Lymphangiomatosis uye Lymph System

Lymphangiomatosis chirwere umo zvironda zvakawanda (lymphangiomas) kana kuti cysts zvinokura mu lymph system yemuviri. Kunyangwe izvi zvipembenene hazvisi kenza, dzinopinda mumuviri maviri uye dzinokonzera marwadzo, kunetseka kufema, uye zvimwe zviratidzo zvakasiyana siyana zvichienderana nepo zvinowanzoitika. Lymphangiomas inogona kukura mumapfupa, maitiro anobatana, uye nhengo dzomuviri, uye dzinogona kuvhiringidza, kudzivirira, kana kuparadza mishonga.

Chinokonzera lymphangiomatosis hachizivikanwe.

Lymphangiomatosis inonyanya kuongororwa mucheche nevana vaduku asi inogona kuitika chero ipi zvayo. Inobata vose varume nevakadzi vemarudzi ose. Nemhaka yokuti lymphangiomatosis haigoni uye inonetsa kuongorora zvakanaka, hazvizivikanwi kuti vanhu vangani vanovhiringidzwa nayo munyika yose.

Zviratidzo

Zviratidzo zve lymphangiomatosis zvinotarisa pane kuti matumire ari kukura mumuviri.

Nokufamba kwenguva, imwe kana mamwe mapfupa angashandurwa ne lymphangioma tissue, inozivikanwa sehosha yeGorham. Lymphangiomas hairi kukura muuropi nokuti lymph system haina kuwedzera mairi.

Kuziva

Kuongororwa kwe lymphangiomatosis kunobva pane zviratidzo uye kuvapo kwemaitiro akawanda emumuviri. CT (computed tomography) scan uye magnetic resonance imaging (MRI) inoshandiswa kuongorora chirwere chacho. Chiyero chemuviri (biopsy) chinotorwa kuti chibatsire kusimbisa kuti maronda ane lymphangiomas.

Kurapa

Lymphangiomatosis inowedzera kunonoka kupfuura nguva. Sezvo maronda ari kukura, anogona kukonzera zviratidzo zvakakomba, zvimwe zvingave zvinopisa upenyu, zvakadai sekuita kuti mvura inotonhora iunganidze pamapapu anorega kufema. Kugadziriswa kubviswa kwemakumbo kunogoneka, asi mamwe mvere dzinogona kuva dzakaoma kubvisa zvachose kana dzakapararira. Mishonga inonzi Intron A (interferon alfa), chemotherapy, kana remishonga inonzi radiation inogona kubatsira pakurapa chirwere chacho. Dzimwe mishonga kana kuvhiyiwa zvinogona kubatsira pakubvisa zvimwe zviratidzo kana zvinetso zvinokonzerwa ne lymphangiomatosis. Semuenzaniso, tube inogona kuiswa mubhokisi (thoracentesis) kuti ibvise mvura yakawanda, kana kuti kuvhiyiwa kunogona kuitwa pamutsara kuti udzikinure mitsetse.

Sources:

> "Pamusoro peLymphangiomatosis." Lymphangiomatosis & Gorham's Disease Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, & Reginald Munden. "Generalized Lymphangiomatosis." American Journal of Roentgenology 182 (2004): 1068.

> Rostom, A Y. "Kurapa kwetroacic lymphangiomatosis." Archives of Diseases in Childhood 83 (2000): 138-139.