Lymphoblastic Lymphoma

Lymphoblastic lymphoma inzira isingawanzokurumidza kukura, ine utsinye isiri Hodgkin lymphoma (NHL), inowanzoonekwa muvechiri kuyaruka uye vaduku vakuru. Imwe zita rayo ndeye precursor lymphoblastic lymphoma. Inowanzo chiremera chemasero eT asi dzimwe nguva masero e-B masero, uye mazwi iwayo achashandiswa mukutumidza zita.

Overview

A blast cell inenge isina kuisa masero mumapfupa emapfupa ayo anopa kukwira kwemasero eropa, Mukati ye lymphoblastic lymphoma, iyo yakavhiringidzika masero ndeye lymphoblast iyo inowanzoita mutsara wakanaka wemagetsi emasero, lymphocytes.

I-lymphoblasts yaiwanzogara mumapfupa emapfupa, ichibudisa lymphocytes inopararira muropa uye lymphatic system, kusanganisira lymph nodes.

Chii Chinogadzira Lymphoblastic Lymphoma?

Lymphoblastic lymphoma chirwere chekusava nemamine lymphoblast. Iyo inowanzowedzerwa kakawanda kubva kuT-lymphoblasts kupfuura B-lymphoblasts. Icho chinotyisa kwazvo lymphoma, inonziwo grade yepamusoro lymphoma. Izvozvo zvinoreva kuti lymphoma inokura nokukurumidza, uye inogona kupararira zvakasimba kumativi akasiyana emuviri. Munzira dzakawanda iyo yakafanana neyeukemia. Muchiitiko ichi, inodonha muhutano hweacute lymphoblastic leukemia kana pane zvinopfuura 25% lymphoblasts mumapfupa emapfupa.

Zivai mazita anopiwa kune zvakasiyana-siyana zveNHL munyaya yeNHL .

Ndiani Anowana Lymphoblastic Lymphoma?

Lymphoblastic lymphoma inowanzokonzera vechidiki vari mumakore ekuyaruka kana makore makumi maviri. Izvo zvinowanzoonekwa kune varume kupfuura vakadzi.

Iyo inofanirwa ne20% yeNHL muvana.

Maitiro Ehutano Hunoita Sei Muviri

Iyi lymphoma inokura zvakanyanya. Vakawanda vanorwara vanoita zviratidzo zvakakomba munguva shomanana yenguva. Lymph nodes mu mediastinum (iyo inonyanya chikamu chebhokisi pakati pemapapu) ndiyo inowanzobatwa. Izvi zvinokonzera kuwanda mubhokisi rinotungamirira kumatambudziko ekufema nekukandira.

Mvura inogonawo kuunganidza mumapapu. Iropa remafu rinowanzobatanidzwa. Uropi uye rwonzi rwomumutsipa runogonawo kuitika mune dzimwe nhamba.

Kuongororwa uye Miedzo

Kuongororwa kwe-lymphoma kunowanzoitwa neine lymph node biopsy kana node dzakakura dzingawanika nyore nyore, kana nenyuchi inoda (FNAC) pasi pekutungamirirwa kwe CT-scans kana ultrasound scans. Chirwere ichi chinosimbiswa se-lymphoma, uye rudzi rwe lymphoma runotsanangurwa nokutarisa masero ayo pasi pe microscope uye kuongorora kwakakosha . Varwere vatsva vanoongororwa vanofanira kuongororwa mutsva kuti vaone kuti chirwere ichi chinokanganisa sei muviri. Ona chikamu chekuedzwa kwevechangobva kuongororwa .

Prognosis

Kufananidzira kwe lymphoblastic lymphoma kwakafanana nenzira dzakawanda kune leukemias. Izvo zvinoenderana nenyaya dzinoverengeka kusanganisira danho rezvirwere. Zvinhu izvi zvinotsanangurwa muchikamu chekufananidzira kweChina-Hodgkin Lymphoma (NHL) .

Kurapa

Mishonga iri pamiganhu yeukatei pane pane mamwe mishonga. Chemotherapy inopiwa muzvikamu zvitatu - 'induction', 'consolidation', uye 'kuchengetedza'. Induction chemotherapy inosanganisira kutungamirirwa kwezvinodhaka zvinodhaka kuburikidza nekuputika uye mahwendefa kwevhiki shoma muchipatara.

Kutevera izvi mishonga mishoma inoshandiswa mukukanganiswa nguva nenguva kwemwedzi mishomanana kubvisa chero sarudzo dzese dzinosara. Izvi zvinonzi kusunganidzwa. Kugadziriswa kunosanganisira kushandiswa kwezvinodhaka zvinowanzo mukanwa mumuromo kwemakore mashomanana. Vamwe varwere vane lymphoblastic lymphoma vanoita kurapwa nemakemikrapa yakasimba. Muvanhu vakuru, kunyanya kusanganiswa chemotherapi kunopiwa uye mapfupa emapfupa okupinza anogona kuitwa.

Sources:

Mhando dzisiri yeHodgkin lymphoma muvana, American Cancer Society, yakadzokororwa 01/27/2016.

Childhood Hasi-Hodgkin Lymphoma Kuchengetedza-kune vashandi vehutano (PDQ®), National Cancer Institute, January 26, 2016.

Munhu Mukuru Ari-Hodgkin Lymphoma Treatment-yevashandi vehutano (PDQ®). National Cancer Insit, January 15, 2016.