Vabereki Vatsva Vanogona Sei Kuzorodza Pasinei Nekurwadziwa Kwevana Kwavo
Zvinhu zvishomanana zvinorwadza mwoyo seine mwana ane chirwere chakakomba chisingabatsiri. Asi kana dzimwe kukanganisa kunogona kukonzera zvinetso zvakakomba mukukura kwevana, nekutenda kwete zvose kugumburwa kunokanganisa vatsva zvakanyanya.
Generalized Epilepsy Syndromes mucheche
Kukanganiswa kwemazuva ose kunodanwa nokuti kunoratidzika kuitika mumuviri panguva imwe chete.
An electroencephalogram (EEG) inoratidza kushanda kwemajeri kusina kukodzera kunosanganisira uropi hwose panguva imwe chete.
Benign Neonatal Kugumburwa
Kune mhando mbiri dzehutachiona hwehutachiona husina matambudziko makuru kune mwana achangoberekwa. Nhengo dzemhuri dzinosangana neonatal (BFNS) uye bhendi idiopathic neonatal seikudzika dzinowanzobatanidzwa nekanaka.
BFNS inowanzotanga mumasvondo mashomanana ekutanga ehupenyu nechinguva chiduku asi kakawanda. Pakati pemagunha, mwana wacho akajairika. Chikamu chakakosha pakuita kuti chiongororwa cheBFNS chiitiko chemhuri chekukundwa. BFNS inotora nhaka mumutambo unotenderera, unoreva kuti kana mwana aine, mumwe wevabereki angave anewo zvakare. Kunyange zvazvo kugumburwa kunowanzogadzirisa kubva pakutanga kusvika pakati pemucheche, anenge 8 kusvika ku16 muzana yevana vanoenderera mberi kukura kuora mwoyo mushure mehupenyu.
Bhenign idiopathic neonatal seizures inowanzoitika mune dzimwe nzira dzese dzese dzinenge dzichizvarwa. Zviratidzo zvinowanzotanga pazuva rechishanu rehupenyu uye dzinonyanya kuoma, dzimwe nguva dzinopera muhupenyu hwehupenyu . Mushure memaawa makumi maviri nemaviri, kukanganisa kunovandudza.
Generalized Epilepsy neFririle Seizures Plus
Chirwere chechirwere chinokonzerwa nefibrile seizures pamwe (GEFS +) chinogona kukanganisa vana kubvira paucheche kusvika pakuyaruka, asi nerufaro, kupera kwemafiriri kazhinji kunenge kusingabatsiri uye kazhinji haisi kutungamirira kune mamwe matambudziko. Muna GEFS +, kunyange zvakadaro, kupera kwemafiriri kunopfuura kudarika makore emakore matanhatu uye kunowiriranawo nemamwe marudzi ekugumburwa. Kufanana neBFNS, GEFS + inotora nhaka mumutambo mukuru unotenderera. Asi nekuda kwezvinonzi kushanduka kushanduka kwekuchinja kwemuviri, pakati pe20 kusvika ku40 muzana yevabereki vangave vasina zviratidzo, kunyange kana vane mutendi wakashandurwa.
Vazhinji vana vane GEFS + vachavandudza, kunyange kusvika kusvika 30 muzana inogona kuwedzera kuora mwoyo kwakanyanya.
Myoclonic Astatic Epilepsy (Doose Syndrome)
Myoclonus inonyanya kushanduka musimba kune zvikonzero zvakasiyana-siyana, kusanganisira kuora mwoyo kwekurwadziwa. Myoclonic astatic epilepsy (MAE) inokanganisa nevana mu10 000 vana. Mukuwedzera kune myoclonus, vana vane zvimwe zvinotambudza uyewo kusanganisira atonic kugumburwa, umo vanobva vaenda. Doose syndrome inogona kutanga semwedzi minomwe, kana kuti inopera makore matanhatu. An electroencephalogram (EEG) inogona kubatsira mukugadzirisa.
Doose syndrome haisi nguva dzose inobatanidzwa nekanaka. Nepo huwandu hwevana vane MAE huchakura zvakanaka, kusvika 41 kubva muzana ichava neIQ-borderline kana chirwere chepfungwa. Vamwe vachava nekuputika kwekufa.
Chikamu Chine Chirwere Chirwere Chirwere Chidiki Mucheche nevana
Kusiyana nehuwandu hwemagetsi, kukanganisa kunokanganisa kunotanga mune imwe nzvimbo uye kunokwanisa kupararira kunosanganisira mamwe mativi europi. Kunyange zvazvo dzimwe nguva kukanganiswa kwechikamu kunokonzerwa nehutano hwepfungwa husina kufanana nehupenyu hwemudziyo husina kukwana, dambudziko dzimwe nguva kunepo kubva pakuberekwa.
Benign Infantile Familial Convulsions
Bhenign vana vekudzikana kwemhuri vanovhiringidza kunotanga apo mwana ari pakati pemwedzi we3 kusvika kune gumi nemaviri. Mwana wacho anobva atanga kufamba achibva atanga kusvetuka kwemakumbo anenge 5 kusvika 10 pazuva. Sezvo zita racho rinoreva, chirwere chekubatwa chinokwana nhaka. Pane chimiro chemuitiro pane EEG iyo inogona kubatsira pakuita kuti kuongororwa. Kazhinji, kugumburwa kunogadzirisa zvese kana mwana achikura, uye kubudirira kunowanzoitika.
Simba Rakasiyana Nechirwere Mucheche
Iyi seizure syndrome inofanana chaizvo neyakanaka yekushungurudzika kwemhuri yekurwadziwa-mutsauko mukuru ndeyokuti mumamiriro aya, genetic mutation haisi kuonekwa.
Childhood Epilepsy ne Occipital Paroxysms (Panayiotopoulos Syndrome)
Ichi chirwere chinowanzowanikwa muzvidzidzo zvekuchechera vana asi zvinogona kuitika mushure megore rimwe chete. Kubatwa kwepanayiotopoulos syndrome kunonyanya kusanganiswa ne dysautonomia , ine zviratidzo zvakadai sokunyunyutira, kurutsa, uye kutadza. EEG ine chimiro chemafungu akaoma pamusana we musoro, unonzi occipital paroxysms. Kukanganwa kazhinji kunogadzirisa mumakore 1 kusvika ku2.
Benign Childhood Chirwere neCentrotemporal Spikes (Benign Rolandic Epilepsy)
Bhenign rolandic epilepsy inowanzotanga muvana vemakore manomwe kusvika kune gumi, asi dzimwe nguva inogona kuonekwa kuvana vaduku segore rimwe chete. Kukanganiswa kunobatanidza ne drooling uye kuchinja kwekunzwa. Kukanganwa kazhinji kunokonzerwa nekudzungaira kana kurara. IEEG inobatsira zvikuru mune iyi syndrome, sezvo inoratidza mazai akajeka munzvimbo dzeprotemporal dzeuropi. Nepo izvi zvinotyisa zvinotyisa kuvana (avo vanoramba vakasvinurira mukati), havasi nengozi uye kazhinji vanozvigadzirisa pachavo nezera remakore gumi nematanhatu.
Pasi Pasi
Sezvawakaona, nepo huwandu hwekugadzirisa hutachiona hunova nemigumisiro yakanaka, vamwe vavo vanowedzera njodzi yokuti mwana haazove noupenyu huripo. Sezvo zvinosuruvarisa sezvino izvi, zvichienzaniswa nedzimwe s syndromes umo mararamiro asina kunaka anonyatsova nechokwadi, idzi syndromes dzinobvumira vabereki kuti vave nehuwandu hwekutarisira.
Kunyange zvazvo vabereki vashomanana vangambodikanwa kuti mwana wavo awane dambudziko, uye akawanda emishonga inopfuura pamusoro, zvinowanzoitika ndeyehupenyu huripo - dzimwe nguva kunyange pasina mushonga. Kuisa pfungwa pazvinhu zvakanaka, asi kunyatsogadzirisa zvirongwa zvakanyanya kuitika, zvinogona kubvumira vana kuti vararame hupenyu hwakanakisisa hwavanokwanisa nehutupa.
Sources:
Elaine Wirrell, Katherine C. Nickels. Continuum: Chirwere, Bhuku 16, Nhamba 3, June 2010.
Gerald M Finichel. Clinical Pediatric Neurology. 6th Edition. Sanders-Elsevier, 2009.