Kubatana Kunobatanidza Nezviratidzo Zvakawanda
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIH), inozivikanwawo seBerdon syndrome, inokonzerwa nehutano hwehutendere hwakanaka mumudumbu uye chirwere chekudya. Dambudziko racho rinodzivisa mudumbu, mumatumbo, itsvo, uye chidzitiro kubva pakushanda zvakanaka.
Hazvizivikanwe kuti sei kana sei chikonzero cheMMIH syndrome chiripo. Vamwe vatsvakurudzi vanotenda kuti yakagara nhaka sezvo kubva mave nezviitiko zvevana vehama vari kuchinjwa.
Inenge dzose dzezvizivikanwi zviitiko zviri musikana. Chimwe chikonzero nei izvi zvingave ndezvokuti MMIH inogona kushandiswa zvisina kuonekwa seproducune swelling, zvikurukuru kuvakomana.
Zviratidzo
Zviratidzo zveMMIH zvinokonzerwa nehutachiona hwehutachiona hwakanaka. Uturu hwehumuviri huri mukati uye hahukure zvakanaka mutero. Zviratidzo zveMMIH ndezvi:
- megacystis - chirwere chikuru chinenge chisina simba
- microcolon - zvakare-duku duku mumukumbo
- mumukati hypoperistalsis - musikana muduku wakazara uye masimba ayo asina simba haapfuuri zvokudya kuburikidza chaizvo
Mishonga yepamuviri inofadza, zvichiita kuti dumbu recheche rionekwe rakanyunguduka, sechando. Iyo hypoperistalsis inotungamirira pakuvhara uye kuvhara mumatumbo.
Kuziva
MMIH yakaoma kufungidzira mwana asati aberekwa. Nhengo dzomukati dzisina kufanira dzakadai sechirwere chakawedzerwa uye chisina kudziviswa chinogona kuonekwa pa fetal ultrasound, asi zvingasava pachena kuti mwana ane MMIH, kunze kwekuti mwana ane munin'ina ane chirwere.
Kana mwana aberekwa, kuongorora muviri uye ultrasound kunokwanisa kuona kana MMIH iripo.
Mukuongorora kwepanyama, vanachiremba vachange vachitsvaga mharidzo inotevera yezviratidzo chiratidzo chekutanga chechimiro:
- Bumbi rakareba kana rakawedzerwa
- Kusuruvara-kusvibiswa uye kusakwanisa kupfuurira meconium (chinhu chine ruvara rwemavara chigadzirwa chigamba chekutanga chechecheche).
- Nzira dzakasiyana-siyana dzevisceral nervous system dzisina kunaka (iyo inodzora misoro yakaoma, musikana wemwoyo, uye gland masero)
- Digestive tract issues kusanganisira microcolon, kudyiwa kwemvura, uye mafupa maduku.
- Kusagadzikana kwemashoko emuguta
- Undescended testis mune dzimwe nguva
Kurapa
Zvinosuruvarisa, hapana mushonga weMMIH (Berdon Syndrome), uye maonero akaderera kune vacheche vakazvarwa naro; vazhinji vanofa mukati megore rokutanga rehupenyu. Vana vacheche vanogona kudyidzwa mukati memajoka akasiyana-siyana, asi chirwere ichi chinowanzokonzera chiropa kusakundikana.
Vanachiremba vakaedza kuchinja zvose zvenhengo dzomukati dzisina kukwana mukati memucheche ane MMIH kuburikidza nekugadzirwa. Imwe nyaya iri mumagazini inonzi Transplantation muna 1999 yakashuma pamusoro pavanasikana vatatu vane MMIH avo vakagashira zvirongwa zvakawanda. Izvozvo zvakaputsika zvakakundikana mumwana mumwe, uyo akafa; mumwe mwana akafa makore gumi nemashanu gare gare kubva pneumonia , asi mwana wechitatu akanga ari mupenyu uye zvakanaka panguva yechinyorwa chacho.
Chimwe chiedza chekugadziriswa kwezvikwata zveMMIH zvakaitwa musi waJanuary 31, 2004. Alessia Di Matteo, weGenoa, Italy, akagamuchira nhengo nhatu kubva kune rimwe kacheche: chiropa, dumbu, makanda, mukomana muduku, utumbo hukuru, spleen, uye maviri kidneys. Vanachiremba paYunivhesiti yeMiami / Jackson Memorial Hospital, uko kuvhiyiwa kwaitwa, yakashuma mavhiki manomwe gare gare kuti Alessia aive achiita zvakanaka.
Anofanira kuramba achiita zvinorambidza zvinodhaka kwemakore ose eupenyu hwake, asi vabereki vake vanofunga kuti mutengo muduku wokubhadhara chipo chehupenyu chaakapiwa.
Sources:
Brecher, EJ Mwana anowana nhengo gumi nhatu muMami. The Miami Herald, Chishanu, March 19, 2004.
InfoBiogen. Megacystis-microcolon-intestinal-hypoperistalsis syndrome.
Masetti, M., Rodrigues, MM, Thompson, JF, Pinna, AD, Kato, T., Romaguera, R. l., Nery, JR, De Faria W., Khan, MF, Verzaro, R., Ruiz, P ., Tzakis, AG (1999). Multivisceral transplantation ye megacystis microcolon intestinal hypoperistalsis syndrome. Kudyarwa , 68 (2), mapeji 228-232.