Overview
Kunyange zvazvo mashoko acho angaita seanotyisa, Zuva reErythroblastopenia reMwana (TEC) inoratidzika kuti haigone kupera simba kubva paudiki. Ndicho chikonzero chinowanzokonzerwa nekuderedza kushandiswa kwemasero matsvuku eropa muhuduku. Erythroblasts ndiyo masero anotangira kuva masero matsvuku eropa uye -penia inobva mushoko rechiGiriki nokuda kwekushaiwa. Chaizvoizvo, chirwere chepfungwa chinokonzerwa nokusakwanisa kwemafupa ekutora kubudisa masero matsvuku eropa kwenguva yakati.
Zviratidzo
Inemia muTEC inononoka kuitira kuti vamwe vana vangave vasina zviratidzo. Vana ava vanogona kuwanikwa nenzira inowanzo nebasa rekushandisa ropa kana kuti vanogona kudzoka vasina nguva dzose kuenda kuchiremba. Mune vamwe varwere, zviratidzo zvakabatana neanemia. Dzinosanganisira:
- Kuneta kana kuneta
- Pallor kana ganda ganda
- Chizutu
- Rapid heartbeat, inozivikanwa se tachycardia
- Kupfupika kwemhepo
Rick Factors
Sezvo zita rinoratidza, TEC inoitika muhuduku. Vazhinji vevana vanoongororwa pakati pemakore nemakore emakore. Vakomana vanoita kunge vane ngozi shomanana yakaenzaniswa nevasikana.
Kuziva
Hapana humwe huongorori hutano hweTEC. Vamwe varwere vanogona kuzivikanwa nebasa rega rega rega rekutarisisa vana. Mune vamwe varwere, kana chirwere chekushaya ropa chichifungidzirwa, TEC inoratidzirwa pahuwandu hwekuverenga ropa (CBC). Muzhinji, iCBC icharatidza kupererwa kweanemia. Pane dzimwe nguva kungave neutropenia (yakaderedza nhamba yeeutrophils, rudzi rwechichena chemukati ropa).
Masero matsvuku eropa akaenzana nehutachiona asi anogona kuwedzerwa apo murwere anotanga kudzoka.
Chikamu chinotevera chekushanda ndeye reticulocyte count. Reticulocytes masero masero matsvuku eropa akangobudiswa kubva mumufupa. Pakutanga kwechikoro, reticulocyte count iri pasi, inonzi reticulocytopenia.
Kana imwe nguva mapfupa emapfupa achisarudzwa, reticulocyte count inokwira kumusoro (yakakwirira kupfuura yakasarudzwa) kuti idzose iyo tsvuku yakatsvaga yeropa uye inodzokera kune yakajairika apo chirwere chinopera simba chinogadzirisa.
Munguva yebasa, zvakakosha kusiyanisa TEC kubva kuDamond Blackfan Anemia (DBA), rudzi rwakagarwa nhaka yeanemia. Varwere vane DBA vane utano husingaperi hwehupenyu hwose. Varwere vane DBA vanowanzova vaduku (pasi pezera remakore 1) pavanoongororwa uye masero matsvuku eropa akawandisa kupfuura mashoma (macrocytosis). Kazhinji, kana kuongororwa hakusi pachena kuti aspirate yemapfupa uye biopsy inogona kudiwa. Dzimwe nguva hurumende inosimbiswa yeTEC ndeyokuti murwere anowana zvakare pasina kupindira.
Zvinokonzera
Mhinduro shoma ndeyatisingazivi. Inenge imwe hafu yevarwere vacharondedzera chirwere chetachiona 2 - 3 mwedzi isati yaongororwa. Inofungidzirwa kuti hutachiona hunokonzera kudzvinyirira kwenguva pfupi kwekutsva kwemasero eropa mumapfupa emapfupa. Mishonga yakasiyana-siyana yakabatanidzwa neTEC asi hapana kana yakafanana.
Nguva
Muzviitiko zvakawanda, TEC inogadzirisa mumwedzi 1 - 2 asi kune mitsara yevana vanotora nguva refu kuti vadzoke.
Mishonga
- Kucherechedza: Kana chirwere chemahyamu chiine unyoro uye mwana wako haana kumira, hapana kurapa kunogona kudiwa. Chiremba wako angaita kuti mwana wako awedzere ropa nguva yakawanda kusvikira yagadziriswa.
- Corticosteroids: Dzimwe nguva steroid yakafanana ne prednisone yakashandiswa asi hapana humwe humwe hwakasimba hwokuti kurapwa uku kunopedza nguva yekudzoka.
- Kuwedzerwa kwemuviri: Kana chirwere chekushaya ropa chiri chakakomba kana mwana wako ane zviratidzo kubva kune chirwere chepfungwa (kuve nehutano, kuneta, kupera kwepfungwa, kukwira kwemwoyo yakakosha, nezvimwewo) kuwedzerwa ropa kunogona kupiwa.