Ikoopathic myelofibrosis, inonziwo agnogenic myeloid metaplasia, chirwere chepfupa remafupa apo marora anoumba mavara uye anobudisa masero asina ropa. Idiopathic myelofibrosis imwe yezvinetso zvemyeloproliferative . Iyi dambudziko inobata varume nevakadzi uye inowanzoonekwa kune vanhu vari pakati pemakore makumi mashanu kusvika makumi manomwe, asi inogona kuitika chero ipi zvayo.
Inofungidzirwa kuti inowanikwa kune 2 kubva kune 1 000 000 vanhu.
Zviratidzo
Vose vanenge 25% yevanhu vane idiopathic myelofibrosis havana zviratidzo. Avo vane zviratidzo zvinogona kuva:
- Chirwere chakawedzerwa, chinokonzera kusagadzikana muchepamusoro-kuruboshwe mumimba kana kurwadziwa mumusoro wepamusoro-kuruboshwe
- Kushaya simba, kuneta
- Kupfupika kwemhepo
- Kuonda
- Night sweats
- Kusatsanangurwa kubuda ropa
Mamwe maitiro akakomba e-idiopathic myelofibrosis angave:
- Mishonga inogadzirwa nekuvandudza masero eropa anogona kuumba kunze kwefupa remapfupa mune chero maronda mumuviri
- Kusvetuka kweropa kunopinda kuchiropa, zvichiita kuti pave nechiitiko chinonzi "portal hypertension"
- Mhemberero dzakashamwaridzana dziri mudumbu, inozivikanwa seesophageal varices, iyo inogona kuputika uye kubuda ropa.
Kuziva
Kune avo vasina zviratidzo, idiopathic myelofibrosis inogona kuwanikwa apo chiitiko chekuongorora chiremba chinowona chirwere chakawedzerwa uye zvisingaenzaniswi zvekuongorora ropa. Izvi zvinogona kuratidza huwandu huwandu hwemasero matsvuku eropa (zvichikonzera chirwere chemaemia ), yakakwirira kudarika nhamba yakasviba yemasero eropa eropa, uye nhamba isingawanzo yemaplatelets (angave ari kumusoro kana pasi).
Vamwe vanhu, zvisinei, vanogona kuratidza kuchinja kuduku muhuwandu hwemasero eropa.
Apo muenzaniso weropa romunhu mumwechete uri kuongororwa pasi pema microscope, masero mashoma eropa anogona kuonekwa. Mimwe miedzo yeropa inogona kunge isinganzwisisiki zvakare. Kuti ibatsire kusimbisa kuongororwa kweidiopathic myelofibrosis, sampu yemapfupa emafuta (biopsy) inotorwa uye iongororwa pasi pe microscope yekuvapo kwe fibrosis.
Kurapa
Vanhu vasina zviratidzo zvinowanzosarapwa. Ropa ropa rinoitwa nguva dzose kuti riongorore chirwere.
Kune avo vane zviratidzo, kurapwa kunobva pakugadzirisa kusafara uye kuderedza dambudziko rezvinetso. Vanhu vane chirwere chekushaya ropa vanogona kuwana iron, folate uye / kana kuwedzerwa ropa. Vamwe vanogona kurapwa nemishonga, yakadai seDeltasone (prednisone) kana Zometa (zoledronic acid).
Vanhu vane huwandu hwemasero eropa vanogona kurapwa nemishonga, yakadai Hydrea (hydroxyurea), Agrylin (anagrelide) kana interferon alfa.
Vamwe vanhu vangave vachida kuti chirwere chacho chibviswa (splenectomy), kunyanya kana chiri kukonzera matambudziko. Mimwe mishonga inogona kusanganisira rayation therapy kana bone marrow (stem cell) transplantation .
Outlook
Paavhareji, vanhu vane idiopathic myelofibrosis vanorarama kwemakore mashanu mushure mekuongororwa. Inenge 20% yevanhu vane chirwere, asi, vanopona makore 10 kana kupfuura. Iyi nhamba iri kuwedzerwa nekufamba kwenguva sekurapa mitsva kunoitwa uye kutsvakurudza kunovandudza ruzivo rwechirwere.
Sources:
> "Idiopathic Myelofibrosis." Disease Information. 24 Sep 2007. Leukemia & Lymphoma Society.
> Niblack, Joyce. "MF FAQ." MPD-FAQS. 3 Feb 1999. MPD Research Center, Inc.