kune zvimwe zviratidzo zvinoputika nehosha yeAlzheimer sezvo zvirwere zvose izvi zvinowanzokonzera cognition, manzwiro uye mafambiro. Zviratidzo zvepakutanga zvechirwere cha Pick, zvisinei, zvinosanganisira zvikuru kuchinja mumanzwiro, kutonga , hutungamiri hunobata uye hutsika, panguva mune chirwere cheAlzheimer, chiyeuchidzo, kutarisana uye kutaurirana kunowanzova kwakajairika pakutanga.
Kuziva
Kuongororwa kweBvFTD kazhinji kunonoka nokuti pakutanga zvingafungidzirwa kuti munhu akabatwa ari kungove asina hanya, udyire, kuora mwoyo kana kuita zvisiri pamunhu. Sezvo zviratidzo zvichipfuurira, zvisinei, mhuri dzinowanzotsvaka rubatsiro rwechiremba wekuongororwa uye kurapwa. Kuongororwa kunoenderana nekuvapo kwezviratidzo zvakawanda zvakataurwa pamusoro apa, uyewo kukwanisa kutonga kunze kwechimwe chimiro chetementias chakadai seAlzheimer's or vascular dementia . Kudzokorora mitemo yepamusoro yehutsika yakasiyana-siyana yeFTD inogona kubatsira kumhuri dzemhuri kana BvFTD ichionekwa kana kuti inofungidzirwa nachiremba.
MRI inogona kubatsirawo pakuongorora bvFTD nokuti inowanzoratidza mamwe atrophy (shrinkage) yelobe yakatarisana yeuropi. Sezvo chirwere chacho chichifambira mberi, kukanganisa kuchawedzera uye kupararira kunzvimbo dzemazuva, pamwe chete nebasal ganglia.
Prognosis uye Upenyu Tarisiro (Long-Term Outlook)
Avhareji yemararamiro ehupenyu kubva kutanga kwezviratidzo anenge makore masere kusvika mapfumbamwe, kunyange vamwe vanhu vangararama makore makumi maviri kana kupfuura nehosha. Sezvo nehupi nehupi hwehutano hwemweya, inogona kuva chirwere chakaoma kune vanochengeta, uye kune avo vanozviona.
Kurapa
Kurapa kunogona kusanganisira kuedza kushandisa nzira dzisiri dzezvinodhaka kuti udzivise tsika dzakasiyana.
Vamwe vanachiremba vanorayira zvinodhaka zvinonzi serotonin reuptake inhibitors (SSRIs), iyo inogona kubatsira nedzimwe nzira dzekunyengera-dzinomanikidzika dzakadai sokucheka kana kudya.
Shoko kubva
Zvakajairika kunzwa uchinetseka pane dzimwe nguva apo iwe unotarisana nematambudziko ehutano hwakasiyana-siyana pamberi pekunamata kwemunhu. Rega muedzo wokuedza kuzviita iwe pachako; panzvimbo pacho, shingairira rubatsiro kune avo vakakupoteredza, kana iri kuburikidza nepurogiramu yemutsigiro wevanhu munharaunda, kukurukurirana paIndaneti pamusoro peBvFTD kana shamwari iyo inoda kukutorera kunze kwekofi kana kugara mumba newaunoda iwe paunenge uchitora.
Kuwedzeresa, The Association for Frontotemporal Dementia inoronga mapoka emapoka ekutsigira pamwe chete nemichina yepaIndaneti uye mutsara wefoni kuti ubatsirwe.
Sources:
Annals of Neurology. Kudya uye hypothalamus zvinoshanduka mukuzvibata-zvakasiyana-siyana pamberi pekunamata. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3084499
Sangano re Frontotemporal Degeneration. Izvo zvibvumirano zvenyika dzakawanda dzehutsika dzakasiyana-siyana FTD. http://www.theaftd.org/wp-content/uploads/2009/02/Table-3-International-consensus-criteria-for-behavioural-variant-FTD.pdf
Mabhangi, S., Weintraub, S. Journal of Geriatric Psychiatry neNeurology. Neuropsychiatric Symptoms in Behavioral Variant Frontotemporal Dementia uye Primary Progressive Aphasia .. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892801/
Neurology. Kunzwa kwezvino maitiro ekuongororwa kwehutano hwekuita zvakasiyana-siyana pamberi pepototemoral dementia. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2821829/
Yunivhesiti yeKalifornia, San Francisco. Dendaase Kuwedzera: Maitiro akasiyana-siyana eFTD. http://memory.ucsf.edu/ftd/overview/ftd/progression/multiple