Huntington Akasiyana Sei neAlzheimer?
Chirwere cheHuntington (HD) chirwere chinopfuurira neurodegenerative chinotapurirwa pamagetsi kubva kuvabereki nevana. MuH HD, masero ehutano hwomunhu anotanga kuoma, zvichikonzera matambudziko emumuviri, mupfungwa uye mupfungwa. Zviratidzo zvekare zvinosanganisira kuora mwoyo , kusagadziriswa kushamwaridzana nekufamba uye kazhinji kusanzwisisa kwekuita.
Nhamba dzezvirwere zveHuntington
Vose vanenge 250 000 vanhu muUnited States vane kana kuti vachakudziridza HD.
Zviratidzo zvinowanzotanga pakati pemakore makumi matatu nemakumi mashanu, kunyange zvazvo vana vechidiki HD vanokanganisa vana vaduku se 2. Izvo zvave zvichionekwawo nevanhu vakura sevana makumi mapfumbamwe, asi izvozvo hazvishamisi. Kazhinji, mudiki munhu apo zviratidzo zvinotanga, nokukurumidza chirwere chinobudirira. Varume nevakadzi vanogona kunge vakagadzirisa mamiriro acho ezvinhu.
Zviratidzo zveHonda hwaHuntington
- Pakutanga Stage HD: Zviratidzo zvokutanga zveH HD zvinosangana nekuoma kudzidza zvinhu zvitsva kana kuita zvisarudzo, zvinetso nekutyaira, kusagadzikana, kushandura mafungiro, kushandiswa kwekuzvipira kana kukanganisa, kurongeka uye zvinetso zvenguva pfupi yekuyeuka .
- Middle Stage HD: Sezvo HD inopinda muchikamu chepakati, munhu ane dambudziko nekumedza, kutaura, kufamba, kuyeuka nekuisa pfungwa pamabasa. Mafambiro akasiyana-siyana (anonzi chorea ) eHD angave akarehwa zvikuru uye anopindira zvikuru nekushanda kwezuva nezuva. Munhu wacho anogonawo kukudziridza maitiro akaoma.
- Gumi reStart HD: Mazuva ekupedzisira zviratidzo zveHIV zvinokonzerwa nokusakwanisa kufamba kana kutaura, uye zvinoda kutarisirwa zvakakwana kune mutarisiri. Vanhu vane danho rekupedzisira HD vane pangozi yakakura yokugunzva.
Chii Chinokonzera Matambudziko aHuntington?
Anenge mamiriro ose eHD ane nhaka, zvinoreva kuti chirwere chacho chinotora nhaka kubva kuvabereki.
Kana baba vako kana amai vane HD, une mukana we50% wokuva neHD gene. Kana iwe uine nhaka yeHD gene, iwe pane imwe nguva unotanga HD. Kana iwe usati uine nhaka yeGENG gene, hauzokudziri HD uye iwe haungapfuuri jena pane vana vako.
Inenge 1% kusvika ku3% yevaya vane HD havana mubereki ane HD. Muchiitiko ichocho, chirwere chacho hachikwanisi kutariswa kune mumwe munhu mumhuri.
Masayendisiti akacherechedza HD gene muna 1993. Vamwe vanhu vari pangozi yeHIV vanoongororwa ropa ravo kuti vaone kana vari kutakura geni, asi vamwe vanorega kuongororwa sezvo pasina kurapwa kwechirwere panguva ino.
Kurapa kweHwere hwaHuntington
Hakuchina mushonga wechirwere chaHuntington, asi zviratidzo zvekuzvipira zvinoshandiswa zvinogona kurapwa ne tetrabenazine, iyo chete inogamuchirwa (muna 2008) neU.S. Food and Drug Administration nokuda kwechiitiko. Mamwe mishonga yakafanana neaya inoshandiswa muAlzheimer inogona kushandiswa kubata maHD ekufungisisa, maitiro uye mazviratidzo zvepfungwa. Mukuwedzera, zvinodhaka zvakadai saHaloperidol (Haldol) uye olanzapine (Zyprexa) zvinowanzoshandiswa.
Kuita- kuburikidza nenzira dzakarongeka sehutano hwepanyama uye hwekushanda, uye nzira dzisiri dzisina kufanana dzakadai sokufamba uye dzinoramba dzakashanda-dzakaratidzawo kuti dzinobatsira mukudzikisa kuderera kweHD kunokonzera.
Kudzivirira Dambudziko reHuntington
Ikozvino hapana nzira yekudzivirira HD. Zvisinei, kuchengetedza muviri unoshanda uye pfungwa dzakanaka zvichida kubatsira kunonoka zviratidzo kana kuti kunonoka kufambira mberi.
Zvirwere zvezvirwere zveHuntington
Kufanirwa kweH HD kwakaipa panguva ino. Ivhareji yemararamiro ehupenyu hunotevera hutachiona hunotangira kubva pamakore gumi kusvika makumi maviri. Rufu kazhinji runokonzerwa nezvinetso zveHD, zvakadai sokukanganisika kana kukwanisa kurwisana nehutachiona sepineumonia. Zvisinei, sezvo geni rinotarisirwa kupfuura HD pa rave rakataridzirwa, vatsvakurudzi vari kutarisa chirwere ichi nokudzidza migumisiro pahuropi, nechinangwa chekudzorera kukanganisa.
Iko kunewo kuenderera mberi kwekliniki miedzo yekuedza mishonga uye dzimwe nzira dzokurapa.
Hosha yeHuntington yakasiyana sei neAlzheimer's Disease ?
Zviratidzo zveHD neAlzheimer pakutanga zvakanyatsofanana, kunyange zvazvo HD yevheji yemakore ekutanga (makore makumi matatu kusvika ku50) yakawanda kudarika chirwere cheAlzheimer, iyo yakawanda inowanzoitika kune avo vanopfuura 65. Zvirwere zvose zvinokonzera kuora mwoyo uye zvinokanganisa kuyeuka , mano ekugadzirisa zvisarudzo uye kukwanisa kudzidza zvinhu zvitsva.
Sezvo kufambira mberi kweHDH, vanhu vanoratidzira kufamba kwechirwere chechirwere ichi; muAlzheimer's, kukwanisa kwemunhu kutama kazhinji kunowedzera zvishoma nezvishoma, asi havawanzoona huwandu hwakawanda husingabatsiri. Pakupedzisira HD, vanhu vanogona kunge vachiri kunzwisisa zvinotaurwa nevamwe, uye mhuri neshamwari vangaramba vachizviziva. Pakupedzisira kweAlzheimer's , vanhu vakawanda havakwanise kunzwisisa vamwe uye havaiti sevanoziva vamwe vanovapoteredza.
Uyezve, zvinenge zvose zvikamu zveH HD zvakatora nhaka, asi vazhinji veAlzheimer havasi nhaka yakananga.
Shoko kubva
Zvakajairika kuva nezvinhu zvakawanda kana iwe kana mudiwa wako akaonekwa kuti ane, kana kuti akaongororwa zvakanaka, chirwere chaHuntington, Kuziva kuti pane zvakawanda zvigadzirwa uye zvinotsigirwa zvinowanika zvinogona kubatsira sezvo iwe uchidzidza zvaunotarisira uye kuti ungaita sei. Iwe unogona kutanga kutanga nekusangana neHuntington's Disease Society of America, sezvo iri rimwe remasangano akawanda anogona kupa ruzivo rwezvekuwedzera uye inogona kukwanisa mapoka ekutsigira.
Sources:
Alzheimer's Society. Zvinokonzera Zvinokonzera Dementia.
Huntington's Disease Society of America. Nhanho dzeHurtington's Disease.
Huntington's Disease Society of America. Chinyiko Chirwere chaHuntington.
National Institute of Neurological Disorders uye Stroke. National Institute of Health. NINDS Dambudziko reHuntington Information Information.