Dzidza Zvakawanda Pamusoro Pezvakasiyana, Zvinetso Zvepanyama zvePrune Belly Syndrome
Prune Belly syndrome, inozivikanwawo seEagle-Barrett kana kuti triad syndrome, inokonzerwa nehutano nehutano hwakasiyana hwenyama iyo mwana anoberekerwa nayo. Zvinetso izvi ndezvi:
- Mishonga yepamuviri iri mberi kwemuviri haina simba kana iripo
- Zvikamu zve urinary tract zvinokura zvisiri izvo. Izvi zvinosanganisira kuwedzera kusina kukwana (kuputika) kwehuputi hwekuvhenekera, kuunganidza urin mumatope anokonzera urinhe kubva muinso kusvika kune chidzitiro, uye / kana kudzoka kwemuti kubva pachikanda kusvika mumatope uye mahara (anonzi vesicoureteral reflux).
- Mumadzimai (95% emhosva), ma testes anosimuka mukati mechimbudzi uye haazoburuki mukati.
Panogona kunge kune zvimwe zvinetso mumuviri, sekuputika kwemusana, kuputika kwechiuno, clubfoot, zvinopfutidza kana zvinetso zvemoyo, uye matambudziko emimba.
Zvinokonzera Prune Belly Syndrome
Chikonzero chechirwere hachizivikanwi, asi vatsvakurudzi vanodavira kuti kuvhiringidzwa kwekukura kwe fetus kunokonzera matambudziko kukura. Inofungidzirwa kuti chimwe chinhu chinovhara chikamu che fetus 'urinary tract, uye izvi zvinokonzera dzimwe chikamu cheturakiti kuti chive nechinhambo. Prune Belly syndrome inowanikwa mune 1 mu 40,000 mavambo anozvarwa mumaU.S.
Kuongororwa kweChiitiko
Ultrasound panguva yekuzvitakura dzimwe nguva inoona kukura kusina kukwana kwebhanyi uye urinary tract. Kunyange zvazvo fetus inokura, mvura inobuda mumimba yaro, inotakura uye yakakura. Mvura inoshandiswa ichidzorerwa asati aberekwa, saka nenguva yekuzvarwa, mucheche ane chirwere chinoputika kana kubwinya (naizvozvo zita rokuti "prune belly").
Mushure mokuberekwa, ultrasound uye x-rays zvinogona kusarudza kuti rudzi rwei urinary rutivi rwakakosha huripo. Prune Belly syndrome inowanzozivikanwa ne:
- Mamwe kana masimba emimba akawanda haasipo. Izvi zvinopa kuratidzika kwakaoma kana kuita semuchena.
- Kunyange zvazvo zvigunwe zvemasumbu kusvika pamapfupa zvingave zviripo, mishonga yacho shoma uye inoonda pamusoro pechiropa.
- Rusvingo rwemuviri rudukupa, mimba pachayo inoratidza kuti yakakura uye yakasununguka, uye utumbo hunogona kuonekwa kuburikidza nemadziro mashoma emadziro.
- Danda reganda rinoratidzika richibuda kubva mubhokisi remuviri kana kuenda kumudumbu.
- Chimwe chinhu chinobva pamabheji kusvika kune dzimwe nzvimbo chinogona kunge chiripo uye dzimwe nguva bhomba ringave rakabatana nechidzitiro kuburikidza negwenga (urachus) kana cyst.
- Kupisa kwembambo kana kuderedza chifukidzo kunogona kuita kuti chifukidzo chive chakakomba mune vana vane chirwere.
- Chirwere chakawedzerwa chiripo munenge mamiriro ezvinhu ose.
Zvinosuruvarisa, Prune Belly syndrome inogona kuva nemigumisiro yakaipa pamucheche. Nhamba idzi dzinoratidza kuti 20% yevana vanofa vasati vaberekwa, uye makumi matatu kubva muzana vanofa kubva pamatambudziko emagetsi nemakore maviri ekutanga ehupenyu. Mukusara kwe50% yevana, pane zvikamu zvakasiyana zvezvinetso zvekuvhota.
Prune Belly Syndrome inowanzoongororwa pasi pemhando dzakasiyana dzemazita, zvakadai sedumbu rekushaya urombo syndrome, kusagadzikana kwemahuro emimba, kushayikwa kwemuviri musumbu, Eagle-Barrett syndrome, Obrinsky syndrome kana triad syndrome.
Kurapa kweEagle-Barrett
Hakuchina mushonga weEagle-Barrett (prune belly syndrome), asi kugadziriswa kwegurani rinogona kugadzirwa.
Vamwe vanachiremba vanoedza kugadzirisa zvinetso pamucheche asati aberekwa, asi izvi zvave nemigumisiro yakavhenganiswa. Vana vanowanzoita zvirwere zvekuvhenekera vanopiwa zvirwere zvinodzivirira maantibiotics uye chirwere chinogona kuunza mhinduro dzemukomana kusvika muchikamu chake.
Dzimwe nguva pasinei nekurapa kwakanakisisa, itsvo dzevana dzicharega kushanda (kukundikana kwechirwere). Mushonga weiyi ndewe dialysis kana kuti mafungiro ekuchinja.
Nzira dzokuvhiya dzakanakisisa, kunyanya kushandisa laparoscopy, dzichaita mabasa ekugadzirisa anodiwa kumwana nePrune Belly syndrome zvishoma nezvishoma. Sezvo zvakawanda zvinodzidziswa nezvehurwere, kurapa kunogona kuvandudzwa uye vana vakabatsirwa kurarama kwenguva refu.
Sources:
Prune Belly Syndrome Network. About Prune Belly.
Franco, I. I. (2001). Prune Belly syndrome. eMedicine yakawanikwa pa http://www.emedicine.com/med/topic3055.htm
Leeners, B., Sauer, I., Schefels, J., Cotarelo, CL, Funk, A. (2000). Prune-belly syndrome: Kurapa maitiro anosanganisira mu utero kuiswa kwe vesica amniotic shunt. J Clin Ultrasound, Vol. 28, Nha. 9, mapeji 500-507.