Cystic fibrosis (CF) chirwere chakagara nhaka chinokonzerwa nechiremera chemafu chinopinza simba remuviri wekutakura munyu uye mvura uye kubva kumasero. Izvi zvinokonzera huni hwehutu hwakawanda hunovhara mapapu uye nhengo dzekudya. Vanhu vazhinji vanoziva cystic fibrosis sehosha yemapapu asi hazvizivi kuti mucus buildup inokanganisa dzimwe nhengo pamwe chete.
Nhengo dzakabatwa neCF dzinosanganisira:
- Mapungiro
- Pancreas
- Chiropa
- Utumbo
- Sinuses
- Zvibereko zvinobereka
Cystic fibrosis ndechimwe chezvirwere zvinowanzozivikanwa zvegeneti uye zvinokanganisa 1 muvana 2500 vakaberekerwa muUnited States. Inowanzopararira pakati peCaucasians uye Hispanics uye inowanzoitika kuvanhu veAfrica kana kuAsia.
Zviratidzo
Zviratidzo zveCF zvinogona kusiyana zvichienderana nechetatu rechirwere uye nhengo dzinosangana.
Zviratidzo zvekutanga:
- Kuwedzera kudya kudya
- Kukura kukura
- Oily, zvinotyisa, zvinonyangadza zvinyuchi zvokufamba
- Ganda-inonaka paganda
- Kuramba uchikanganiswa
- Anogara achifema kupora
- Kuoma kufema kufema
Zviratidzo zvepamusoro zvinowanikwa nenzira yezvinetso, kusanganisira:
- Unexplained kuora kurasikirwa
- Chirwere cheshuga
- Pancreatitis
- Chiropa chechiropa
- Infertility
Kuziva
Cystic fibrosis inoratidzwa nekuongorora ropa, sweat kana kuti fetal cells kuti kuve kwezvinhu kana mazamu akawanikwa muCF varwere.
Kuberekwa
Kana vakatarisira vanoziva kana kuti vachifungidzira kuti vanogona kutakura mhando yeCF , anniocentesis kana chorionic villus sampling inogona kuitwa panguva yekuzvitakura kuziva kana mwana achava nechirwere ichi.
Mucheche
Iye zvino, makumi mana makumi mana anosanganisira cystic fibrosis mumatambudziko avo ekuberekwa kwekuzvarwa . Ropa rinotorwa kubva chitsitsinho checheche asati asvika kumba achibva kuchipatara. Ropa rinotumirwa kuhurumende yehurumende uye kana chiremera chacho chikaonekwa kuti chiremba wekuchiremba uye chiremba wehutano vemo vanozoziviswa.
Infancy uye Childhood
Kana zvisingawanikwi pakuberekwa, cystic fibrosis inowanzoongororwa mugore rokutanga kana maviri ehupenyu apo mwana anotanga kuratidza zviratidzo zvinowanzoitwa kunyevera. Chimiro chetsika ye cystic fibrosis i sweat test. Nemhaka yokuti muviri haukwanise kushandisa munyu wose unotora, vanhu vakawanda vane cystic fibrosis vanowanzonyanya kukura kupfuura yakakura yemunyu mu sweatshi ravo.
Mukuedzwa kwekutuka, magetsi anoshandiswa paganda remurwere kuti awedzere maziso e sweat. Tsvina inounganirwa uye inotumirwa ku laboratori kuti inyore munyu. I sweat test haisi inorwadza uye yakashandiswa kwemakore mazhinji kuti iongorore cystic fibrosis.
Kurapa
Hakuna mushonga we cystic fibrosis. Kurapa kunosanganisira kusanganiswa kwemishonga, kudya, kurovedza muviri, uye kurapwa kwakagadzirirwa kudzora zviratidzo uye kudzivirira zvinetso.
Mishonga inorayirwa kuti:
- Kudzivirira uye kudzora zvirwere zvokufema
- Chengeta mhepo yakasununguka uye ibatsire nekufema
- Kusunungura uye kubvisa nyota inonamatira
- Batsira muviri kutora mishonga
Zvirongwa zvekudya uye zvekudya zvinorayirwa kuti:
- Tora mavitamini asingagoni kuchengetwa
- Iva nechokwadi chokuti calori inowanikwa inosangana nepamusoro pemasimba ekuda simba
- Iva nechokwadi chekudya kwakakwana kwezvokudya kuitira kukura kwakanaka uye kubudirira
- Dzorera munyu unorasika kuburikidza neshutu
Kudzidzira uye kurapa kunorayirwa kuti:
- Simbisa mwoyo nemapapu
- Kusunungura uye kujekesa mucus
- Kuvandudza kutsungirira uye chimiro chemuviri
- Wedzera huwandu hweokisijeni inowanikwa mumasukisi
Zvinokonzera
CF inokonzerwa nechirema mu cystic fibrosis transmembrane conductance regulator ( CFTR ) gene. Basa reCFTR jena ndekuita mapuroteni anodzora kufamba kwemunyu nemvura mukati nekunze kubva mumasero ose mumitumbi yedu.
Mumwe nomumwe wedu ane makopi maviri eCFTR gene nokuti tine imwe kubva kune umwe neumwe wevabereki vedu. Dzimwe nguva CFTR gene inowanikwa kubva kuvabereki vedu isingawanzoitiki, asi izvozvo hazvirevi nguva dzose kuti tichava neCF.
Kana munhu akagara nhaka:
- 2 miviri yeCFTR yemazuva ose: Haazove neCF uye haazovi mutakuri.
- 1 yakakwana CFTR gene uye 1 isina kukodzera CFTR geni: Iye haazove neCF asi achabata jena risina kukwana uye anogona kupfuudza kuvana vake.
- 2 dzisina kukodzera CFTR mazamu: Iye achava neCF chirwere.
Kudzivirira
Nokuti cystic fibrosis chirwere chakazvarwa, hachigoni kudziviswa. Zvisinei, kuvapo kwechiremera CFTR geni kunogona kuonekwa nekutsvaga ropa. Asati abata pamuviri mwana , vakaroorana vanoziva kana kuti vanofungidzira kuti mumwe kana vashandi vose vanogona kutakura chiremera cheCF vanofanira kutsvaga mazano ekugadzirisa maitiro ekutsanangurira dambudziko ravo rekupfuura chirwere cheCF.
Kurarama NaCystic Fibrosis
Zvakanga zvisati zvaitika kare kare kuti vana vane cystic fibrosis vaisambogara vachiri kuyaruka. Iye zvino, zvakawanda zvinozivikanwa nezvechirwere chisingazivikanwi munguva yakapfuura. Idzi ruzivo rwakatungamirira kumagadziro emishonga anobvumira vanhu vane cystic fibrosis kuti vararame hupenyu uye hune hupenyu huri nani kusvika pakukura. Vanhu vanorarama ne cystic fibrosis vanofanira kutora matanho akawanda pamusoro pezvirwere. Vachange vachidawo kutora enzyme yekudya, inhaled antibiotics, nemimwe mishonga kwehupenyu hwavo hwose. Varume vanowanzobatwa nevakadzi, vakadzi vanogona kunge vashoma kubereka asi vachikwanisa kubata pamuviri.
Kana Mwana Wako Anozivikanwa
Chiremba wemhuri yako kana chiremba wevana vanogona kunge vachipfuurira kupa rubatsiro nerubatsiro rweboka revanyanzvi. Iye angangodaro anokutumira kune cystic fibrosis centre munzvimbo yako. Kana zvisina kudaro, kumbira kutumirwa. Cystic fibrosis nzvimbo dzinoshandiswa navanachiremba uye vashandi vezvoutano vanoona nezvechirwere uye vanogona kunyatsogadzirirwa kuongorora mwana wenyu uye kurayira kurapwa zvichienderana nekutsvakurudza kwezvino. Pakati penyika, mwana wako achaona boka revatsigiri kusanganisira pulmonologist (muchengeti wemapapu) uye nutritionist. Inonzi cystic fibrosis centre inzvimbo yakanaka yekuwana ruzivo nezvemunharaunda uye nyika inowanikwa iwe.
Kunobva:
Cystic Fibrosis. National Heart Lung uye Blood Institute: Dendaase uye Conditions Index. August 2007.