Migumisiro yeGene Inopesana Pamutumbi
Cystic fibrosis (CF) chirwere chisingaperi, chinopfupisa hupenyu chinoitika sechikonzero chechiremera chemajini. Icho chinokonzerwa nehutachiona chinokanganisa simba remuviri yekuendesa mvura nemunyu kune uye kubva kumasero anogadzira kutuka, mbundu, uye majekiseni emuviri. Izvi zvinokonzera minyoro, iyo inowanzo yakaonda uye mvura mune vanhu vane hutano, kuti ive yakaoma kwazvo uye yakasimba.
Iyo miviri yakavhara yakavhara nhengo uye inovadzivirira kushanda zvakanaka. Migumisiro ye cystic fibrosis inogona kukanganisa nhengo dzakawanda uye zvirongwa.
The Cystic Fibrosis Effect
MuCF, nhengo dzakawanda dzomuviri uye maitiro zvinokanganisa, kusanganisira:
- Kuporesa (zviratidzo zvakadai semapapu nezvimwe zvivako pamuviri zvinokubvumira kufema uye kuparadzira ropa rinopa oksijeni mumuviri wose)
- Gastrointestinal system (inoratidzira mudumbu uye mumatumbo)
- Musculoskeletal system (musuru uye masaga)
- Genitourinary system (inobatanidzwa nhengo dzepabonde uye dzekuvhunga)
- Urongwa hwekubereka (urongwa hwezvikamu zvepabonde zvinosanganisira mvura, mahomoni, uye pheromones)
Nhengo Dzakasangana NeCF
Zvimwe zvikamu zvikuru zvakagadziriswa neCF zvinosanganisira mapapu, pancreas, chiropa uye gallbladder, matumbo uye nhengo dzinobereka.
Mapungiro
Kune mhando yekushambadzira isingawanzofambidzana pamwe chete nemugwagwa wekupema nekuda kwekutakura kwakashata kwe electrolytes mumigwagwa yendege.
Izvi zvinoputika nyore nyore uye zvakaoma kubvisa kubva kumhepo, izvo zvinogona kukonzera kudzima, zvinokuvadza alveoli (duku duku midzi) mumapapu uye kubvumira kune dzimwe nyika zvinyorwa kuti dzigadzire (zvichikonzera zvirwere zvisingagoneki mapapu).
Cystic fibrosis inokonzera matambudziko mumapapu kana hutu hwakaoma huchikwira uye hunoomerera mumhepo.
Apo izvi zvinoitika:
Nzira dzinopisa dzinovhara uye mweya haigoni kupfuura.
Bhakitiriya inokura mumucheka wekusungira uye inokonzera utachiona mumapapu, mumhino, uye sinus.
Nasal polyps inogona kukura mune dzimwe CF varwere.
Pancreas
Iyo panikresi chikamu chekudya kwekudya. Basa rayo nderekuchengetedza mapurojekiti anodiwa kugadzira zvokudya, uye hormone inonzi insulin inodzora shuga yeropa. Cystic fibrosis inokonzerawo kuti minyoro idzi dzive dzakaoma.
Apo izvi zvinoitika:
Madzika epaccatic anovharwa.
Mazimbe emuviri haagoni kukwanisa kupfuudza kupfigirwa.
Zvokudya hazvigadziri zvakakodzera uye muviri haugoni kudya mishonga.
Pakupedzisira, kuvhiringidzwa kwepancreas kunogona kukonzera kuora kunokanganisa masero ekubudisa insulini uye kudzivirira kuti vasabudisa insulini. Insulini haisviki kumasero, izvo zvinokonzera mazinga ega shuga kuwedzera. Iyi inonzi inonzi insulin-inokonzerwa nechirwere cheshuga, chinoitika munenge 15% yevamwe varwere veCF.
Chiropa neGallbladder
Kunyange zvazvo zvisingashamisi, kuvharidzirwa kwemafuro kunogonawo kuvhara bicy ducts yechiropa uye gallbladder uye kuvadzivisa kushanda zvakanaka.
Kana kuvhara kwemakumbo ari muchiropa ichienderera kwenguva yakareba, chiropa chinogona kuparadzwa zvachose.
Kana ducts yegorovladder yakavharwa, iyo nduru inowanzobviswa.
Utumbo
Dzimwe nguva, utumbo ndiyo nhengo yekutanga yekugadziriswa ne cystic fibrosis. Munenge makumi maviri kubva muzana yevana vose vachangobva kuberekwa neCF, miviri yakawanda yakaita mumatumbo ichikonzera kuvharwa kwehupenyu hwemukati hunozivikanwa seyeikisium yeus.
Zvibereko zvekubereka
Cystic fibrosis inobata nhengo dzekubereka dzevarume nevakadzi nenzira dzakasiyana uye nenzira dzinotevera:
- Varume inenge nguva dzose isingakwanisi kubereka nokuti mhepo yakakura mumharayi inoita kuti kuvharidzirwa kunodzivirira humuviri kuti usapinda.
- Vakadzi vanowanzokwanisa kubata pamuviri asi vangave vakaderedza kubereka nekuda kwekudzivirira kwechiberekero chechibereki chinodzivisa kupinda kwemuviri.
Kunobva:
Cystic Fibrosis. Vose Vana Vezvipatara. Health Information.