Kana iwe kana munhu waunoda akaudzwa kuti une Rasmussen's syndrome kana encephalitis raRasmussen, iwe unogona kuva neruzivo rwekuzorodzwa pakuziva kuti iwe pakupedzisira une chirwere chinotsanangura zviratidzo zvako. Asi iwe unogonawo kuva nehanya zvikuru pamusoro pezvaunotarisira kubva pane izvi.
Rasmussen's syndrome kana encephalitis raRasmussen haisi isiri, uye inofungidzirwa kuti panogona kuva nevashoma kudarika vanhu 2000 vanorarama nemamiriro aya muUnited States.
Pasinei nokuti hazviwanzoitiki, pane kurapwa kweRasmussen's syndrome uye encephalitis raRasmussen, kunyange zvazvo kunewo mukana wakareba kuti iwe ucharamba uine humwe hurefu kwenguva yakareba kunyange mushure mekunge mawana kurapwa uye kuti muchada kuchengeta kurapwa kwemakore akawanda.
Chii chinonzi Rasmussen's Syndrome uye Rasmussen's Encephalitis?
Rasmussen's syndrome ndiyo izwi rinoshandiswa kurondedzera mamiriro ezvinhu chero nguva panguva yechirwere chacho. Zvinotendwa kuti raRusmussen's syndrome dzimwe nguva rinokonzerwa kana kutungamirirwa nerudzi rwekuputika kweuropi inonzi Rascussen's encephalitis.
Encephalitis yeRasmussen pachayo inenge iyo iyo uropi ine simba rakasimba rekuzvidzivirira mumuviri inokonzera kukanganiswa kwakanyanya kweuropi kushanda kune rumwe rutivi. Izvi zvinogona kuratidza sekutambudzika, kushaya simba, matambudziko emutauro kana kukanganisika kwepfungwa (kufunga uye kugadzirisa matambudziko).
Kazhinji, kuputika kunobatsira hakusi kuramba kwenguva refu, asi mushure mokunge kutuka kugadzirisa, vanhu vanowanzoramba vachiona zviratidzo. Zviratidzo izvi zvinogona kunzi raRusmussen's syndrome panzvimbo yeRusmussen's encephalitis kana pasina humwe uchapupu hwekuputika kwehutano muuropi.
Rasmussen's syndrome ndeye chirwere chenguva refu chinoramba chiripo chinopfuurira kwemakore, dzimwe nguva mushure mekunyanya kunetseka kwekuvhiringidza kwaRusmussen's encephalitis. Dzimwe nguva sarmussen's syndrome inogona kuitika kunyange kana isingazivikanwe kana pane imwe nguva yakambova encephalitis yaRasmussen inotangira.
Rasmussen's syndrome, yakafanana neencephalitis raRasmussen, inoratidzika nekutambudza kwakaoma kutora uye kunobva kune rumwe rutivi rweuropi. Vamwe vanhu vane Rasmussen's syndrome vanoonawo kushaya simba kune rumwe rutivi rwemuviri, matambudziko emutauro, kana kuti dambudziko nekunyatsoziva.
Izvi zvinowanzokonzera vana pakati pezera remakore maviri kusvika ku12, asi zvinogona kukanganisa vanhu vemazera ose.
Chii Chandinofanira Kutarisira?
Kazhinji, kukanganisa kunokonzerwa ne encephalitis raRasmussen kwakaoma kutarisa nemishonga, uye kazhinji kunobata rumwe rutivi rwomuviri. Kutora kunowanzobatanidzwa nekudengenyeka nekudzungira kune rumwe rutivi rwemuviri, kazhinji nekurasikirwa kwekuziva kana kuderera mukuziva.
Kana iwe uine encephalitis raRusmussen, iwe unogona kusakanganwa kugumburwa zvakadzama, uye unganzwa uchineta shure. Kushaya simba, matambudziko emitauro, uye matambudziko ekufungisisa zvinotanga kuitika mwedzi mushure mokunge matambudziko atanga, asi zviratidzo izvi zvingaitika nokukurumidza kana kwete zvachose.
Kuongororwa kweRasmussen's Encephalitis
Zvinogona kutora nguva yakareba kuti iwe upiwe tsanangudzo yekujekesa yaRusmussen's encephalitis. Izvi ndezvokuti hapana kuedza kwakajeka kunogona kusimbisa izvi.
Rasmussen's encephalitis uye raRusmussen's syndrome zvinoratidzwa zvichibva pane zvido zvechiremba wako nezvezviratidzo zvekuchipatara kwemwedzi (kana kunyange makore) pamwe nekuongororwa kweEEG uye uropi hunonzi MRI test.
IEEG inotarisirwa kuratidzira basa rekubata kune rumwe rutivi rweuropi. Asi iyi EEG muenzaniso haisi yakasiyana neRasmussen's syndrome, saka saka EEG haisi kuongorora kwakasimba, asi inoshandiswa mukuratirana nemararamiro ako, mamwe maedzo, uye kuonekwa kwechiremba wemamiriro ako.
Uropi MRI inotarisirwa kuratidza kusiyana kwakakura pakati pemativi maviri europi. Pakutanga kwechirwere chechirwere, rumwe rutivi rweuropi runogona kuratidza chimiro chekuvhiringidza chinoratidzika sehutachiona. Gare gare muchirwere chechirwere, uropi MRI inogona kuratidza atrophy yechirwere chakakanganiswa, icho chiri kunyanya kuora kweuropi pamusana pekuparara kwenguva refu kubva kuvhunika. Iro uropi hunoonekwa MRI haisi ihwohwo kuRusmussen's encephalitis kana raRusmussen's syndrome, uye inofunganidzwa pamwe chete nemamiriro ezvinhu ose kuitira kuti uwane mhedziso yokuti une Rasmussen's syndrome kana encephalitis raRusmussen.
Treatment uye Management
Kana iwe uine encephalitis raRusmussen, iwe unogona kunge wakagamuchira mishonga inopesana nekutengesa kuti ubatsire kudzora kwako. Dzimwe nguva, steroid inoshandiswa kuderedza kupisa muuropi. Kana boka rako rezvechiremba rine chikonzero chekutenda kuti une chirwere muhutano hwako (infectious encephalitis ) , iwe unogonawo kugamuchira mishonga yekuwana chirwere chacho zvakare.
Kana iwe wakagumburwa kana utera kana chero humwe hutsinye hwepfungwa, asi hapana uchapupu hwekuputika, ipapo kurapa kwako kunonyanya kutarisirwa kugadzirisa kukanganisa kwako uye kukanganiswa kwako kwepfungwa.
Dzimwe nguva, kuurayiwa kweRasmussen's syndrome kwakanyanya zvokuti unogona kuve nekuvhiyiwa kwekufa. Kuvhiyiwa kunogona kusanganisira kusunungura nzvimbo yakakanganiswa yeuropi yako kana chirwere chiri mune imwe nzvimbo yehupfungwa dzako chinowanikwa chiri kukonzera kukanganisa kukuru. Kazhinji, nzira yekuvhiya inobereka migumisiro yakadai sokusarura kana kukwana zvakakwana kune rumwe rutivi rwemuviri. Kugadziriswa kweRasmussen's syndrome kunongororwa zvakanyatsorongeka, uye zvinongosarudzwa kana zvinotarisirwa kuvandudza mararamiro ako ehupenyu hwose.
Chii Chinokonzera Rasmussen's Encephalitis uye Rasmussen's Syndrome?
Encephalitis kuputika kweuropi. Hazvizivikanwi kuti chii chaicho chiri chikonzero chaicho chaRusmussen's encephalitis. Pari zvino, chikwata chezvezvehutano chakakurukura zvinhu zviviri zvakakosha:
- Izvo zvinogona kukonzerwa nehutachiona hunokonzera maitiro ekudzivirira immune.
- Inogona kukonzerwa nekugadzirisa kwemajini (muviri unozvidzivirira pachawo).
Zvinosuruvarisa, nokuti chikonzero cheRusmussen's encephalitis hachizivikanwi, hapana chakazivikanwa kudzivirira kwechirwere chisingawanzoitiki.
Shoko Rinobva
Kana iwe kana mudiwa wako ane chirwere chisina kujairika chirwere chakadai saRusmussen's encephalitis kana Rasmussen's syndrome, inogona kubatsira kusangana nevamwe vanhu vari kurarama nehosha imwe chete. Iwe unogona kuwana mazano uye dzidza kuburikidza nematambudziko akagoverana kana ukabatana neboka rekutsigira uye utaure kune vamwe vanogona kupa mazano uye mazano apo iwe unofamba noupenyu neRasmussen's syndrome.
> Sources:
> Nabbout R, Andrade DM, Bahi-Buisson N, et al, Mugumisiro wehutano-hutano hwekufa kubva pakuyaruka kusvika pakukura: Kuchinja kwehupenyu, Epilepsy Behav. 2017 Feb 27. pii: S1525-5050 (16) 30629-1. doi: 10.1016 / j.yebeh.2016.11.010.