Rheumatoid vasculitis isingadikanwi, inonyanya kukonzera rheumatoid arthritis iyo inogona kunge inopisa upenyu. Muurumatoid vasculitis, kuputika kunopararira kumidziyo yeropa shoma kana midhisi mumutumbi. Kazhinji, mishonga inobatanidzwa, asi mitsetse inogona kunge yakafanana. Mishonga yakakura yeropa haiwanzobatanidzwa.
Masvingo emidziyo yeropa inoputika yakawanda uye sechiedza chemuviri weropa chakakanganiswa, chinogona kuvhara.
Ropa kunopa nhengo rinogona kushandiswa, kana risingaregi. Rheumatoid vasculitis inogona kusanganisira nhengo dzakasiyana-siyana, kusanganisira ganda, maziso, mitsetse, mwoyo, mapapu, uropi, itsvo, kana marumbo. Asi, kunewo mashoko akanaka pamwe chete. Vashomanana rheumatoid arthritis varwere vari kuwedzera rheumatoid vasculitis, zvichida nemhaka yemishonga inoshanda yakawanda yakagadzirwa uye inotengeswa mumakore gumi apfuura kana zvakadaro (kureva, biologic zvinodhaka ).
Kuwanda uye Njodzi yeRhumatoid Vasculitis
Kunyange zvazvo kupararira kwerhumatoid vasculitis kunoratidzika kuderera, zvinofungidzirwa kuti pasi pe1 kusvika ku5 muzana yevarwere vepamusoro rheumatoid arthritis inowedzera rhumumatoid vasculitis. Zvisinei, zvidzidzo zve autopsy zvakashuma 15-31%. Kuipa uye kufa kwehuwandu hunobatanidza nerhumatori vasculitis inokosha nemakore mashanu ekufa kwevakafa pa30-50% nehuwandu hwehutachiwana hwehutano hwakabatanidzwa nehutano hwehutano kana hwekurapa.
Zvinhu zvinotevera zvinowedzera dambudziko rekuwedzera rhumatoid vasculitis:
- Chinhu chakanaka cherheumatoid chinhu
- Zvakanaka zvekurwisa CCP
- Murume (1 mu9 varume ne rheumatoid arthritis vanokudza rheumatoid vasculitis)
- Kusvuta
- Kuvapo kwerumatoid nodules
- Munhu akwegura paanotanga kurwara kana kuti kwenguva yakareba ye rhumumidhi arthritis (anopfuura makore gumi)
Zviratidzo uye Zviratidzo zveRheumatoid Vasculitis
Chero nhengo yomuviri inogona kuchinjwa nedheumatoid vasculitis. Ganda uye manzwiro emvura zvinowanzobatanidzwa. Kunyange zvazvo hukuru huchibatanidzwa hunoonekwa huchiri hushoma, hunobatanidzwa nekukosha kwekufa nekufa.
Kubatanidzwa kweganda kunogona kusanganisira purpura, maronda, zvironda, uye necrosis yezvinyorwa, kunyanya pamuromo. Livedo reticularis inowanzowanikwa. Kubatanidzwa kweganda kunoda kuti uwedzere kutsvakurudza kune imwe nhengo inobatanidzwa. Scleritis , pleuritis , kana pericarditis ndiyo mienzaniso yezvinogona kuitika. Kana ganda racho richibatanidzwa pasina mamwe maitiro ekugadziriswa, kufungidzira kuri nani.
Nechirwere chengwena chinonzi peripheral neuropathies chinogona kukura, chakadai se distal symmetric sensory polyneuropathy, distal motokari kana kubatana neuropathy, kana mononeuritis multiplex. Apo vasculitis inokuvadza mitsipa. apo kunogona kunge kusina simba, kurira, kurasikirwa kwekunzwa, kushaya simba, nekurasikirwa kwebasa mumaoko kana patsoka. Zviratidzo zvakawanda zvinogona kuitika zvakare, zvakadai sefivha, kuora muviri, kurasikirwa kwechido, uye kurasika kwesimba.
Kuongororwa kweRheumatoid Vasculitis
Kunyange zvazvo muenzaniso wezviratidzo ungaita kuti chiremba afungidzire rheumatoid vasculitis uye maitiro e laboratori inogona kupa uchapupu hunosimbisa hwechiitiko chinogona kuongororwa, biopsy inofanirwa kujekeswa.
Kushanda kweganda kunogona kuve kwakagadzirwa, pamwe chete nemusuru kana musungo mukati memharaunda, kana nhengo inopindirwa.
Nepo kuongororwa ropa kwerumatoid factor uye anti-CCP zvinowanzokwidziridzwa muurumatoid vasculitis, mhinduro haisi yakananga. Zvirwere zviviri izvi zvinowanikwawo mune rheumatoid arthritis pasina vasculitis. Anti-neutrophil cytoplasmic antibodies (ANCA) uye inosanganisira anti-myeloperoxidase uye anti-proteinase-3 antibodies inowanzosava muhutukutu hwevashumitis.
Kurapa kweRheumatoid Vasculitis
Kurapa kwerhumatoid vasculitis kunonyanya kugadziriswa nhengo dzemuviri dzinobatanidzwa.
Uyezve, rheumatoid arthritis inofanira kunyatsorapwa inoshandiswa kushandisa DMARD kana madhiragi biologic, zvakadai seN TNF blockers . Kudzora kuvhiringidza muzvikamu zviviri uye mumidziyo yeropa kunokosha.
Mutsara wokutanga wehutachiona hwerhumatoid vasculitis unosanganisira kushandisa korticosteroids (kazhinji prednisone ). Prednisone inogona kuwirirana ne methotrexate kana azatioprine. Zvine zviratidzo zvakakura uye kushanda kwechirwere chakaoma, kuedza kunotyisa kwekudzivirira mafungiro kunogona kusanganisira cyclophosphamide pamwe nekuwedzerwa kwakanyanya kwe prednisone. Rituxan (rituximab) iri kubuda senzira yekutanga yekurapa kwerheumatoid vasculitis. Maererano nemushumo weArthritis Care and Research (2012), kuongororwa kwemashoko kubva kuAustimmunity uye Rituximab registry kwakaratidza kuti kuregererwa kwakagadziriswa mu12 kubva ku17 rumumatoid vasculitis varwere vanobatwa ne rituximab. Vachiremba vakakwanisawo kuderedza chido chavo che prednisone.
Sources:
Rheumatoid Vasculitis. Johns Hopkins Vasculitis Center.
http://www.hopkinsvasculitis.org/types-vasculitis/rheumatoid-vasculitis/
Rheumatoid Vasculitis. Cleveland Clinic.
http://my.clevelandclinic.org/services/orthopaedics-rheumatology/diseases-conditions/hic-rheumatoid-vasculitis
Rheumatoid Vasculitis. Vasculitis Foundation. Svondo 2012.
http://www.vasculitisfoundation.org/education/forms/rheumatoid-vasculitis/
Rheumatoid Vasculitis: Vanopera Mungozi kana Vanotarirwa Kurapa Mutsva? Bartels uye Bridges. Nhasi Rheumatology Reports. December 2010.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2950222/
Rituximab therapy ye systemic vasculitis inobatanidza nerheumatoid arthritis: Zviwanikwa kubva kuAustimmunity uye Rituximab Registry. Puechal X et al. Arthritis Care and Research. March 2012.
http://www.ncbi.nlm.nih.gov/pubmed/22076726