Polymyositis Inobatsira Kuboka Guru rezvirwere Anozivikanwa seMyositis
Polymyositis is systemic, chirwere chinoputika chirwere, chinonyanya kuonekwa nemusana utera. Icho chikamu chechirwere chinotumidzwa chinonzi myositis, zvinoreva kuvhiringidza kwemisumbu. Polymyositis inowanzokonzera misumbu iri pedo nemutumbi wemuviri, asi nekufamba kwenguva mamwe mitsipa inogona kuitika. Kazhinji, polymyositis inokura zvishoma nezvishoma, uye iyo inogona kukura kune ani zvake, kusanganisira vana, haiwanzobata vanhu vane makore pasi pemakore 18.
Kazhinji kazhinji, inobata vanhu pakati pemakore makumi mana nemakumi matanhatu. Polymyositis inokanganisa vakadzi vakawanda kazhinji kupfuura varume, nehuwandu hweviri kusvika kune imwe.
Dermatomyositis iyi inokonzera kupisa muviri kune polymyositis, musiyano uri kuti dermatomyositis inobatawo ganda. Polymyositis inogona kuitika pamwe chete nemamwe makondombera, kusanganisira lymphoma , kenza yemazamu , kenza yemapapu , kenza yemuviri , uye kenza yemaroni . Polymyositis inogona kuitika nedzimwe zvirwere zverheumatic, zvakadai se systemic sclerosis (scleroderma), yakavhiringidza zvirwere zvehutu , rheumatoid arthritis , systemic lupus erythematosus , uye sarcoidosis .
Chikonzero chePolymyositis
Kunyange zvazvo chikonzero chepolymyositis chinonzi hachizivikanwe, zvinoratidza kuti hutano ndicho chinhu. Vatsvakurudzi vanotenda kuti kushandiswa kwezvimoto kune musimba kunowanikwa kune vanhu vane maitiro ekugadzirisa muviri. HLA subtypes -DR3, -DR52, uye -DR6 inoonekwa seyobatanidza kune zvakatemerwa.
Ikoko kunogonawo kuve chiitiko chinokonzera, zvichida chirwere chemusitis kana kenza yekare isati yavapo.
Zviratidzo zvePolymyositis
Utsi husina simba, sezvataurwa pamusoro apa, ndiyo chiratidzo chinowanzoonekwa. Utachiona husina simba hunobatanidza nepolymyositis hunogona kufambira mberi kwemavhiki kana mwedzi. Maererano neMerick Manual, kuparadzwa kwe50 muzana yemasikironi emasumbu kunokonzera zviratidzo zvishoma nezvishoma, zvinoreva, panguva iyoyo myositis yakanyatsokura.
Matambudziko anowanzoshanda anowanikwa ne polymyositis anosanganisira kukwira kubva pachigaro, kukwira makwande, nekusimudza maoko. Kushaya simba kwemasumbu emapapu uye epafudzi kunogona kuita kuti munhu arara-akasungwa kana kuti ane magwari-akasungwa. Kana mitsipa yemutsipa ichibatanidzwa, zvingave zvakaoma kusimudza musoro wako kubva pamutsiro. Kubatanidzwa kwemafuro emakumbo uye eesophageal kunogona kuchinja kumedza. Zvinofadza, misumbu yemakumbo, tsoka, uye chiso hazvibatanidzi mu polymyositis.
Ikoko kunogona kuve nekubatanidzwa kunobatanidzwa semunhu munyoro wepolyarthralgia kana polyarthritis . Izvi zvinowedzera kukura mu-subset ye polymyositis varwere vane Jo-1 kana mamwe antisynthetase antibodies.
Zvimwe zviratidzo zvine chokuita nepolymyositis zvinogona kusanganisira:
- generalized fatigue
- kukurumidza kufema
- Inzwi risina kunaka kubva pamusana wemakumbo
- fever
- kurasikirwa nechido
Kuongororwa kwePolymyositis
Sezvo kune chirwere chipi nechipi kana chimiro, chiremba wako achaongorora nhoroondo yako yezvokurapa uye ozoongorora zvakakwana mumuviri sechikamu chekuongorora chirwere. Kuongorora ropa kunogona kunge kwakarayirwa kutarisa kuvepo kwezvimwe zvinonzi autoimmune antibodies uye kuona kusina kuvhiringidza kwakakwana . Electromyography uye nerve test conduction zvinogona kupa chiremba zvine ruzivo rwekuongorora ruzivo, zvakare.
MRI yemisungo yakakanganiswa inowanzorairwa. Uyezve, muyeso unogona kuongorora myoglobin, puroteni mumasero emasumbu anokonzerwa muropa uye acheneswa neitsvo apo musuru inokuvara. Ropa kuongororwa kuti uone kutaridzika kwemaitiro enyoka emuviri, zvakadai seCK uye aldolase, inogona kurairwa uye inoitwa. Nekukuvara kwemisumbu, mazinga emasikirisi emasumbu anowanzokwiridzirwa. Imwe nzira yekuongorora ropa, iyo ANA (antinuclear antibody test) , inofadza kusvika kusvika ku80 muzana yevanhu vane polymyositis.
Pakupedzisira, tsvina yemasumbu inogona kuitwa kuitira kuti ibudise hutano hwepolymyositis.
Bhiopsy inokurudzirwa isati yatanga kurapwa kuitira kuti zvimwe zvirwere zvemasumbu zvinogona kubudiswa kunze.
Kurapa kwePolymyositis
Corticosteroids pamvura yakakwirira ndiyo inotangira mishonga yekurapa kwepolymyositis kuti kuderedza kuputika mumisungo. Kana izvo chete zvisingakwanisi, zvirwere zvemuviri zvinogona kuwedzerwa kuhurongwa hwekurapa. Immunosuppressants inogona kufungwa inosanganisira methotrexate (Rheumatrex), azathioprine (Imuran), mycophenolate (CellCept), cyclophosphamide (Cytoxan), rituximab (Rituxan), cyclosporine (Sandimmune), uye IV immunoglobulin (IVIG).
Polymyositis inosangana nekenza kazhinji inenge isingagamuchirwi ne corticosteroids. Kumhanyirira kubviswa, kana zvichibvira, kunogona kubatsira zvikuru mukenza-yakabatana myositis maitiro.
Shoko Rinobva
Nekurapwa kwepakutanga kwepolymyositis, kuregererwa kunogona. Makore mashanu ekupona kwevanhu vakuru vane polymyositis, maererano neMerck Manual, ine chikamu che75-80 muzana. Rufu runogona kuguma nemigumisiro yekukurira uye kufambira mberi kwemaviri kusasimba. Vanhu vane chirwere chemwoyo kana chemapuraneti vanoita sevanowedzera kuwedzera. Izvo zvinogonawo kutaurwa nezvepolymyositis varwere vane kenza.
Cancer screenings inokurudzirwa kuti ipo polymyositis varwere vane makore makumi matanhatu nekure. Funga nezvekudikanwa kwekugadzirisa kenza kuongorora. Kuwana chirwere chisina kufanirwa chinogona kuva chinhu chinoita kuti uchinje kufungidzira kwako nepolymyositis.
> Sources:
> Cleveland Clinic, Polymyositis, http://my.clevelandclinic.org/health/articles/polymyositis. Yashandurwa Sep. 2015.
> Hajj-ali, RA., MD. Polymyositis uye Dermatomyositis. Merck Manual. Professional Version. Yakadzokororwa / Yakarongwa muna June 2013.
> MedlinePlus, Polymyositis - Mukuru. Yakarongwa naGordon A. Starkebaum, MD. January 20, 2015.
> Nagaraju K, et al. "Kuvhiringidza Zvirwere zveMuscle uye Zvimwe Myopathies." Kelley's Textbook yeRheumatology. 2016.