Iwe UCTD Wakasiyana Sei Kubva MCTD?
Undifferentiated connective tissue disease (UCTD) uye mishonga yakasiyana-siyana inogadzirisa zvirwere (MCTD) ndiyo mitemo ine zvimwe zvakafanana kune zvimwe zvirongwa zvinogadziriswa kana zvirwere zvinogadzirisa zvirwere, asi pane zvakasiyana zvinoita kuti zvive zvakasiyana. Mune chirwere che systemic autoimmune, muviri wose unoshandiswa uye maitiro ezvirwere zvemuviri , izvo zvinowanzochengetedza muviri kuburikidza nekurwisa vapanduki vekune imwe nyika, kurwisa miviri yomuviri.
Mune chirwere chinoputika, sezvinoratidzwa nezita racho, mishonga inobatanidza inorwiswa uye inoshandiswa. Nhengo dzakagadzikana dzinotsigira uye dzinobatanidza zvikamu zvakasiyana-siyana zvemuviri uye dzinosanganisira ganda, cartilage, nezvimwe mishonga.
Utachiona hwehutachiona hwehutachiona hutachiona hunoputika hune humwe hutachiona humwe hutatu humwe hutachiona hunokonzerwa nehutachiona - systemic lupus erythematosus , scleroderma , uye polymyositis. Iko dzimwe nguva inonzi inonzi sylaprome. Pane zvakasiyana, zvirwere zvisina kufanira zvinogadzirisa zvirwere Zvirwere hazvikwanisi zvimwe zvinhu kana kuti zvinotarisirwa kuenzanisirwa seimwe yezvimwe zvirwere zvinogadzirisa zvirwere.
Zviratidzo zveUndifferentiated Connective Tissue Disease
Varwere vane zvirwere zvisina kufanira zvinokonzera zvirwere (zviratidzo, marwadzo akabatana), maitiro ekuongorora maitiro (eg, positive ANA ), kana zvimwe zvikamu zvehutachiona hwemagetsi, asi haagutsiri maitiro ekugadzirisa zvirwere zvakasiyana-siyana zvinokonzera zvirwere, zvakadai se lupus , rheumatoid arthritis , Sjogren's syndrome , scleroderma, kana vamwe.
Kana paine hutachiwana hunhu hunogona kuenzaniswa sehupi huri hutachiona hwehutachiona hwehutachiona, mamiriro acho anotsanangurwa se "zvisinafferentiated". Izwi rechirevo chekusava nehutano hwehutachiona hutachiona hwekutanga hwakatanga kutamba muma1980. Chaizvoizvo, chakashandiswa kune varwere avo vaifungidzirwa kuti vari mumatanho ekutanga ekubatana kwezvirwere zvirwere.
Latent lupus uye isina kukwana lupus erythematosus mamwe mazita anoshandiswa kutsanangura boka iri revarwere.
Inofungidzirwa kuti 20% kana vashomanana varwere vane zvirwere zvisina kufanira zvinogadzirisa zvirwere zvinopfuurira kusvika pakujekeswa kwechirwere chechirwere chinogadzirisa zvirwere. Inenge chikamu chimwe chete muzvitatu chinopinda mukuregererwa, uye vamwe vose vanochengetedza runyararo rwusingaverengeki rwehutachiona hwehutachiona.
Unhu hunoita zviratidzo zvehutachiona hunosanganisira zvirwere zvinosanganisira arthritis, arthralgia, Raynaud's phenomenon , leukopenia (low white blood cell count), rashes, alopecia, muromo wemakumbo, maziso akaoma, muromo wakaoma, low fevory fever, uye photosensitivity. Kazhinji, hapana maitiro emagetsi kana kushaya mafungiro, kana kupindira kwechiropa, mapapu, kana uropi. Ruzhinji rwevarwere vane hutachiona husingaregi hutachiona, zvichida 80%, vane maitiro e-autoantibody maitiro, kazhinji anti-Ro kana anti-RNP autoantibodies.
Kuongorora nekurapa UCTD
Sezvimwe chikamu chekuongororwa kwehutachiona hwehutachiona hwehutachiona hwehutachiona, nhoroondo yakakwana yezvokurapa, kuongororwa kwepanyama, uye kuongororwa kwebhroreta kunofanirwa kubvisa kukwanisa kweimwe zvirwere zverheumatic. Nezvekurapa kwehurumende isina hutachiona hwehutachiona hunenge husina kufanira, pakange pasina kumboongorora masayenzi emishonga chaiyo yekusagadzikana kwechirwere chetachiona.
Kusarudzwa kwekurapa kunowanzobva kune zviratidzo zvinowanikwa uye kubudirira kwechiremba yapfuura mukuronga kurapwa kwakasiyana kwezvirwere zverheumatic.
Kazhinji, kurapa kwaUCTD kunosanganisira kusanganiswa kweanalgics uye NSAIDs kuti vararame marwadzo, mapepa corticosteroids eganda uye mucous tissue, uye Plaquenil (hydroxychloroquine) sechirwere-chinorwisa anti-rheumatic drug (DMARD). Kana mhinduro yacho isingakwanisi, chirwere chepasi chakanyanya prednisone chingawedzerwa kwenguva pfupi. Maitiro akakwirira e-corticosteroids, cytotoxic zvinodhaka (semuenzaniso, Cytoxan), kana zvimwe DMARDS (zvakadai seImuran) hazviwanzoshandisi.
Methotrexate inogona kunge iri sarudzo yekuoma-kubata-maitiro ematambudziko asingabatsiri anogadzirisa zvirwere.
The Bottom Line
Kufananidzira kwekusakanganiswa kwechirwere chinokonzera zvirwere zvinoshamisa zvinoshamisa. Kune ngozi yakawanda yekufambira mberi kune zvakanyatsorondedzerwa zvinogadzirisa zvirwere, kunyanya pakati pevarwere vane ruzivo rusina kuchinja huwandu hune hutachiona hwehutachiona hwemakore mashanu kana kupfuura. Zviitiko zvizhinji zvinoramba zviri zvishoma uye zviratidzo zvinotapurirwa kunze kwekudiwa kwemutoro unorema immunosuppressants.
Sources:
Undifferentiated Connective Tissue Diseases (UCTD). Mosca M. et al. Selfimmune Reviews. 2006; Nov (6) 1-4. http://www.ncbi.nlm.nih.gov/pubmed/17110308
Undifferentiated Connective Tissue Disease - In-Depth Overview. Jessica R. Berman, MD. Chipatara Chekuvhiya Kunokosha. 11/10/2009. https://www.hss.edu/conditions_undifferentiated-connective-tissue-disease-overview.asp