Cataplexy uye Hypocretin Testing Inogona Kusiyanisa Madzimai
Kusagadzikana kwemazuva ose kunowanzozivikanwa nekurara kwezuva kwekurara , asi pane zvimwe zviratidzo uye mitsva yekuedza iyo inoshandiswa kusiyanisa zvinyorwa zvemamiriro acho ezvinhu. Kune mhando mbiri dzechirwere chinokambaira, asi ndeupi musiyano pakati pe narcolepsy type 1 uye firimu 2? Dzidza nezvekusiyana uku, kusanganisira basa rekudzivirira uye kuongororwa kwehutano hwe hypocretin mu-cerebrospinal fluid (CSF).
Zviratidzo zvekunyengedza Zvingave Zvingaita Kusiyana Nedzimwe Nyaya
Zvose zviri zviviri zvechirwere chinosanganisira kusakanganiswa kwekuda kurara kana masikati kunonoka kurara. Pasina hope, narcolepsy haisi yakakodzera kuongororwa. Pane zvimwe zviratidzo zvinosanganiswa, uye zvimwe zvei zvingabatsira kusiyanisa zviduku.
Kune mhando mbiri dzeincolepsy: rudzi rwekutanga 1 uye rudzi rwechipiri. Tsika 1 inogona kusanganisira kuvapo kwechiratidzo che cataplexy. Cataplexy inorondedzerwa sezvikamu zvinopfuura kamwe zvechidimbu, zvinowanzoenzanisa nekurasikirwa kamwe kamwe kwetema musimboti nekuchengetedzwa. Uku kushaya simba kunogona kukanganiswa nemanzwiro akasimba. Aya manzwiro kazhinji anowanikwa zvakanaka; somuenzaniso, cataplexy inogona kusanganiswa nekuseka. Utera hunogona kusanganisira chiso, maoko, kana makumbo. Vamwe vanoratidzirwa vachave nemaputi emaziso, muromo wemuromo, ruvara rwemirimi, kana musoro kubvongodza. Vamwe vanhu vanogona kuwira pasi pasi pakurwiswa kwechikafu.
Zvose zviri zviviri zveincolepsy zvinogonawo kusanganisira kurara kuora mwoyo uye hypnagogic hallucinations . Kurara kwakaparadzana usiku kunowanzoitika mumamiriro ose maviri pamwe chete.
Basa rekuedzwa kwe Hypocretin uye MSLT
Kunyatsoongorora kunogona kushandiswawo kusiyanisa pakati pezviviri zviduku zveancolepsy. Kurara kwezuva masikati kunotsanangurwa kuburikidza nemigumisiro yevhesi yakawanda yekudzivirira latency (MSLT).
Ichi chiyero chinotevera chidzidzo chekurara zvakakwana uye chinosanganisira mikana mina kana mashanu yep nap napano inowanikwa panguva dzenguva 2. Nyaya yacho inopiwa mukana wekurara, uye vanhu vane chirwere chinoputika vachabatwa nehope mumaminitsi masere masere paavhareji. Mukuwedzera, kurara kwe REM kunowanikwa mumaminitsi gumi nemashanu ekurara kunotanga mumikana miviri yep nap.
Uyezve, kuongororwa kwei hypocretin mazinga muScF fluid sechikamu chekuvhara kwemavara kunogona kuzarura. Kana zviyero izvi zvichienzaniswa kuti zvisingasviki 110 pg / mL, izvi zvinopindirana nehutachiona hwechirongwa chechirwere chepano. Kana mazinga ari akajairika (kana kuti asina kuyerwa) uye chikafu chisina kuwanikwa, chinyorwa chechipiri chinonzi narcolepsy chinowanikwa kana MSLT yakanaka. Kana uwandu hwe hypocretin hunowedzerwa kuti huve husina kuitika gare gare, kana kana chikafu chinowedzera, kuongorora kunogona kuchinjwa kuti kuve 1.
Kunyange zvazvo kunyunyuta kunenge kusingawanzoitiki, zvinowanzoitika zvakakwana, nerudzi rwekutanga runobatsira vanenge 1 muvanhu 5 000. Kuongororwa kunofanirwa kuitwa nenyanzvi yekurara iyo inokwanisa kushandisa kuongororwa kwakakodzera uye inopa chirwere chinoshanda.
Kana iwe uine hanya kuti iwe unogona kunge une zviratidzo zvekunyengera, tsvaga kuongororwa nenyanzvi yehope iyo inokwanisa kukupa kutarisirwa uye kutsigirwa kwaunoda.
> Kwakabva:
> American Academy of Sleep Medicine. International classification of disorder, 3rd ed. Darien, IL: American Academy of Sleep Medicine, 2014.