Sarcoid-Lymphoma Syndrome Findings

Kunyange zvakadaro zvimwe zvisinganzwisisiki, sarcoidosis chirwere chisingazivikanwi chikonzero-kunyange zvazvo maitiro ezvirwere zvemuviri nemafungiro evanhu anokonzerwa kuti anokosha. Sarcoidosis, dzimwe nguva inongonzi sarcoid, inotungamirira kune chimiro chekuputika kunoonekwa pasi pe microscope uye kunogona kukanganisa nhengo dzakasiyana dzomuviri. Sarcoidosis inogona kukanganisa nhengo ipi neipi, asi inogona kuchinja mawebsite anotevera:

Sarcoidosis inozivikanwawo nezvayo inogona kuchinja maziso uye chiropa. Pashoma pacho, mwoyo uye uropi zvinogona kukanganiswa, zvinotungamirira kumatambudziko akakomba.

Kubva pamaonero emasero nemasukisi, chiratidzo che sarcoidosis chimwe chinhu chinonzi granuloma. Granulomas inounganidza masero ayo, pasi pe microscope, anotarisa zvakafanana neaya muviri unoshandisa kurwisa zvirwere zvakadai sechirwere chetachiona.

Haasi munhu wose ane sarcoidosis anoda kurapwa, uye kazhinji inoenda pasina kurapwa, asi mune dzimwe nguva, inogona kutungamirira kune zvirwere zvakakomba. Apo nhengo yebasa inoshandiswa, somuenzaniso, zvakasiyana-siyana zvezvinodhaka zvakagadzirirwa kudzivirira masimba ezvirwere zvinogona kushandiswa.

Zviratidzo zvinogona kureva nhengo dzinobatanidzwa muchirwere ichi, kana kune dzimwe zviratidzo zvinowanzoitwa zvakadai sokuneta, fivha, kuvhupa lymph nodes, uye kuora muviri . Kupindira kwemawere kunowanzozara uye zviratidzo zvinogona kusanganisira kuramba uchioma, kushaya kufema, kuputika kana kurwadziwa kwepfupa.

Vamwe vanhu vane sarcoidosis vanoita zviratidzo zveganda zvakadai sokuputika kunenge kwakatsvuka kana kuti kwakajeka tsvuku tsvuku-yepepuru.

Lymphoma

Lymphoma imwe ye "marariya eropa," kana hematologic malignancies, izwi rinosanganisirawo leukemias uye myeloma . Lymphoma ine kenza yemasero machena eropa lymphocyte. Kune marudzi mazhinji akasiyana e-lymphoma.

Yakawanda, asi kwete yose, lymphomas inotanga mumakirinikodhi.

Izvo zvikamu zviviri zvakakosha zve lymphoma ndiHodgkin (HL) uye kwete-Hodgkin (NHL) lymphoma. Zvose zviri zviviri zvine marudzi akawanda uye subtypes mukati, ane zvirwere zvakasiyana siyana uye zvinowedzera.

Zvose Hodgkin uye kwete-Hodgkin lymphoma zvinogona kukanganisa lymph nodes yebhokisi - nzvimbo iri pedyo nemwoyo inonzi mediastinum. Sarcoidosis inowanzosanganisira nzvimbo iyi.

Sarcoidosis uye Lymphoma

Kwemakumi emakore, vatsvakurudzi vave vachishamisika nezvehukama pakati pe sarcoidosis uye lymphoma. Ukama uhwu hunoramba husingazivikanwi kunyange nhasi, nokuda kwezvikonzero zvakawanda.

Maererano neboka revanotsvakurudza vanosanganisira Ishida uye vashandi pamwe chete navo, "Inonyanya kutaurwa yechirpidoma yemarchiidosis inonzi Hargidkin lymphoma, asi inoparadzanisa B-cell lymphoma, follicular lymphoma, uye myeloma yakawanda inogonawo kubatanidzwa mune sarcoidosis-lymphoma syndrome. "Izwi rokuti" Sarcoid-lymphoma syndrome "rakagadzirirwa kutsanangura izvi zvakawanikwa.

Chiratidzo chinonzi granulomas che sarcoidosis chinogadziriswa, chakagadzirirwa kuunganidza masero emumune akavharwa ne lymphocytes. Sezviri pachena, lymphomas dzimwe nguva inogona kubatira "sarcoidal" granulomas mukati mekenza - uye shanduko iyi, kunyange isingawanzoiti, inofungidzirwa kuti inogona kuratidzira zvirwere zvekudzivirira zvirwere mumuviri wekenza, kwete chirwere che systemic, sarcoidosis.

Mapepa akabudiswa mumakore akawanda apfuura akacherechedza kuti kusiyanisa pakati pemakumbo ane sarcoidal reaction uye zvechokwadi systemic sarcoidosis inogona kuva yakaoma.

Zvose sarcoidosis uye lymphoma zvinogona "kupenya" pane PET inoongorora, kuwedzera kuoma uye zvingaita kuti munhu awedzere kushandiswa kune imwe. Vatsvakurudzi varikukumbira zvimwe zvidzidzo zvekunatsiridza makiriniki ekushandiswa kweDGG-PET / CT mune varwere vane sarcoidosis.

Muchidimbu, mibvunzo yakawanda pamusoro pe sarcoidosis-lymphoma syndrome haigoni kupindurwa.

> Sources:

Ishida M, Hodohara K, Furuya A, et al. Sarcoidal granulomas mumakirini emasikirini emunharaunda mushure mekurapwa kwemazamu omunharaunda lymphoma wepamuti: mushumo wekodzero nekudzokorora kwechirevo che sarcoidosis-lymphoma syndrome. Int J Clin Exp Pathol . 2014; 7 (7): 4428-4432.

Mellemkjaer L, Pfeiffer RM, Mabhii EA, Gridley G, Wheeler W, Hemminki K, Olsen JH, Dreyer L, Linet MS, Goldin LR, Landgren O. Kuita zvirwere mumunhu mumwe nomumwe uye mumhuri yepedyo uye kugamuchirwa kune kwete Hodgkin lymphoma. Arthritis Rheum . 2008; 58: 657-666.

Reich JM, Mullooly JP, Johnson RE. Kubatanidza kuongororwa kwemarignancy-yakabatana sarcoidosis. Chest. 1995: 107: 605-613

National Heart Lung uye Blood Institute. Chii Chinonzi Sarcoidosis? Yakasvika muna January 2016.

Goswami T, Siddique S, Cohen P, Cheson BD. The sarcoid-lymphoma syndrome. Clin Lymphoma Myeloma Leuk . 2010; 10: 241-247.