A Progressive Motor Neuron Disease
Primary primary latal sclerosis (PLS) inofambira mberi inogadziriswa motokari yeuroni neuron . PLS inokanganisa masero emutsipa mumuviri anodzora kufamba kwokuzvidira kwemisungo, inonzi motor neurons. Nokufamba kwenguva, idzi motokari dzinokanganisa kukwanisa kwavo kushanda, zvichikonzera kusava nesimba asi kupfuurira kusimba uye kuoma kwemisungo.
Hazvizivikanwi nei PLS inowanzoitika, kana kuti iyo yakadini masero emasero anoparadzwa.
Primary primary latal sclerosis inoratidzika kutanga pashure pemakore 40 kusvika ku50 yemakore. Hazvizivikanwi kuti vanhu vangani vari munyika vanovhiringidzirwa ne PLS, asi hazviwanzoitiki.
Zviratidzo
Kurasikirwa kwemasero emagunha kunokonzera mitsipa kuti ive yakaoma uye yakaoma kufamba. Kazhinji, zvinetso zvemasumbu zvinotanga mumakumbo uye zvinokwira mumuviri kune chitunha, maoko, uye mutsvuku mumeso nemutsipa. Kufambira mberi kwePSS kunosiyana kubva kune imwe nyaya kune imwe nyaya-Vamwe vanofambira mberi nokukurumidza mumakore mashomanana kana kuti zvishoma nezvishoma pamakumi emakore mashomanana.
Pakutanga zviratidzo. Muzviitiko zvizhinji, chiratidzo chekutanga che PLS chiremera chisina simba uye kuoma mukati memakumbo ezasi. Zvimwe zviratidzo zvokutanga zvinosanganisira:
- Rimwe gumbo rinowanzotarisa kupfuura rimwe, nekufambira mberi zvishoma kusvika kune rimwe jumbo
- Zvishoma nezvishoma, kufamba kwakasimba kwemakumbo pamusana pekusagadzikana kwemaviri mashoma (spasticity)
- Kuoma nekufamba nekuchengetedza kuenzanisa, zvakadai sokukwira kana kugumburwa
- Kugumburwa kwemasumbu akasvibiswa
- Zvose zvinokanganisa
Zviratidzo Zvichibudirira. Vanhu vakavhiringidza vangave vachiwedzera kuoma mukufamba. Kushandiswa kwekadhi kana chipangizo chakafanana kuti ubatsire mukufamba kunogona kudiwa. Mune zvimwe zviitiko, zvimwe zviratidzo zvinogona kutangira kukura kwemasumbu kusimba mumakumbo. Dzimwe zviratidzo zvinogona kusanganisira:
- Tsvina yemasumbu mumaoko kana kuti muchero hweuropi.
- Uturu hwakashata huri mumakumbo, shure, kana mutsipa
- Dambudziko rinofambisa maoko uye kuita mabasa akadai kusangana nevhudzi kana kupwanya mazino
- Dambudziko rokuumba mazwi (dysarthria) kana kutaura
- Dambudziko rokuedza (dysphagia)
- Kurasikirwa kwechirwere kutora nguva munguva yekutanga kwemazuva ekupedzisira lateral sclerosis
Zviratidzo zvishoma nezvishoma zvinowedzera kupfuura nguva.
Kuziva
Icho hachisi kuedza kwakananga kwepamusoro lateral sclerosis, saka nguva yakawanda yekuongorora kunoitika semugumisiro wekubvisa zvimwe zvinokonzera zviratidzo. Nokuti amyotrophic lateral sclerosis (ALS, kana chirwere chaLou Gehrig) chinonyanya kuzivikanwa, uye nokuti zvirwere zviviri zvinowanzoratidza zviratidzo zvakafanana, PLS inowanzovhiringidzika neAIDS.
Kurapa
Ikoko hakuna mushonga panguva ye PLS, saka kurapwa kunowedzera pakuderedza zviratidzo zvechirwere. Mishonga ye PLS inosanganisira:
- Mishonga yakadai saBaclofen uye Tizanidine kuderedza kusvibiswa kwemisumbu
- Kurapa kwezvinodhaka kutarisa kurasikirwa kwekanyara
- Kurapa kwepanyama uye yebasa kunobatsira kuderedza mararamiro, kuvandudza kufamba, uye kupa mishonga kuti ibatsire nekufamba nekudya
- Kutaura kunobatsira kubatsira nekutaura
- Orthotics uye shangu inowedzera kugadzirisa matambudziko emakumbo nemakumbo
Support
Primary primary lateral sclerosis inounza kupora nekubudirira kwekushanda asi haipindi pfungwa kana kuderedza upenyu hwevarwere zvakananga. Nokuda kwechikonzero ichi, mapoka ekutsigira zvakadai seSpastic Paraplegia Foundation kune varwere uye mhuri dzavo chinhu chinokosha pakuchinjanisa nemitoro yepanyama uye yepfungwa dzechirwere.
> Sources:
National Institute of Neurological Disorders uye Stroke. NINDS Primary Primary Sclerosis Information Page.
Spastic Paraplegia Foundation. Nezve PLS.
Spastic Paraplegia Foundation. Mishonga uye Mishonga.
National Organ for Rare Diseases. Primary Lateral Sclerosis.