Nguva yakawanda inoratidzirwa nepamusoro pemaplatelets eropa
Chinokosha thrombocythemia (ET) chirwere chisina kujairika umo mafuta emuti anounza maplatelet akawanda. ET chikamu chechikwata chezvirwere zvinonzi myeloproliferative disorders, boka rematambudziko rinoratidzwa nekuwedzera kwekugadzirwa kwemhando chaiyo yeropa rega.
Platelets ndiyo masero anokonzera kuvhara ropa ayo anonamatira pamwe chete panzvimbo yekudzivirira kana kukuvara kuitira kuti asiye kubuda ropa.
Mune vanhu vane ET, kuvapo kweplatelet zvakanyanya kunogona kuva dambudziko, zvichiita kuti kusagadzikana kwekugadzirisa mukati meropa mudziyo (chiitiko chinonzi thrombosis ).
Kunyange zvazvo chikonzero chaiyo che ET chinenge chisingazikamwi, vanenge 40 kusvika ku50 muzana yevanhu vane chirwere vane genetic mutation inozivikanwa seJAK2 kinase. ET ndiyo chirwere chisina kujairika, chinokonzera pasi pevatatu kubva kune 100 000 vanhu pagore. Inogadzirisa vakadzi nevarume vemarudzi ose asi vanoita kuti vaonekwe kune vanhu vakuru vanopfuura 60.
Zviratidzo zve Essential Thrombocythemia
Vanhu vane hutachiona hunokosha vanowanzotaridzirwa mushure mekuvandudza zviratidzo zvakanangana neropa rekuvhara . Zvichienderana nokuti pane chivharo chiripi, zviratidzo zvinogona kusanganisira:
- Headache
- Uchechezi kana kuchena
- Kushaya simba
- Kupera
- Chest pain
- Kuchinja kwemaono kunochinja
- Unhu, kubwinya, kurira, kana kunzwa kunopfuta mumaoko netsoka
Zvishoma nezvishoma, kubuda kwemazuva ose kunogona kukura semugumisiro we ET.
Kunyange zvazvo pasi shoma yakawanda inogona kukonzera kubuda ropa nekuda kwekushayiwa kwekuvhara, maplatelets akawanda anokwanisa kuva nemigumisiro yakafanana neipi yeprotein inoda kuisungirira pamwe chete (inonzi von Willebrand factor) inogona kupararira zvakare yakaonda kuti ibudirire. Apo izvi zvinenge zvichiitika, kuputika kusina kuchena, nosebleeds, kubuda kubva pamuromo kana gums, kana ropa mune chigaro chinogona kuitika.
Kuumbwa kweropa clots dzimwe nguva kungava kwakakomba uye kunogona kutungamirira kumarwadzo emwoyo, kurohwa, kushungurudzika kwechikafu chinokanganisa ("mini-stroke"). Chirwere chakawedzerwa chinowanikwawo munharaunda inopoteredza 20 muzana yematambudziko nekuda kwekudziviswa kweropa rekupararira.
Kuongorora Kukosha Kwechirwere Chetachiona
Chinokosha thrombocythemia inowanzoonekwa panguva yekuongorora ropa nguva dzose kune vanhu vasina zviratidzo kana zviratidzo zvisinganzwisisiki, zvisingaiti (zvakadai sokuneta kana kuti musoro). Chero huwandu hwehuwandu hweplateti dzinopfuura 450 000 pam microliter hunofungidzirwa kuva mutsvuku. Avo vanodarika mamiriyoni nemaundi microliter vanobatanidzwa nehuwandu hwehutachiona hwekunyangadza kana kubuda ropa.
Chirwere chemuviri chinogona kuratidzira kuwedzera kwepleen kunoratidzwa nekutambudzika kana kuzara mukati mechikamu chepamusoro chepamusoro chinogona kupararira kuruboshwe rworuboshwe. Kuenzanisa kwemajeni kunogonawo kuitwa kuitira kuona JAK2 mutation.
Kuongororwa kwe ET kunonyanya kusabatanidzwa, kureva kuti chero chimwe chikonzero chepamusoro cheplatelet kuverengwa chinofanira kutanga chisina kubviswa kuitira kuti chigadziriswe chekujekesa. Mimwe mitemo inosanganiswa nepamusoro peplatelet count inosanganisira polycythemia vera , isingaperi myeloid leukemia , uye myelofibrosis .
Kurapa Kunonyanya Kuita Thrombocythemia
Kurapa kwechirwere chinokonzerwa nehutachiona kunobva kunyanya kukura kwokuti kukwirira kweplatelet kunowanikwa sei uyewo mukana wezvinetso.
Havasi vanhu vose vane ET vanoda chirwere. Vamwe vanongoda kuongororwa kuti vaone kuti chirwere chacho hachina kuipa.
Kana zvichidiwa, kurapwa kunogona kusanganisira aspirin yezuva nezuva kune avo vanofunga kuti vari pangozi yakaderera. Kune avo vari pangozi yakakura (zvichienderana nekukwegura, nhoroondo yezvokurapa, kana mararamiro akaita sekusvuta kana kuneta) inogona kubatsirwa nemishonga yakadai sa hydroxyurea, anagrelide, kana kuti interferon alpha, iyo yose inogona kuderedza mapeletletlet nhamba.
Mune dambudziko, plateletpheresis (imwe nzira iyo ropa rinoparadzaniswa muzvikamu zvaro pachavo) inogona kuitwa kuti ikurumidze kuderedza platelet count.
> Kwakabva:
> Bleeker, J. naHogan, W. "Thrombocytosis: Kuongorora Kuongororwa, Kuongororwa Kwengozi yeTromboti, uye Njodzi-Inotungamirirwa Mazano." Thrombosis. 2011; chinyorwa ID 536062.