Idiopathic pulmonary fibrosis ( IPF ) haisi kurapwa, asi inoporesa. Ndinofara, mishonga mitsva yakabvumidzwa kubva muna 2014 iyo iri kuita mutsauko muzviratidzo, hutano hwehupenyu , nekufambira mberi kwevanhu vanorarama nechirwere ichi. Kusiyana neizvi, mishonga yakashandiswa kusvika munguva pfupi yapfuura yakanzi yakakonzera kukuvadza kupfuura kunaka kwevamwe vanhu vane IPF.
Kana wakamboonekwa kuti une chirwere ichi, iva nechokwadi chokuti hauodzwa mwoyo nemashoko akare.
Zvinangwa Zvokurapa kweIdiopathic Pulmonary Fibrosis
Kukanganisa kwakaitika mu IPF kunoreva kusakanganiswa; the fibrosis (scarring) yakaitika haigoni kuporeswa. Saka, zvinangwa zvekurapa ndezvekuti:
- Deredza kuderedza mhirizhonga kumapapu. Sezvo chinokonzera chinokonzera IPF kukanganisa kunoteverwa nekuporesa kusingaperi, kurapwa kunotungamirirwa pane izvi.
- Kuvandudza kufema kunetseka.
- Kurisa basa uye hupenyu hwehupenyu.
Sezvo IPF iri chirwere chisingawanzoitiki, zvinobatsira kana varwere vanogona kutsvaka kutarisirwa kune imwe nzvimbo yezvechiremba iyo inonyanya kugadzirisa idiopathic pulmonary fibrosis uye interstitial lung disease. Nyanzvi inogona kunge ine ruzivo rwemazuva mashoma rwekusarudzwa kwehutano huripo uye inogona kukubatsira kuti usarudze chimwe chinonyanya kukosha pane imwe nyaya yako.
Mishonga yeIdiopathic Pulmonary Fibrosis
Tyrosine Kinase Inhibitors
Muna Gumiguru ra2014, mishonga miviri yakatanga kuva mishonga inotenderwa neDFA chaiyo yekurapa idiopathic pulmonary fibrosis. Iyi mishonga, pirfenidone uye nintedanib, inotarisa mishonga inonzi tyrosine kinase uye inoshandiswa nekuderedza fibrosis (antifibrotics).
Zvinyoronyoro, tyrosine kinase enzymes inobatsira kukura kwezvinhu zvinokonzera fibrosis, naizvozvo mishonga inovhara ma enzyme uye naizvozvo kuwedzera zvinhu zvinogona kuita kuti frosis inowedzera.
Iyi mishonga yakawanikwa ine zvikomborero zvakawanda:
- Vakaderedza zvirwere zvishoma nehafu mukati megore varwere vakatora mishonga (iko zvino yava kuidzidzwa kwenguva yakareba kwenguva yakareba).
- Zvinoderedza kuparara kwebasa mumapapu ekushanda (kuderera kweFVC kuderera) nehafu.
- Zvinokonzera kusanyanya kuderera kwechirwere ichi.
- Varwere vachishandisa madhiragi aya vaiva nehutano hwakanaka-hunoenderana neutano hwehupenyu.
Iyi mishonga inowanzoremeswa zvakanaka, iyo inonyanya kukosha kune chirwere chinopfuurira pasina mushonga; chiratidzo chinowanzovhiringidzika kuva chirwere.
N-Acetylcysteine
Munguva yakapfuura n-acetylcysteine ​​yaiwanzoshandiswa kurapa IPF, asi zvidzidzo zvenguva pfupi hazvina kuwana kuti izvi zvibudirire. Kana ichinge yaputsika inoratidzika kuti vanhu vane mazita emhando dzedzinza vanogona kuvandudza pamishonga, nepo avo vane rumwe ruzivo rwemhando (rumwe rutivi) vanowanzovhiringidzwa nemishonga.
Proton Pump Inhibitors
Zvine kufarira ndeimwe yedzidzo yakashandiswa uchishandisa esomeprazole, proton pump inhibitor , pamasero emapapu murabhu uye mumakonzo. Iyi mishonga, inowanzoshandiswa kurapa chirwere chegastroesophageal reflux, yakaguma nekuwedzera kupona mumaviri emapapu uye mumakonzo. Sezvo GERD inonyanya kutsvaga ku IPF, inofungidzirwa kuti asidi kubva mudumbu inoshuva mumapapu inogona kuva chikamu cheEtiology yePFF.
Kunyange zvazvo izvi zvisati zvamboedzwa kuvanhu, zvechokwadi kurapwa kweGERD isingaperi muvanhu vane IPF inofanira kufungwa.
Muchengetedzwa Kupinda Chirwere
Kushandiswa kwekushandiswa kwemapapu maviri kana kusina mapepa sekurapa kwePF kwave kuchiwedzera zvishoma nezvishoma pamusoro pemakore gumi nemashanu apfuura uye inomiririra boka guru revanhu vanomirira kuputika kwemapapu muUnited States. Inotakura ngozi yakawanda asi ndiyo chete kurapa inozivikanwa panguva ino kujekesa hupenyu hwekutarisira.
Parizvino, kupona kwemazuva mashoma (nguva inotevera iyo hafu yevanhu vakafa uye hafu vachiri vapenyu) makore 4.5 ane kuwedzerwa, kunyange zviri pachena kuti kupona kwakagadziridzwa panguva iyoyo apo mushonga unowedzera kupfuura.
Kupona kwepabonde kune yakakwirira kudarika kwepakati pemapapu maviri, asi zvinofungidzirwa kuti izvi zvinowanzoita nezvimwe zvinhu kunze kwekuisa, sezvinoitwa nevanhu vane imwe kana maviri mapapu akaputika.
Kutsigira Mushonga
Sezvo IPF iri chirwere chinopfuurira, chirongwa chinotsigira kuve nechokwadi chehutano hwakanaka hwehupenyu hunoita zvakakosha zvikuru. Zvimwe zvezviyero izvi zvinosanganisira:
- Kutarisana kwezvinetso zvenguva imwe chete.
- Kurapa kwezviratidzo.
- Flu shot uye pneumonia inopfurwa kuti ibatsire kudzivirira zvirwere.
- Kuvandudzwa kwepulmonary .
- Oxygen therapy - Vamwe vanhu vanozeza kushandisa oxygen nekuda kwekushorwa, asi kunogona kubatsira zvikuru kune vamwe vanhu vane IPF. Zvechokwadi, zvinoita kuti kufema kuve nyore uye kunobvumira vanhu vane chirwere kuti vave nehutano hwakanaka hwehupenyu, asi kunoderedzawo matambudziko anokonzerwa neakisijeni yakadzika muropa uye inoderedza zvirwere zveupemenia (high blood pressure in arteries that travel between the right side of mwoyo nemapapu).
Mamiriro ezvinhu anowirirana uye Matambudziko
Zvinetso zvakawanda zvinowanzoonekwa kuvanhu vanogara ne IPF. Izvi zvinosanganisira:
- Kurara kuputika
- Gastroesophageal reflux chirwere (GERD)
- Pulmonary hypertension - High blood pressure mu arteri yemapapu inoita kuti zvive zvakaoma kupinza ropa kuburikidza nemidziyo yeropa inopinda mumapapu, saka rutivi rworudyi rwemwoyo (kurudyi uye rworuboshwe) rinofanira kushanda zvakaoma.
- Kuora mwoyo
- Kanza yemaperembudzi - Inenge 10 muzana yevanhu vane IPF vanova nekenza yemapapu
Kana uchinge waonekwa kuti une IPF , unofanirwa kurukura nezvekugona kwezvinetso izvi nachiremba wako uye uronga hurongwa hwekuti iwe unogona sei kutarisira kana kuvadzivirira.
Online Support Groups uye Makomba
Hapana chakafanana nekutaura kune mumwe munhu ari kurwara nechirwere chakafanana newe. Asi, sezvo IPF isingawanzoitiki, pane imwe nguva haisi boka rekutsigira munharaunda yako. Kana uri kugamuchira kurapwa pane imwe nzvimbo inonyanya kuwanika kuI IPF, pangava nemapoka ekutsigira-munhu anowanikwa kuburikidza nehutano hwako.
Kune avo vasina boka rekutsigira rakadai-rinofanira kunge rinoreva kuti vanhu vazhinji vane mapepa ekutsigira IPF-inharaunda uye mharaunda ndiyo yakasarudzwa. Mukuwedzera, izvi ndezvikwata zvaunogona kutsvaga mazuva manomwe pavhiki, maawa makumi maviri nemasere kana iwe unofanirwa kubata nheyo nemumwe munhu.
Mapoka ekutsigira anobatsira pakukweretesa kutsigira kwevanhu vakawanda uyewo inzira yekuchengetedza zvitsvakurudzo zvekare uye kurapwa kwechirwere. Mienzaniso yevamwe vanogona kubatana inosanganisira:
- Pulmonary Fibrosis Foundation
- Inspire Pulmonary Fibrosis Community
- VarwereZvino Pulmonary Fibrosis Community
Shoko Rinobva
Iroopathic pulmonary fibrosis inowanzosiyana-siyana, nevamwe vanhu vane zvirwere zvinokurumidza kufambira mberi, uye vamwe vanoramba vakasimba kwemakore akawanda. Zvakaoma kufanotaura kuti chii chichava nemumwe murwere. Kuwedzera kwepakati pemvura kwaive nemakore 3.3 muna 2007 zvichienderana nemakore 3.8 muna 2011. Chimwe chidzidzo chakawana kuti vanhu vane makore makumi matanhatu nemakumi matanhatu vakagara kwenguva yakareba ne IPF muna 2011 kupfuura zvavakanga vari muna 2001.
Kunyangwe pasina mishonga inongobvumidzwa, kutarisirwa kunoratidzika kuva kuri nani. Usavimba nemashoko akwegura aunowana, izvo zvingave zvisipo. Taura nachiremba wako pamusoro pezvakataurwa zvinotevera uye izvo zvakakunakira iwe.
Sources:
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de Boer, K., naJo Lee. Zvinonzwisisika zvinowanikwa mumiti in idiopathic pulmonary fibrosis: kuongorora. Respirology . 2015 Sep 13. (Epub mberi kwekudhinda).
O'Riordan, T., Smith, V., naG. Raghu. Kuvandudza Novel Agents yeIdiopathic Pulmonary Fibrosis: kufambira mberi pakutsvaga kutsva uye kliniki yekuongorora. Chest . 2015 May 8. (Epub mberi kwekudhinda).
Raghu, G. et al. Kuongororwa kweIdiopathic pulmonary fibrosis ne-high-resolution CT mune varwere vane zvishoma kana kuti hapana zvehurogiological uchapupu hwokuti uchikanganiswa: kuongorora kwechipiri chekuongorora kwakarongeka, kutongwa. Lancet Respiratory Medicine . 2014. 2 (4): 277-84.
Spagnolo, P., Maher, T., naL. Richeldi. Idiopathic pulmonary fibrosis: Ichangopfuura kufambira mberi kwehutano hwemishonga. Pharmacology & Therapeutics . 2015. 152: 18-27.