Zviratidzo Zvokutanga uye Zvakawedzerwa zveCF, Progressive uye Genetic Disease
Kazhinji, zvirwere zvinonzi cystic fibrosis zvinowedzera sezvo chirwere chacho chiri kufambira mberi. Mamiriro acho ezvinhu, anokonzerwa nechiremera chinokanganisa, anokonzera kubatana kwemajasi okuvaka mumapapu (kuvhara ndege uye kutungamirira kuhutachiona, kukanganisa kwemapapu, nekushaya kupora), pancreas (kudzivirira muviri kuti urege kupedza kudya zvakanaka kunwa mishonga), uye dzimwe nhengo.
Izvo zvisina kukwana jeni haibvumiri kuti muviri uwedzere mvura uye munyu kune uye kubva kumasero, zvichiita kuti zvivande (zvinowanzopfa uye mvura mune vanhu vane utano hwakanaka uye yakawanda kwazvo uye yakasimba kune vanhu vane CF). Iyo miviri yakavharidzirwa ndiyo iyo inogadzirisa nhengo uye inodzivirira kushanda zvakanaka kwemuviri.
Zviratidzo Zvokutanga zveCystic Fibrosis
Nguva zhinji, vana vanozvarwa ne cystic fibrosis (CF) vanotarisa sevana vane utano nokuti chirwere hachikonzeri kusakanganisika kunooneka mumavambo ekutanga. Inenge 20 muzana yenguva iyo, vana vacheche vane CF vachave nekudzivirirwa kwepachivi mumatambudziko ekuberekwa kunonzi meconium ileus. Izvi zvinowanzoitika kunze kwekuti mwana ane CF, saka kana ikaitika inowanzoonekwa sechiratidzo chekutanga chechirwere.
Common Cystic Fibrosis Symptoms
Kana cystic fibrosis isingawaniki pakuberekwa, zvimwe zviratidzo zvinowanzotanga kuonekwa mugore rokutanga kana maviri ehupenyu, zvakadai se:
- Kushaya Kukura Kwekukura. Zvipembenene mumapascasi uye matumbo emukaka zvinodzivirira chirwere chekudya kushanda zvakanaka. Zvokudya zvinodyiwa zvinopfuura mumutumbi pasina michina yakawanda inogadzirwa, zvichiita kuti varambe vachikura. Kana mwana asina kutorazve kuberekwa kwake kwemavhiki masere mana kana matanhatu kana kuratidza chimiro chinoramba chiripo chekukura zvakashata, chiremba angatanga kutanganisa CF.
- Huge Appetite. Nemhaka yokuti mishonga haisati yakanyanyisa kubva pane zvekudya, uropi huri kuedza kusangana nesimba remuviri kuburikidza nokutumira zviratidzo zvekusha. Vanhu vane cystic fibrosis vanowanzoda kudya uye vanogona kudya zvinodyiwa zvisingabatsiri.
- Bulky, Mafuta, Foul Smelling Bowel Movements. Kushanda zvakanaka kwekudya kwekudya kunokonzera dambudziko kudya mafuta uye mapuroteni. Zvizhinji zvezvaiwanzobatwa nehutano hwakanaka huchideredzwa nemarumbo, zvichiita kuti zvirwere zvisingawanzoitiki zvinowanzoitika kune varwere vane CF.
- Kuramba Kuchengeta uye Kufuridzira Utachiona. Kushungurudza, kunetseka kufema, uye kugara uchiputika maitiro zvinowanzotanga zviratidzo zvinowanikwa nevabereki vevana vane CF.
- Salty Skin. Chiremera chemajini chinokonzera cystic fibrosis chinopesana nekukwanisa kwemuviri kubvisa munyu mukati uye kunze kwemasero. Munyu usingakwanisi kunyatsogadziriswa unodedzwa kuburikidza neganda nemajira e sweat, zvichiita kuti chiratidzo chinonzi salta chikafu chinonaka. Dzimwe nguva, pangangodaro kuve kune inoonekwa munyu kune ganda. Salt excretion nemafuta e sweat ndiyo nheyo yesero yakajairika inoshandiswa kuongororwa ne cystic fibrosis.
Zviratidzo zvepamusoro uye Matambudziko eCF
Zviratidzo zvepamusoro zve cystic fibrosis hazviwanzo zviratidzo zvechirwere chacho pachako, asi zviratidzo zvekukuvara kweCF kunokonzera nguva. Nenguva iyo mamiriro ezvinhu aya aonekwa, vanhu vakawanda vanoziva kare kuti vane cystic fibrosis uye vave vachirarama nechirwere kwenguva yakati. Zvinetso zvinotevera zvinotevera zviratidzo zveCF:
- Kunonoka Kuberekwa. Kunonoka kwehupombwe dzimwe nguva kunowanikwa kuvasikana vane cystic fibrosis nemhaka yekushaya zvokudya zvakashata.
- Infertility. Varume vakawanda vane cystic fibrosis vane infertile nekuda kwekuvharidzirwa kunodzivirira kubuda kwemunhu. Vakadzi vanogona kuve nekushaya simba nekuda kwemusana wechipupiti wakasimba unovhara kupinda kwemuviri mukati memitezo inobereka.
- Chirwere cheshuga. Nokufamba kwenguva, kukanganisa kwakaitwa pancreas ne cystic fibrosis kunokonzera kuti irege kubudisa zvakakwana insulin. Inenge 15 muzana yevanhu vane cystic fibrosis iyo inosvika pakukura ichaita kuti shuga yehushuga inokonzerwa nechirwere cheshuga .
- Chiropa Chirwere. Kuvharwa kwebiya ducts muropa kunokonzera kuora uye kuora kwechiropa munenge 5% yevashandi ve cystic fibrosis. Kana kuora kwechiropa kuchiitika, inowanzoonekwa kuvanhu vakuru.
- Gallbladder Disease. Iyo nduru yakachengetedza zvinhu zvinonzi bile izvo zvakasikwa nechiropa uye zvinobatsira mukudya kwemafuta. Mune vanhu vakawanda vane cystic fibrosis, iyo bile yakawanda uye haigoni kudarika budu duct kuti ibve mujeri . Kazhinji yenguva iyi haibvumiri zviratidzo, asi inenge 10 muzana ye cystic fibrosis ichakudziridza mazamu anodiwa kuvhiyiwa.
- Pancreatitis. Apo bheri rinobuda muhondo, inopinda mumucheche muduku kuburikidza nevakawanda bhati duct iyo inowananidzirwa ne pancreas. Kana gorosi richibuda muhombodo uye inoramba yakabatanidzwa mune yakazara bile duct, pancreatic secretions haigoni kusvika. Izvi zvinokonzera kurwadziwa kukuru nekutsamwiswa kwepascreas inozivikanwa sepancreatitis, iyo inoda kupindira kwekuvhiya.
Kunobva:
Cystic Fibrosis Foundation. NezveCystic Fibrosis. 10 Mbudzi 2016