Sturge-Weber syndrome chirwere cheganda uye nervous system. Chiratidzo chayo chinonyanya kuzivikanwa chiedza chinopenya kusvika pakuberekwa kwepuruvara yepepuru pane chiso chinonzi port port stain. Zvisinei, havasi vanhu vose vane tambo yewaini yepayiti vane Sturge-Weber syndrome. Sturge-Weber syndrome iripo pakuberekwa, asi hazvizivikanwi chinokonzera iyo kana kuti kanowanzoitika sei.
Inobata vose varume nevakadzi vemarudzi ose.
Kune marudzi matatu eSturge-Weber syndrome:
- Ita I-inonyanya kunyorwa, inosanganisira port wine stain uye brain angiomas
- Rudzi rwechipiri - chikwata chewaini chinoshandiswa asi harina uropi angioma
- Rudzi rwechitatu - uropi angioma asi hausi yewaini yewaini
Zviratidzo
Zviratidzo zveSturge-Weber syndrome zvinosanganisira:
- Pini yepaini yakasviba - Ichi chiratidzo chekuberekwa pachiso chinogona kusiyanisa muhukuru, asi kazhinji kacho chinosvika kamwe kemhizha yepamusoro nehuma. Inogona kubva kubva kumuchenje kusvika kumadziro epepuru uye inokonzerwa nekukura kukuru kwemidziyo yeropa (capillaries) iri pasi peganda. Nzvimbo yewaini yewaini inogona kuva yakaoma kuona muvanhu vane ganda rakasviba.
- Kushungurudzika - Inenge 75 kusvika ku90 muzana yevanhu vane Sturge-Weber syndrome vanokurira, kazhinji kunotanga gore rimwe chete. Kuwirwa kunokonzerwa nekukura kukuru kwemidziyo yeropa (angioma) pamusoro peuropi, kazhinji kumashure kweuropi kune rumwe rutivi sezvinoitwa port port wine stain.
- Kushayiwa simba - Inenge 25 kusvika ku5 muzana yevanhu vanotanga kusimba kana kurasikirwa kwekushandisa rumwe rutivi rwemuviri (hemiparesis), kazhinji kune rumwe rutivi rwakatarisana nechiteshi chetaini yewaini.
- Kuenderera mberi kunonoka uye kukanganisa kwepfungwa kunobata anenge 50 kusvika ku 60 muzana yevanhu.
- Headaches
- Kuwedzererwa muziso (glaucoma) - Inenge 70 muzana yevanhu vanogadzira glaucoma muziso pedyo nechiteshi chetaini yewaini.
Kuziva
Kuongororwa kweSturge-Weber syndrome kunogona kuratidzirwa nekuvapo kwechiteshi chewaini chechikepe pamusoro peziso rimwe nehuma. Computed tomography (CT) scan kana magnetic resonance imaging (MRI) inogona kuongorora uropi pakuvapo kweimwe kana kupfuura angiomas, iyo inogona kusimbisa kuongororwa. Mwana ane Sturge-Weber syndrome achava nekuongorora kwepfungwa kuti aongorore zvinetso zveuropi angioma, zvakadai sekukurira kana kushaya simba.
Kurapa
Kurapa kweSturge-Weber syndrome inotarisa zviratidzo. Kana kugumburwa kuitika, mishonga inoshandiswa nemishonga yakadai se carbamazepine (Tegretol), phenytoin (Dilantin), kana valproic acid (Depakote, Depakene) inopiwa. Mishonga inoshandiswa kuderedza nekudzivirira glaucoma uye musoro. Kurapa kwema Laser kunogona kuchenesa kana kubvisa chikepe chewaini chinotarisana nechiso. Mishonga yakawanda inogona kudiwa.
Kunobva:
> "Chii chinonzi Sturge-Weber Syndrome?" Nezve SWS / KT / PWS. Sturge-Weber Foundation. 10 Mbudzi 2007