Nhungamiro Yako Yepamusoro kuNLPHL Kubva kuSymptomes kusvika Kuchirwa
Nodular lymphocyte inonyanya kukosha Hodgkin lymphoma (NLPHL) chirwere cheHodgkin chirwere , kenza yemakirini masero . Icho chimwe chezvinhu zvishoma zvishoma zveHodgkin lymphoma , inenge inenge 5% yezviitiko zvose zvekenza iyi. Zvisinei, ine zvikamu zvakasiyana-siyana zvakasiyana zvinoita kuti zviparadzanise nedzimwe mhando dzehosha yeHodgkin inonzi classical Hodgkin lymphomas.
Ndiani Anowana Nodular Lymphocyte Predominant Hodgkin Lymphoma?
NLPHL inogona kuitika panguva ipi zvayo, kunyange zvazvo varwere vakawanda kazhinji vari mumakumi matatu avo. Iko katatu kakawanda inowanzoonekwa kune varume kana ichienzaniswa nechiyero chevakadzi. Hapana chikonzero chinogadziriswa, asi njodzi dzinosanganisira kuve nehutachiwana hweHIVE-Barr uye kuva nechikwata chekutanga chechipiri neHodgkin lympoma.
Ndezvipi zviratidzo zveNLPHL?
Chiratidzo chinonyanya kukosha chechirwere ichi ndechekuwedzera kwe lymph nodes mumutsipa, pachipfuva kana mumakumbo. Kubatanidzwa kwemamwe lymph nodes kana dzimwe nhengo hazvisi nyore. Zvimwe zviratidzo zveLymphoma zvinosanganisira fever, kuora muviri uye kuputika usiku. Kuongorora muviri, nhoroondo yezvokurapa, uye kuongorora ropa kuchaitwa.
Kuongororwa kwe lymphoma kunoitwa ne lymph node biopsy . Mhando chaiye ye lymphoma inotsvakurudzwa nemakoromendi anokwanisa kutaurira musiyano pakati peNLPHL nemamwe marudzi eHodgkin lymphoma.
NLPHL inokonzerwa nokushungurudzwa kweB-seli, iyo inowanzoita chikamu chemuviri wezvirwere mumuviri unobudisa zvirwere. Vane nzira yakasiyana yeCD antigens, mapuroteni ari pamusoro pemasero, anogonesa kuongororwa kushandiswa kwezvinhu zvinokonzerwa nehupenyu hwepanyama uye CD marker testays. Izvi zvakasiyana-siyana zveCD antigen zvinoshandiswawo kune zvakagadziriswa mishonga inonzi monoclonal antibody.
NLPHL Inotarirwa Sei?
Vanenge vatatu pavatatu vanorwara neNLPHL vanorwara nekambani yekutanga lymphoma , inosanganisira lymph nodes chete mumutsipa uye nehafu yemuviri. NLPHL inowedzera kukura zvishoma kupfuura yekare yeHodgkin lymphoma, uye kana usina zviratidzo zvinogona kugadziriswa kutarisa uye kurindira zviratidzo zvisati watanga kurapwa. Kana iyo lymphoma iri mukutanga uye iwe hauna zviratidzo zveB zvinogona kurapwa nehutachiona hwemaawa chete. B zviratidzo zvinosanganisira fevha, kurasikirwa, uye kupera usiku.
Kana iwe uine zviratidzo zveB kana kuti iwe uri pane imwe nguva yakanyanyisa, chirwere che nodular lymphocyte chinonyanyisa Hodgkin lymphoma chinosanganisira chemotherapy uye kazhinji kurapa kwemaawa kunowanikwawo saizvozvo. Iro monoclonal antibody rituximab inogona kupiwawo Vagari vazhinji vanopindura zvakanaka kwazvo kurapwa, uye vanopfuura 90% vanorapwa. Kupona mazinga eHodgkin chirwere chiri kuwedzera nekuda kwekufambira mberi mukurapa.
Kunyange zvazvo ichi chiri chirevo chakanaka, mu10% kusvika ku40% yevarwere vanopararira zvikuru B-cell lymphoma inotanga nemakore gumi mushure mekurapa. Sezvo NLPHL inowanzowanikwa mumajaya, zvakakosha kuti varambe vachichiteverwa kwenguva refu kuti vaone kudzoka. Kunyange zvazvo kurapwa kwavo kwokutanga kungaita sokuti kwakabereka mushonga, chiitiko chekudzoka zvakare uye kufambira mberi kwakakosha zvakakwana zvokuti vanoda kuramba vachiongororwa kwenguva refu.
Kurapa kwekudzorerwa zvakare NLPHL varwere vane rituximab, monoclonal antibody, iri kuongororwa.
Sources:
Kanzira: Mazano uye Maitiro eOnology 7th Edition. Vakuru: VT DeVita, S Hellman uye SA Rosenberg. Yakabudiswa naLippincott Williams naWilkins, 2005.
> National Cancer Insit. Mukuru Hodgkin Lymphoma Treatment-yevashandi vehutano (PDQ®).
> America Cancer Society. Kurapa nodular lymphocyte yakawanda zvikuru yeHodgkin chirwere (NLPHD).