Lupus chirwere chinogadzirisa muviri chinotora pamhando dzakasiyana-siyana, iyo systemic lupus erythematosus (SLE) imwe. Lupus inogona kukanganisa chero chikamu chemuviri, asi inowanzokonzera ganda rako, mafundo, mwoyo, mapapu, masero eropa, itsvo, uye uropi. Vanenge mamiriyoni 1,5 vokuAmerica vane rumwe rudzi rwe lupus, maererano neLupus Foundation yeAmerica, uye inofungidzirwa 16 000 ichangobva kuongororwa gore negore.
Chero ani zvake ari muzera ripi zvese anogona kuwana chirwere ichi, kunyange zvazvo vazhinji varwere vane lupus vari vakadzi pakati pemakore gumi nemashanu ne45.
Immune System
Kazhinji, masimba edu emasikirwo anochengetedza muviri wedu kurwisana nemakirwe emakemikari anenge mavairasi uye mabhakitiriya. Nechirwere chekudzivirira, izvi zvinowanzochengetedza zvirwere zvemuviri uye zvinotanga kurwisa muviri.
Kana izvi zvikaitika, munhu anogona kuve nekuputika (chinonyanya kukosha kwe lupus), kurwadziwa, uye kuora kwechivi. Kuvhiringidza mukati uye pachako kunogona kukonzera marwadzo, kupisa, kubwinya, kuzvimba, uye kurasikirwa kwebasa, kana mukati (dzimwe nhengo), kunze (kunyanya ganda), kana maviri.
Kuzvidzivirira zvirwere zvakadai se lupus zvinogona kuva zvakaoma kufungidzira nekusiyanisa.
Mitauro yeLupus
Kune mhando ina dze lupus dzinoshandisa zvikamu zvakasiyana zvemuviri. Kunyange kana iwe uine chirwere chakafanana nemumwe munhu, zviratidzo zvako hazvizove zvakangofanana, sezvo chirwere chacho chinonyanya kuenzaniswa.
Systemic Lupus Erythematosus (SLE)
Nzira yakakurumbira ye lupus ndiyo systemic lupus erythematosus (SLE), iyo inogona kukanganisa nhengo dzakawanda dzomuviri, kusanganisira majoints, ganda, mutezo weropa, uye nhengo. Izvi zvinokanganisa makumi manomwe kubva muzana yevanhu vane chirwere uye ndizvo zvinowanzoendeswa kune vanhu pavanotaura "lupus."
VANHU vanorwara vanokwanisa kupfuura nemakore emavhudzi matsvuku, kuneta zvakanyanya, zvinorwadza kana zviputi zvinoputika, kana fevha vasina kumboona chimiro kumoto kana kuti chiremba anokwanisa kukwanisa kuona SLE. Zviratidzo izvi zvinogona kuuya uye zvichienda kamwechete uye zvinogona kubva kubva kune zvinyoro kusvika kune zvakanyanya.
SLE inowanzoongororwa ichishandisa anti-nuclear anti-blood test (ANA) , iyo inoratidzira autoantibodies inorwisa muviri wako maviri nemasero. AAA inofadza hazvirevi kuti iwe une lupus, asi pane izvo zvinokonzerwa nechikamu chimwe chepikicha yemapirus diagnosis inosanganisira zviratidzo zvako, kuongorora muviri, nezvimwe, kunyanya kuongororwa kwema laboratori.
Mishonga-Inobatsira Lupus
Zvinodhaka-induced lupus zvinosanganiswa nezviratidzo zvakafanana, asi zvinonyatsounzwa nemamwe marudzi emishonga, kazhinji inotorwa kwenguva refu. Zvinodhaka-induced lupus zvinodzokororwa zvachose mushure mokunge mishonga ichibviswa, uye zviratidzo zvinowanzoenda mukati pemwedzi mitanhatu. Mhando iyi inoratidzira kusvika 10 muzana yemapus kesi.
Mishonga yakawanda yakave ichizivikanwa kuti inokonzera ichi chimiro chechirwere ichi, asi vazhinji vanofungidzirwa kuti vanoita zvakaipa. Iyo inonyanya kurwisa-inflammatories, anticonvulsants, kana zvinodhaka zvinoshandiswa kuporesa zvirwere zvisingaperi sekushaya chirwere chepfungwa, chirwere chetachiona, hutachiona hwepamusoro (kukwirira kweropa), uye marwadzo eurosiyasia.
Iyo mitatu mitatu inowanzopomera mhosva yezvinodhaka-induced lupus ndeyi:
- procainamide - yakashandiswa kurapa mwoyo arrhythmias
- hydralazine - inoshandiswa kuporesa dutu
- isoniazid - inoshandiswa kurapa tuberculosis
Lupus yakagadzikana
Vamwe vanhu vanongova neganda zviratidzo zve lupus, uye vanoonekwa kuti vane lupus-cuta yepepa yakasiyana-siyana ye lupus iyo, yoga, inokonzera kusvika 10 muzana yemapus kesi. Kunyange zvakadaro, zvipembenene zvemapurus lupus zvinowanikwawo muzvikamu zviviri kubva muzvitatu zvevanhu vanoonekwa kuti vane SLE.
Sezvimwe nemamwe marudzi e lupus, inyaya yomuviri wako inorwisa chivara chake chairo. Chikonzero chaicho chechimiro ichi hachizivikanwi, kunyange zvazvo vakadzi vanowanzova nacho uye zvinogona kufamba mumhuri.
Kusvuta fodya uye chiedza chezuva zvakave zvichiratidzwa kuti kuwedzere mamiriro acho ezvinhu.
Iko kune, kazhinji kutaura, zvitatu zvepine lupus, kusanganisira:
- Chirwere chisingagumi ( discoid lupus ): Mu discoid lupus, iyo inowanzojairika yenguva refu inonzi lupus, zvironda zvinopisa zvinokura pachiso chako, nzeve, scalp, uye kune dzimwe nzvimbo dzemuviri. Izvi zvipembenene zvinogona kunge zvakanyanyisa kana zvinyoro uye zvinowanzoora. Kazhinji hazvikuvadzi kana kuparadza. Vamwe varwere vanoridza zvipembenene uye kuputika pachikanda, vachiita kuti bvudzi riwedzere kukura munzvimbo idzodzo. Vanhu vazhinji vane discoid lupus havakwanisi. Ichokwadi, kuwana lupus kunowanzoonekwa kune varume kunze kwevakadzi.
- Subacute cutaneous : Zviratidzo zveganda zvekudzivirira ropa remapurusi zvinowanzonyorova. Vanhu vane chirwere ichi, ichochowo chimiro chavo chemapus, chiripo ne-reddish-purple plaques, iyo yakasimba uye yakasimudza, yakagadzirirwa maperembudzi ematehwe. Aya mahwendefa anowanikwa ari oga kana mumapoka uye anotarisana nehupamhi kubva pa5 mm kusvika 20 mm, kazhinji achioneka padombo, kusanganisira chikamu chepamusoro uye kumashure. Vanenge 10 kubva muzana yevanhu vane SLE vane chirwere chinonzi lupus. Zvimwe zvinodhaka zvinogonawo kukonzera subacute cutaneous lupus.
- Mucheka wakaoma: Uyu ndiwo rudzi rweganda rinoputika apo SLE yako iri kushanda. Zvipembenene zvinosanganiswa nemakumbo akaoma epidus zvinoratidzika sezvipfeko zvemukati mutsvuku mutsvuku pachiso, zvichiyeuchidza kupisa kwezuva-rinonzi butterfly rash . Izvi zvinogona kuonekwa pamakumbo, makumbo, nemuviri, uye zvinosvibisa. Kunyange zvazvo zvipembenene zvinogona kubudisa ganda, hazvirevi. Zvipfeko zvinowanzoonekwa panguva yekutsvaira kana mushure mokunge zuva rabuda.
Cherechedza kuti zvose zvisingagumi / kubvunzwa uye kusangana nemapirus anopus zvinogona kuitika zvakasununguka, kana kuti zvingave zviratidzo zveSLE, nepo lupus yakawanda isingaiti kunze kweSLE.
Neonatal Lupus
Neonatal lupus isiri yomuviri wekanguva yenguva inopinza inobata mwana kana mwana achangoberekwa. Haisi ichokwadi lupus: Inowanzoitika apo maantiantibodies amai vari kupa mwana wavo muUtero. Izvi izvi zvinogona kuchinja ganda, mwoyo, neropa recheche. Nenzira yakanaka, vacheche vakaberekerwa neonatal lupus havasi pangozi yakawanda yekuvandudza SLE gare gare muupenyu.
Vana vakawanda vane chirwere chinonzi neonatal lupus vachave nemapapu emucheka pakuberekwa. Zvimwe zvacho zvichaparara kazhinji mumwedzi miviri kusvika kumashanu. Kusvikirwa kwezuva kunowedzera kuunza kuitika.
Rashes, paavhareji, ichanyangarika pamwedzi mitanhatu kana kuti mushure mokunge, sezvo vanaamai vanozvimiririra vanonyangarika kubva kumucheche. Kurapa kwezvipembenene zveganda zvinowanzosipo kupfuura mafuta ekubatsira kubvisa kusuruvara kwemafuro.
Kunyange zvazvo zvisingawanzoitiki, vamwe vana vemadzimai vane lupus vanogona kuberekwa vane mwoyo wemwoyo usingagumi asi vanoporesa vachishandisa pacemaker. Izvi zvisingaoneki zvinogona kuonekwa mushure memavhiki 18 ekuzvitakura.
Childhood Lupus
Urwere lupus inobata pane imwe nzvimbo pakati pe5000 ne10 000 vana vasati vava nemakore 18 muUnited States. Iyo inowanzoonekwa kuti inenge iri pakati pemakore 11 ne15. Vana vezera ripi neripi vanogona kuva ne lupus, zvisinei, uye lupus inogona kukonzera vana vemarudzi ose kana rudzi.
Lupus inobata vana nenzira yakafanana nenzira iyo inobata vanhu vakuru pakuti inoratidzika pachayo zvakasiyana mumunhu mumwe nomumwe, kunyange zvazvo inoratidzika kuva neine humwe huri hunobatanidzwa. Izvi zvinogona kuva nokuti vana vave vachirwara kwenguva yakareba apo ivo pakupedzisira vanowanikwa.
Zviratidzo zvevana zvakangofanana nezviratidzo zvevanhu vakuru, izvo zvinowanzoitika ndezvokuneta uye kupera. Zviratidzo zvinoratidza zvirwere zvinosanganisira fever, butterfly rash, uye mafungiro epfungwa. Kazhinji zviitiko zvinowanikwa zvakajeka apo chirwere cheAA chirwere chinowanikwa mukuongororwa kwekuongorora .
Mishonga inogona kunge inoda kuve yakanyanyisa kurwisa vana, asi vanachiremba vanofanirwawo kungwarira pamusoro pemigumisiro yenguva refu yemishonga, kunyanya corticosteroids seforenisone. Vana vakawanda vanotungamirira hutano hwakanaka nehutano hwakanaka uye kutarisirwa.
Zviratidzo
Zviratidzo zvepakutanga uye zvisingaperi zvinoratidzira zviratidzo zvezvirwere zvakasiyana-siyana, izvo zvinogona kutungamirira kukusaziva. Zviratidzo zvekutanga zvinowanzobatanidza:
- Fever
- Malaise, kana kusagadzikana kwakawanda
- Joint pain
- Uturu hunorwadza
- Kuneta
Kazhinji, hazvisi kusvikira zviratidzo izvi zvichisanganiswa nezvimwe, zviratidzo zvakawanda zvinoratidza kuti vanachiremba vanowanzofamba pasi nemapirus. Zviratidzo izvi zvinosanganisira, asi hazvirevi kune:
- Ganda zvironda, zvipembenene, uye rashes, zvinonyanya kukosha kwemalalar, anowanzoti butterfly rash
- Anemia
- Kurema kwesimbi
- Nyaya dzemwoyo, dzakadai se pericarditis, myocarditis, uye endocarditis
- Pleuritis nemamwe mapapu kuvhiringidza
- Nyaya dzenhare, kusanganisira chirwere chisina kumira hematuria kana proteinuria (ropa kana mapuroteni mumuguta wako)
- Kugumburwa
Zvinokonzera
Lupus achiri chiitiko chisingazivikanwi kuvatsvakurudzi vezvokurapa. Chikonzero chaiicho chechirwere ichi hachizivikanwi, uye vazhinji vachiri kukakavadzana kana lupus chimwe chirwere kana kusanganiswa kwezvirwere zvakasiyana siyana.
Asi chibvumirano pamusoro penzira dzinonyanya kushandisa iyo lupus inowedzera inosanganisira:
- Genetics (ngozi dzinowanikwa nevabereki vako)
- Zvinhu zvinokonzera zvipenyu (kubva kumishonga, kushungurudzika, zvirwere, uye / kana kuonekwa kwezuva)
- Kuita kwezvinodhaka (munyaya yezvinodhaka-induced lupus)
Kuziva
Kana chiremba wako achifungidzira kuti une chironda che lupus erythematosus chete kana kuti pamwe chete ne systemic lupus erythematosus, zvinhu zvakawanda zvinoonekwa, kusanganisira:
- Physical test findings
- Zvitsva zvinowanikwa muraibhurari
- Antibody test
- Tissue biopsy
- Direct immunofluorescence
Pakupedzisira, nekuda kwezviratidzo zvakasiyana-siyana, zvinogona kuva zvakaoma kune chiremba wako kuti aongorore lupus , uye vanhu vazhinji vanotanga kuonekwa kuti makore mashanu mushure mekutanga kutanga zviratidzo. Nokudaro, kana iwe uchinzwa kuti iwe unenge uine zviratidzo zvinowirirana nekuongororwa kwe lupus, iva nechokwadi chekushanyira chiremba wako uye kuratidza izvi zvinonetsa.
Izvo zvinotaurwa nevaya vane lupus zvinowanzoenderana nehuwandu hwekubatanidzwa kwemuviri. Mune mamwe mazwi, chirwere chinotarisa nhengo panzvimbo peganda nemasangano here? Kuponeswa kwemapirus varwere vane hutachiona hwezviratidzo zviratidzo, hukuru hwekubatanidzwa kwemuviri, uye / kana chirwere chepfungwa , inogona kuva shoma kudarika avo vane ganda uye / kana chibatano chirwere chine chokuita ne lupus. Chikonzero chinowanzofa cherufu chinosangana ne lupus chirwere chinokonzerwa nekudzivirira muviri, chinokonzerwa nemishonga inoshandiswa kugadzirisa chirwere ichi, kunyanya kutanga kwechirwere chacho.
Kurapa
Parizvino, hapana mushonga we lupus. Chirwere chinotarisana nekudzora mhinduro ye autoimmune, kudzivirira kuputika uye kukanganisa kwegunhi, uye kubvisa zviratidzo:
- Kurapa zvinodhaka, zvakadai sokurwisa-kupisa zvinodhaka uye maune immune system modulators
- Lifestyle moderation, kusanganisira kuora muviri uye kudzivirirwa kubva kune zuva
- Acupuncture (uye mamwe marapirwo akasiyana)
- Physical therapy
Kune vamwe varwere vane unyoro vanotambudzwa, lupus zviratidzo zvinogona kutarisirwa sechirwere chisingaperi, asi chirwere chinogona kuva chakakomba uye kunyange kutyisidzira upenyu kune vamwe. Chirwere chacho hachifambi nenzira yakajairika, saka lupus varwere vanowanzosangana nezvinhu zvisingafanozivikanwi (flares) zvinoteverwa nenguva yekuregererwa-kunyange nekurapa.
Kutsungirira
Lupus inogona kuuya nemhando dzose dzematambudziko emumuviri uye nemanzwiro, kunyanya kana iwe uchangobva kuongororwa. Kudzidza kurarama nechirwere chako kunotora nguva nekuita, uye kunosanganisira zvinhu zvakadzidzisa iwe neaunoda nezvehutano hwako, kuzvichengeta nokuwana zvakakwana uye kudya zvakanaka, kudzidza kuti ungagadzirisa sei miromo yako, nekuwana rubatsiro.
> Sources:
> Femia AN. Neonatal uye Vanachiremba Lupus Erythematosus. Medscape. Yakaperedzwa June 8, 2016.
> Lupus Foundation of America. Kuongorora Lupus muvana. Yakavandudzwa August 16, 2013.
> Lupus Foundation of America. Lupus Facts uye Statistics.
> Sontheimer RD. Iyo Lupus Inobata Sei Ganda. Lupus Foundation of America. Yakapedzwa July 12, 2013.