Extranodal Lymphoma

Kunyange zvazvo lymphomas iyo yose inokonzera mararamiro anokonzera lymphocytes - rudzi rwechichena chemuviri weropa - dzimwe nguva ndiyo iyo kufanana kunopera. Kune marudzi akawanda akasiyana uye subtypes e-lymphoma. Izvo zvikamu zviviri zvakakura ndeyeHodgkin's lymphoma , kana HL, uye kwete yeHodgkin's lymphoma, kana NHL . Ruzhinji rweNHL neHL dzine nodal lymphomas, zvinoreva kuti dzinotanga mumakirini nhengo.

Zvinogoneka, zvakadaro, kuti lymphomas dzinomuka pose pose.

Tsanangudzo: Primary Extranodal Lymphoma

Apo lymphoma inofungidzirwa kuti yakatanga kunze kwemakirini anonzi lymph nodes , inonzi extranodal lymphoma, kana kunyanya kunyanya, primary extranodal lymphoma. Pane dzimwe nguva, zvinogona kuva zvakaoma kufungidzira kuti mumuviri mutumbi unonzi lymphoma wakatanga. Muzviitiko izvi, vanachiremba vanogona kutevera tsanangudzo yakawanda: Kana lymphoma pane imwe nguva yaive nehomba huru -iyo yakawanda kwazvo - mune imwe nzvimbo yakaderera, saka inogona kuonekwa se extranodal lymphoma.

Kusiyana Kunokosha

Pakati pemakirini anotanga kuine lymph nodes , kana kuti nodal lymphomas, zvinenge zvese zvinogona kuva nekubatanidzwa kwepranodal - kureva kuti, vanogona kupararira kune nzvimbo dzomukati. A lymphoma inopararira kune dzimwe nhengo kubva kune lymph nodes HAIYE inofungidzirwa sepakutanga extranodal lymphoma. Kuti uve wepakutanga extranodal, lymphoma inofanira kunge yakatanga kunze kwemakirinikodhi.

Overview

Primary extranodal lymphomas inonyanya kuwanikwa muNHL kupfuura muHodgkin's lymphoma. Kusvikira 33 kubva muzana yeNHL yose inoonekwa sepakutanga extranodal lymphoma, asi muHL, chirwere chekutanga chema extranodal chinofungidzirwa kuti chinosara.

Nzvimbo inonyanya kushandiswa yekutanga primary extranodal lymphoma iri mumugwagwa wepamuviri, uye zvinenge zvose izvi ndeNHL.

Nzvimbo inotevera inowanzoitika shure kweGI turakiti iri ganda . Zvisinei, apo NHL inotanga muga pega pega, inonzi kemikari yeganda, kana kuti lymphoma yemavara.

Extranodal lymphoma inogonawo kubuda mumuviri we lymphoid wepleen, bone marrow, thymus, toni, uye adenoids - zviduku zviduku zvakadai zvakafanana zvakavharwa apo nzvimbo dzomumvura dzinosangana nehuro.

Masero omunhengo dzomukati kana lymphoid mudumbu, mapapu, muzvivako zvakakomberedza maziso, muhutano hwetroroid, mazamu anoita salivary, uye mumukati muduku anogonawo kukonzera maitiro ekutanga emymphomas. Lymphomas munharaunda idzi dzinosanganisira 'nzvimbo yakatarisa B-cell lymphomas ye mucosa-inosanganisira lymphoid tissue,' kana kuti MZBCL yeMALT, kwenguva pfupi.

Zvinyorwa zvemakumbo emhino nehuro zvinosanganisira MZBCL yeMALT, inoparadzanisa B-cell lymphoma kana DLBCL , uye muurayi wepanyama / T-cell lymphomas.

Primary lymphomas inogona kuchinja ma testes mumarume uye inonzi primary testicular lymphomas. Lymphoma muuropi, kana CNS lymphoma, inogonawo kuva yekutanga. Kunyange zvazvo primary priranodal lymphoma yeuropi uye ma testes yave ichibatanidzwa nekuoma-kubata-kurapa zvirwere, zvidzidzo zvitsva zvakaratidza kuti kurapwa kwakagadziriswa kune nzvimbo idzi kungaguma nekuvandudza kukuru.

Primary extranodal follicular lymphomas iyo isiri ganda lymphomas inowanzoitika.

Primary bone lymphoma isingawanzoitiki iyo iyo lymphoma inotanga mufupa.

Primary cardiac lymphoma ndechimwe chezvipembenene zvakanyanya zvemoyo. Primary cardiac lymphoma inofungidzirwa kuti inyore 1.3 muzana yemakumbo ose emwoyo uye chete 0.5 muzana yezvose zvinonzi extranodal lymphomas. Kana zvikaitika, rudzi rwakakurumbira rwechirwere ichi runoparadzanisa B-cell lymphoma, uye kazhinji, atrium yakarurama uye ventricle yakarurama inobatanidzwa.

Imwe tsanangudzo yekutanga primary extranodal lymphomas, inowanzo, ndeyokuti yakawedzera zvinoshamisa nekubudirira kweHIV neAIDS.

Primary Extranodal Lymphoma - Prognosis

Ichokwadi kuti lymphoma inonyanya kuwedzera extranodal lymphoma inogona kuva chinhu chinogadzirisa chirongwa chekurapa uye kufungidzira, asi zvimwe zviitiko zvingave zvakakosha zvakafanana kana zvakakosha zvikuru.

I-lymphoma subtype, B cell kana T cell type, uye nhengo yekutanga kana michina inobva kune dzose inogona kuva yakakosha kufungidzira zvinhu.

Extranodal Kubatanidza - Prognosis

Zvinenge zvose zvinonzi nodal lymphomas zvinogona kupararira kune dzimwe nzvimbo dzomugumo, asi mumatambudziko aya, hazvifungidzirwi kuti ndeyokutanga extranodal lymphomas.

MuNHL, zvirongwa zvakanakisisa zvekurapa zvinotarisana nezvimwe zvinhu, uye kubatana kwepranodal kunogona kuva imwe yeiyo. Dzimwe nguva lymphoma inowanikwa kune lymph nodes inonyanya kurapwa uye inofanirwa kunyanya kufungidzirwa kupfuura lymphoma yakapararira kunze kwemakirinikodhi. Kunyange zvakadaro, zvakasiyana-siyana zvemaitiro eEntranodal Primary NHL - pamwe chete nezvimwe zvinhu zvakawanda zvinokonzera kurapwa nemigumisiro - zvinoreva kuti chirongwa chekurapa uye chirevo chinogona kuva munhu mukuru.

Mune zvimwe zviitiko, kubatanidzwa kweexranodal kunoratidza zvirwere zvakanyanya. Mune chirwere cheHodgkin , somuenzaniso, kubatanidzwa kweexranodal - kunze kwepleen ne thymus - inoratidza chirwere chechina Hodgkin chirwere. Kunyange kusvika pfupi-nhanho Hodgkin's disease inogona kunyatsoporesa, zvakadaro.

Sources:

Histopathology yeNodal uye Extranodal Non-Hodgkin's Lymphomas; Alfred C. Feller, Jacques Diebold; Springer Science & Business Media, Jun 27, 2011

Campo E, Chott A, Kinney M, et al. Purogiramu yekubudisa lymphomas. Mhedziso yeChikoro chakaitwa neEAHP uye SH mune Thessaloniki, Greece. Histopathology . 2006; 48 (5): 481-504.

Troppan K, Wenzl K, Neumeister P, Deutsch A. Molecular Pathogenesis yeMALT Lymphoma. Gastroenterology Research and Practice . 2015

Zucca E, Gregorini A, Cavalli F. Kutungamirirwa kwemasero e-non-Hodgkin anowanikwa panzvimbo dzeprandodal. Therapeutische Umschau. 2010; 67 (10): 517-25.

Krol AD, le Cessie S, Snijder S et al. Primary extranodal isingaiti Hodgkin's lymphoma (NHL): zvinokonzerwa nedzimwe sarudzo dzakaedzwa muChitresive Cancer Centre West-based NHL registry. Annals of Oncology . 2003; 14 (1): 131-139.

Primary malignant lymphoma yezamu: Clinicopathological kudzidza nezvemapfumbamwe. Leukemia uye Lymphoma . 2004 Feb; 45 (2): 327-30.

Primary gastric lymphoma. World J Gastroenterol . 2004 Jan; 10 (1): 5-11. Kudzokorora.

Intra-Vascular Large B-Cell Lymphoma Yakaratidzwa neNehrotic Syndrome: Kubviswa kwegore rimwechete Kunokonzerwa neHigh Frequency CHOP neRituximab. Leukemia uye Lymphoma . 2004; 45 (8): 1703-1705.

Jonavicius K, Salcius K, Meskauskas R, Valeviciene N, Tarutis V, Sirvydis V. Primary cardiac lymphoma: maitiro maviri uye kuongorora mabhuku. J Cardiothorac Surg . 2015; 10: 138.