Scleroderma inomira , inogadzirisa zvirwere zvehutu . Icho hachisi chirwere chimwe chete, asi pane chiratidzo cheboka rezvirwere zvakakanganiswa nekukura kusingawanisi kwezvibatanidza zvigunwe zvinotsigira ganda nhengo dzomukati.
Zvinokonzera
Chikonzero icho muviri unorwisa masero awo pachirwere ichi chisingazivikanwi hachizivikanwi. Vatsvakurudzi havabvumi kuti scleroderma inotora nhaka, kana, asi vanhu vanobva kumhuri ine nhoroondo kana zvimwe zvirwere zverheumatic zvingave zvakanyanyogadziriswa pakukudziridza.
Mune zvimwe zviitiko, scleroderma yakabatanidzwa kuve kune humwe makemikari kana kusvibiswa-mune mamwe mazwi, zvakatipoteredza zvinhu.
Kuwanda
Scleroderma inokanganisa 75,000 kusvika ku100 000 vanhu muUnited States. Maererano neAmerican College of Rheumatology, 12 kusvika ku20 matsva matsva e scleroderma pamamiriyoni anowanikwa muUnited States gore negore. Anenge chikamu chetatu chevanhu ava vane systemic sclerosis, iyo inobata muviri wose.
Ndiani Anozviwana?
Vakadzi vari pakati pemakore makumi matatu nemakumi mashanu nemakore makumi mashanu vanoverenga 75 muzana yezvinyorwa zve scleroderma, asi varume nevana vezera ripi zvaro vanogonawo kukura. Mamiriro acho kazhinji anowanzo pakati pemakore 25 kusvika ku55.
Mhando dzeScleroderma
Kune maviri mazamu akaenzana e scleroderma : akawanikwa uye akawandisa (anonziwo systemic sclerosis). Kunzvimbo yakagadzikana kune ganda kuwedzera uye kusimbisa, asi marudzi akawandisa anosanganisira midzi yeropa uye nhengo dzomukati.
- Localized Scleroderma: Localized scleroderma inonyanya kuchinja ganda uye inowanzoparadzaniswa kuva morphea (zvakaoma, mazamu evhapiti paganda) uye yakasvibiswa (ruvara rwakasiyana rweganda rakasvibiswa uye risina kuchena rinowanzobata maoko, mapfumo, kana phuma).
- Systemic Sclerosis: Systemic sclerosis inogoverwa muchengeti scleroderma (zvishoma nezvishoma, zvinongororwa kune dzimwe nzvimbo dzomuviri, zvinogona kukanganisa nhengo dzomukati gare gare) uye kupararira scleroderma (kamwe kamwe rose, thickening inobata nzvimbo huru uye inogona kukanganisa nhengo dzomukati). Sine scleroderma, iyo vamwe vanofunga seboka rechitatu re systemic sclerosis, haibatsiri ganda.
Zviratidzo Zvinowanzoonekwa: CREST
Vanhu vane systemic sclerosis vangave vane zviratidzo zvinokodzera chimiro chemuitiro, chinonzi CREST:
- Calcinosis (calcium inowanikwa mumagetsi anobatana)
- Raynaud's phenomenon (midziyo miduku yeropa kuminwe, zvigunwe, mhino, uye nzeve zvinogadzirisa mukupindura kwechando kana kushungurudzika)
- Esophageal dysfunction (musuru muchitsiko chepasi chesophagus haiti kushanda zvakanaka)
- Sclerodactyly (yakaoma, yakasimba, ganda rinopenya paminwe kana zvigunwe)
- Telangiectasias (maduku, matsvuku matsvuku pamaoko uye nechiso)
Kuziva
Hapana chiedzo chimwe chete chinoshanda sechinhu chinogadziriswa che scleroderma. Kusanganiswa kwezvakawanikwa kubva mumuviri wokuongorora, kuongorora ropa, uye miedzo inogona kuongorora matambudziko nhengo dzomuviri kubatsira kubata scleroderma . Vanhu vazhinji vane scleroderma vane miedzo yakanaka yezvinyorwa zvesimbikiresi. Kuongororwa kwakakodzera kunofanirwa kuvhara mushonga wakanaka.
Treatment Options
Hakuchina mushonga we scleroderma. Hapana mushonga unogona kumira kuwedzera kweganda kuwirirana nemamiriro acho ezvinhu, asi mishonga inorayirwa kuti ipe zviratidzo, izvo zvinogona kusanganisira:
- Raynaud's phenomenon
- kuora mwoyo
- high blood pressure
- interstitial lung disease
- pulmonary hypertension
- arthritis
- musimba simba
- zvinetso zvekudya
- itsvo zvinetso
Shoko Rinobva
Kana iwe uchifungidzira kana wakamboonekwa ne scleroderma kana systemic sclerosis, kuwana kuongororwa kwakakodzera uye kudzidza zvakawanda pamusoro pemamiriro ako ezvinhu kunogona kukubatsira kuti uchitungamirire zviri nani.
Hakusipo kurapwa kwechirwere ichi, asi kune mazano anobatsira ekurarama upenyu huri nani.
Sources:
Scleroderma, Arthritis Foundation
Scleroderma (Systemic Sclerosis), American College yeRheumatology