Microtia: Birth Defect of the Ear

Apo vana vanoberekwa vane nzeve imwe

Microtia inokanganisa kuberekwa kwenzeve yomwana. Izvi zvinoitika kana nzeve yekunze iri duku uye isina kuumbwa kuva nzeve inowanikwa mumucheche mumavhiki mashoma ekutanga ekudzivirira. Pakutanga dambudziko racho rinoitika apo mwana ari mudumbu, kunyanya kuora kwacho. Nzeve yakarurama inobatanidzwa kakawanda kupfuura nzeve yeruboshwe kana nzeve mbiri.

Mumwe kune vashanu vana vacheche vanenge 10 000 vane microtia.

Inobata varume kupfuura vakadzi uye inonyanya kuonekwa muAsia uye Hispanics kupfuura Caucasians uye Africa-America. Izvo zviitiko zvakakwirira chaizvoizvo pakati peNavajo rudzi rwevaAmerica. Vanachiremba vepurasitiki, zvisinei, vanogona kukwanisa kugadzira chirwere ichi.

Zvinokonzera

Hapana anoziva chikonzero chaiicho microtia chinoitika. Mune zvimwe zviitiko, genetics inogadzirisa, zvichida nekuda kwekuchinja kwemajini kana nekuda kwekusafanana mune rimwe gene rinokonzera genetic syndrome. Zvimwe zvinodhaka, zvakadai seAccutane (isotretinoin) inotorwa panguva yekuzvitakura, yakaderera ropa kuyerera kusvika kumucheche, uye zvakatipoteredza zvinhu zvose zvinokonzera kukonzera microtia zvakare.

Zvimwe zvinhu zvinowedzera mukana wekuva nemwana ane microtia zvinosanganisira chirwere cheshuga uye chikafu chemhuri, maererano neU.S. Centers for Disease Control nekudzivirira. Kunyanya kunyanya, kana mukadzi ane chirwere cheshuga asati aita pamuviri, ane dambudziko rakakura rokuva nemwana ane microtia akaenzaniswa nemukadzi asina chirwere cheshuga.

Uyezve, vakadzi vane pamuviri vanodya kudya kunowanikwa mu-carbohydrate uye folic acid vanogonawo kuwedzera mukana wavo wekuchera mwana ne microtia.

Zviratidzo nezviratidzo

Microtia inogona kutora nenzira dzakasiyana. Dzimwe nguva bundu reganda rinogona kuvapo apo nzeve inofanira kuva. Dzimwe nguva zvikamu zvezasi nzeve dziripo, asi nzeve yepamusoro haisipo.

Chimiro chakaipa kwazvo apo nzeve yekunze isipo zvachose, inozivikanwa seotiaaa. Uye panogona kuva nekushaiwa kwemukova munzeve yekunzwa.

Kuziva

Kunyange zvazvo iri nzeve yekunze iyo ine kuora kunooneka, dzimwe nhengo dzenzeve dzinotambudzwa dzinoshandiswa. Iko mukati mezeve, kunyanya munzeve ye nzeve uye nzeve yepakati, kazhinji ine zvikanganiso zvakare. Dzimwe nguva nzeve inonzwa haitombokura. Mune vanhu ava, hapana gomba rinooneka rinotungamirira kune eardrum uye nenzeve iri pakati. Kuipa kwakadaro kunogona kukonzera kurasikirwa kunzwa.

Vanhu vane microtia mazana (mumakumbo maviri) vari mumamiriro akasiyana zvakasiyana nevanhu vane unilateral microtia. Avo vane unilateral microtia vane ruzha rwekunzwa munzeve yakazara, asi avo vane mazana macrotia vanogona kuva matsi.

Kugadzirisa uye Kurapa

Chinangwa chikuru chekudzorera nzeve yekunze ndeyekuvandudza kunzwa sezvo inobata ruzha uye inovatungamirira mumugwagwa wekunzwa kuenda kune eardrum uye majeri anonzwa. Kuvandudza kunzwa kunobatsira nekutaura .

Kushandiswa kwekunzwa kunogona kudiwa. Asizve, kuvandudzwa kwechimiro chimwe chekubatsira kunogona kukurudzira kuzviremekedza uye kugamuchirwa kwevanhu. Kugadziriswa kwekona remakumbo kunoitwa nhengo yehutoriki.

Nzeve inosvika pachizhinji chekukura kwayo (85 muzana) nezera remakore mana. Nzeve inoenderera mberi kuwedzera muhupamhi kusvika makore gumi. Zvisinei, zviitiko zvakanakisisa zvinoitika apo kuvakazve kunonoka kusvika mushure memakore gumi. Zvinhu zviviri zvinokanganisa apo kuvakwa kwenzeve kunogona kuitika ndeizvi:

  1. Kuwanika kwechikwata chakakwana cheti cartilage kuita sarudzo ye nzeve. Hazvisi kusvikira makore mashanu kana matanhatu iyo nhokwe yemwana yakakura yakakura zvakakwana kuti ipe chikwata chakakwana chokupa nzeve.
  2. Kufunga kwepfungwa yekuve asina kufanana / kwete nzeve (s). Kugadziriswa kunowanikwa pasi pezera rechikoro kuitira kuti kuderedza / kurega kuseka nevezera rako.

Nzeve yekunze inogona kuvakwa patsva nemagadzirwa (man-made) zvinhu kana kubva mundiro cartilage. Kune zvakanakira uye zvisingabatsiri kune zvose zvingasarudzwa. Ngatitaurirane navo:

Synthetic Materials

Zvimwe zvekubatsira kushandiswa kwezvinhu zvakagadziriswa kuvakazve microtia nzeve ndezvokuti hapana nyaya, dzakadai semavanga uye marwadzo, kubva pakukohwa nenyuchi cartilage. Inogona kuitwa mune imwe nzira uye chigumisiro chakanakidza kuoneka kwechiso.

Kukanganisa kwekushandisa zvinhu izvi ndezvokuti nzeve inotanga kushungurudzika zviduku uye utachiona pamwe nekukwanisa kwemuviri kuramba nzeve itsva nekuda kwezvinhu zvakashandiswa.

Cartilage Graft

Yakakonzerwa kubva pamubvuti wetirotilage, kuipa kwekushandisa kurapwa uku ndiko kunogona kuva nekutambudzika uye hovha inobatanidza nekuwana mashoko acho. Uyezve, pane zvinopfuura kuvhiya.

Zvisinei, iyi ndiyo yakanakisisa kwenguva refu uye, nokuti inoshandisa zvinhu zvomunhu pachake, hakusi kwekuti muviri unoramba nzeve.

Prosthetics

Mumamiriro ezvinhu apo hapana ganda rakakwana kuti rivhare kana chigadziro chekugadzirisa kana chigunwe chekatetikiti nekuda kwekutsvaira, kupisa, kupiswa kwezuva, nezvimwe, nzeve yeprosthetic inogona kushandiswa. Ive hutere hwekunzwa huri nemafungiro ayo uye kukanganisa zvakare.

Kunyange zvazvo nzeve yehutachiona inogona kutarisa zvikuru sekunze kwekunze, unhu hwechigadziro hunobva pauri hwemhizha uye unyanzvi hwekombiyuta. Kuwedzerwa, nzeve yehutachiona inogona kunge yakadhura. Inguva yakareba sei chigadzirwa chacho chinopera zvinoenderana nekutarisira kunoitwa muridzi.

Muhafu ye microtia matambudziko, pane zvakakwana zvepakati nzeve izvo zvinogona kuvakwazve kuti zvivandudze kana kudzorera kunzwa.

Zvimwe Zvimwe Zvinetso

Sezvakaita chero nzira ipi zvayo yekuvhiya, kune mikana inogona kuitika kana iri pamusoro pokudzorera nzeve. Utachiona ihwohwo hunogona kusanganisa pamwe nehutano hwekugadzira. Hematoma , zvisingazivikanwi inozivikanwa sekuunganidza ropa, inogonawo kukanganisa urongwa hwehututi.

Kurasikirwa kweganda munzeve nzvimbo zvakare kunogona. Kuwedzeresa, mumamiriro ezvinhu apo chibhakera chinoshandiswa chinoshandiswa, matambudziko emapapu, chifukidzo chemadziro emadziro okusvibiswa, uye kupora kusingaoneki kunogona kuitika. Uye zvinetso zvine chokuita nekugadzirisa zvinogona kukonzera kudiwa kuita chiitiko zvakare.

Sources:

Kuparadzana Kwekuberekwa Nokuremara Kubudirira, NCBDDD, Kuzvarwa Kwekuzvarwa: Chokwadi Pamusoro peAnotia / Mirotia. Nzvimbo dzeDaase Control uye Kudzivirira.

LeBlanc DM. Microtia. Mu: Janis E, ed. Zvinyorwa zvePlastiki Surgery. St. Louis: Quality Medical Publishing, Inc., 2007.

Thorne CH. Inzwa Yekunze. Mu: McCarthy JG, RD Galiano, Boutros SG, eds. Current Therapy in Plastic Surgery, 1st Ed. Philadelphia: Elsevier, Inc, 2006.

Thorne CH. Otoplasty uye Ear Reconstruction. Mune: Thorne CH, Beasely RW, Aston SJ, Bartlett SP, Gurtner GC, Spear S, eds. Grabb na Smith's Plastic Surgery, 6th ed. Philadelphia: Lippincott, 2007.