Ndeapi Marudzi Akasiyana-siyana eScleroderma (Systemic Sclerosis)?

Scleroderma Haisi Chirwere Chimwe Chete

Scleroderma chiratidzo cheboka rezvirwere izvo zvakaoma nekukura kusinganzwisisiki kwezvigunwe zvinobatanidza , mhuka inotsigira ganda uye nhengo dzomukati. Vakawanda vanonzi rheumatologists vanotaura nezvechirwere se systemic sclerosis uye kugadzirwa kweganda se scleroderma. Scleroderma chaizvoizvo zvinoreva "ganda rakaoma," rinobva mumagiriki echiGiriki mazwi sklerosis (zvinoreva kushanda) uye derma (zvinoreva kuti ganda).

Scleroderma inofungidzirwa sechirwere cherheumatic (mamiriro ezvinhu anoratidzwa nekuputira nekurwadziwa mumisungo, mafundo, kana michina ye fibrous) uye chirwere chinogadzirisa zvirwere.

Mamwe maitiro e scleroderma ane chirwere chisina kujairika chinowanzoita kuti ganda rive rakaoma uye rakasimba. Mimwe mhando yakanyanya kuoma, inokanganisa mitsipa yeropa uye nhengo dzomukati dzakadai semwoyo, mapapu, uye itsvo.

Pane zvikamu zviviri zvakakosha zve scleroderma: localized scleroderma, iyo inokanganisa zvimwe zvikamu zvemuviri uye inosanganisira linear scleroderma uye morphea, uye systemic sclerosis, iyo inobata muviri wose.

Localized Scleroderma

Localized types of scleroderma inosanganisira ganda uye mamwe maitiro akafanana, uye dzimwe nguva musuru pasi apa. Nhengo dzomukati hazvibatsiri.

Localized scleroderma haikwanise kufambira mberi kuhutachiona hwechirwere. Nzvimbo dzakasiyana-siyana dzinogona kuvandudza nekufamba kwenguva, asi ganda rinoshanduka rinoitika apo chirwere ichi chiri kushanda chinogona kugara chiripo.

Zvinogona kunge zvakakomba uye zvisingabatsiri.

Kune mhando mbiri dzemunzvimbo yakagadzirwa scleroderma: morphea uye yakasiyana.

Morphea

Zvitsvuku zvakasvibirira zveganda izvo zvinokonzera kuti zvive zvakasimba mashizha akafanana zvakasiyana nemhando ye morphea ye localized scleroderma. Nzvimbo dzemakate acho ndeye nyanga dzenzou, dzine mitsara yakasviba. Mavara acho anogona kuitika pachipfuva, mudumbu, kumashure, chiso, maoko, uye makumbo.

Izvo zvipfeko zvinowanzovhara zvishomanana uye vane vhudzi duku kukura. Morphea inogona kuwanikwa munzvimbo (inogumira kune imwechete kana kuti mapepa akawanda, kubva kubva hafu-inch kusvika masendimita gumi nemaviri muhupamhi) kana huwandu (zvivara zveganda zvakaoma uye zvakajeka uye zvinopararira pane zvikamu zvikuru zvemuviri). Morphea kazhinji inopera mumakore matatu kusvika mashanu, asi vanhu vanogona kunge vane ganda rakasviba ganda uye, kunyange zvisingawanzovi, musimba urombo huripo.

Linear

Mutsara mumwechete wakasiyana kana bhande rakasvibiswa, ganda rinenge risina kuchena rinowanzofananidzira rudzi rwakafanana rwemunharaunda scleroderma. Mutsara unowanzosvika pasi ruoko kana gumbo asi unogona kumhanya pasi pehuma.

Systemic Sclerosis

Systemic sclerosis haina kungoita kechena chete asi inosanganisira midziyo yeropa uye nhengo dzakakura.

CREST Syndrome

Vanhu vane systemic sclerosis vane zviratidzo zvose zvinotevera, inozivikanwa seR CREST syndrome, inotsanangurwa:

Chikwereti Scleroderma

Systemic sclerosis yakakamurwa kuva mapoka maviri, asingakwanisi uye akapararira.

Kakawanda scleroderma inowanzoita zvishoma nezvishoma uye inongororwa kune dzimwe nzvimbo dzeganda, zvakadai seminwe, maoko, chiso, zviso zvishoma, nemakumbo.

Raynaud's phenomenon inowanzotarisana kwemakore makore asati agadzirwa kweganda. Vamwe vanotarisana nezvinetso zveganda pamusoro pemuviri wemuviri unoratidza kuvandudza kwemazuva, zvichisiya chete chiso uye maoko nemaoko akaoma, akaoma. Calcinosis uye telangiectasias dzinowanzotevera.

Chisingatarisirwi scleroderma dzimwe nguva chinonzi CREST syndrome nekuda kwezvakawanda zveRESTEST zviratidzo kune ava varwere.

Diffuse Scleroderma

Kuparara kwe scleroderma kunowanzova nekutanga kamwe kamwe. Ganda rinokura rinokura nokukurumidza uye rinofukidza muviri wemiviri, kazhinji mumutambo wakaenzana. Nhengo dzakawanda dzomukati dzinogona kuparadzwa. Zviratidzo zvinowanzoitwa nediffuse scleroderma zvinosanganisira:

Ganda rinogona kuvhurika, rinenge richipenyera, uye rinonzwa rakasimba uye rinotyisa. Kuparara kwekupararira kwechirwere chinonzi scifoderma kunowanikwa kwemakore mashomanana.

Mushure memakore anenge matatu kusvika mashanu, varwere vanowanzogadzikana, chikamu apo kufambira mberi kunoita sediki uye zviratidzo zvinopera-asi zvishoma nezvishoma, ganda rinoshanduka rinotanga zvakare. Chikamu chinozivikanwa sekuchera kunowanikwa, panguva iyo inonzi collagen shoma inogadzirwa uye muviri unozvicherechedza wega kuwedzera kwekorogen.

Nzvimbo dzekupedzisira dzakasimbiswa dzakanyatsogadziriswa. Rimwe ganda revarwere rinodzokera kune izvo zvinoita sezvakanaka asi ganda revamwe rinowonda uye rakaoma. Varwere vane diffuse scleroderma vanotarisana nevanonyanya kutsoropodza kana vakakurira zvinetso zvakakomba muitsvo, mapapu, mwoyo, uye maraga.

Pasingapfuuri chikamu chetatu chevarwere vane chirwere chinopararira che scleroderma vanokura matambudziko akaoma munhengo dzinotaurwa.

Systemic Sclerosis Sine Scleroderma

Vamwe vanoziva systemic sclerosis sine scleroderma senhengo yechitatu ye systemic sclerosis. Iyi fomu inobata miviri yeropa uye nhengo dzomukati, asi kwete ganda.

Shoko Rinobva

Zvakakosha kunzwisisa rudzi rwe systemic sclerosis iwe unowanikwa kuti uwane sarudzo yakanakisisa inoshanda kwauri. Kunyange zvazvo pasina mushonga we systemic sclerosis kana scleroderma, pane zvingasarudzwa zviripo kuti zvikubatsire kutarisira mamiriro ako, kuderedza zviratidzo, uye kuramba uchirarama zvakanaka.

> Sources:

> Scleroderma Handout On Health. NIAMS. http://www.niams.nih.gov/Health_Info/Scleroderma/default.asp

> Firestein GS, Kelley WN. Kelleys Textbook of Rheumatology . Philadelphia, PA: Elsevier / Saunders; 2013.