Myelofibrosis inomira apo kuvhara (fibrosis) kunowanikwa mumapfupa emapfupa. Uku kuvhara kunoita kuti zvive nyore kuti mafuta ako epafu aite masero eropa kazhinji.
Zviratidzo
Myelofibrosis inogona kutadza zviratidzo. Zvisinei, zvinogona kutorwa pane basa rekuita ropa rinowanzoitwa nachiremba wako. Zvimwe zviratidzo zvakabatana nekuderedza masero matsvuku eropa ( anemia ) uye platelets ( thrombocypenia ), se:
- Kuneta kana kuneta
- Pallor
- Tsvuku tsvuku paganda rinonzi petechiae
- Kuwedzera kuputika
- Kuwedzerwa kuteura ropa
- Yakapararira spleen uye / kana chiropa - unogona kuona kuzadza pasi pemibvu dzako.
- Bony kurwadziwa
- Fivhiri kana kuti zvirwere zvinowanzoitika
Ndiani Ari pangozi
Myelofibrosis kazhinji inowanikwa kune vanhu vanopfuura makore makumi mashanu. Zvinogona kuitika kune vana asi hazvina kunyanya kuwanikwa. Varwere vane polycythemia vera kana kuti hutachiona hunokosha hunogona kuenderera mberi kukura myelofibrosis.
Nei Chechi Yako Ichiwedzera?
Iyo spleen inhengo yehematopoietic, zvinoreva kuti inogona kuita masero eropa. Mu myelofibrosis, apo marora ane hutano kuita masero eropa, spleen inowedzera kuedza kuvandudza michina.
Zvinokonzera
Primary myelofibrosis inoratidzika isiri yeropa reropa (chikamu chechigarire myeloproliferative neoplasms). Izvi zvinokonzerwa neine genetic mutation. Panguva ino isu hatizivi kuti chinokonzera kuchinja kweizvi kuitika.
Myelofibrosis inogona kukonzerwa nedzimwe mamiriro uye inonzi wechipiri myelofibrosis.
Izvi zvinosanganisira:
- Dzimwe ropa rekenza, kunyanya achirwa megakaryocytic leukemia (rudzi rwemuteyo myeloid leukemia ) kana myelodysplastic syndrome
- Cancer metastasis kusvika pfupa
- Kurwisa zvirwere zvakadai se lupus, scleroderma
- Pulmonary hypertension: Mumamiriro ezvinhu aya, pane kukwira kwepamusoro kweropa mumidziyo yeropa mumapapu.
- Hyperparathyroidism inobatanidza nehuwandu hwevhitamini D
- Grey platelet syndrome
- Renal ostoeodystrophy: Ichi ndicho chirwere chemamineral uye bone metabolism inowanikwa kune varwere vane chirwere chisingaperi chepfungwa.
Kuziva
Pakutanga, kuderera kwehuwandu hwehuwandu hwemazi kunoonekwa pahuwandu hwehuwandu hweropa . Kazhinji, anemia uye / kana thrombocytopenia zviripo. Kukanganisa kwemasero eropa kunowanzoonekwa pane imwe yeropa ropa smear, microscope slide yedonhi reropa. Masero matsvuku eropa anowanzotsanangurwa seanotarisa se teardrop.
Kugadziriswa kwekupedzisira kunoda mapfupa emapfupa, maitiro apo chikamu chiduku chemasese chinobviswa. Nechipfupa chakakosha, micheka yakagadzirwa nemafuta mumapfupa emapfupa inogona kuonekwa.
Penguva yekuongorora basa-up, chiremba wako achaedza kuziva chinokonzera myelofibrosis. Ichinyorwa mubasa iri richava mazita ekuongorora mazita ekugadzirisa kwakasiyana-siyana kunonzi JAK2, MPL, uye CALR.
Kurapa
Kurapa kunobva pane chinonyanya kukonzera. Kurapa kwekutanga myelofibrosis kunotsanangurwa nehuwandu hwekuwedzera kwezvirwere uye kuponeswa kwese.
- Kucherechedza: Kana iwe usina zviratidzo zvikuru, kurindira kumirira kungave sarudzo yakanakisisa yekurapa.
- Kufuridzira: Inemia uye thrombocytopenia inowanikwa myelofibrosis inogona kuva yakaoma uye inogona kudikanwa kuwedzerwa kuwedzerwa ropa. Kakawanda kwekuwedzerwa ropa kunogona kusarudza kana kurashwa kwakanyanya kuchidiwa.
- Bhoora marora (stem cell) kuiswa: Chisarudzo chekugadzirisa chinofanirwa kuyerwa zvakanyatsocherechedza zvose zvinopisa uye zvinobatsira.
- Ruxolitinib: Mishonga iyi inodzivisa JAK2 inogona kushandiswa kune varwere vane mutsauko weJAK2 vane zviratidzo zvikuru uye havakwanisi kuwana bone marrow transplantation.
- Splenectomy : Kana chirwere chisina kuderera mukukura kubva pakurapa, chinogona kubviswa chirwere.
- Hydroxyurea: Hydroxyurea inorapwa chemhemotherapy mishonga inogona kushandiswa kuderedza ukuru hwepleen nemamwe zviratidzo.
- Mimwe mishonga yakafanana na androgen uye thalidomide
- Radiation therapy ingashandiswa kuderedza ukuru hwepleen
Kurapa kwechipiri myelofibrosis inotungamirirwa pachikonzero chinokonzera. Saka kana myelofibrosis inokonzerwa nekenza yakadai seyakanyanya myeloid leukemia (AML), inobatwa nekemotherapy. Kana myelofibrosis inowedzera kune chirwere chemotokari, chirwere chechirwere ichocho chinogona kuwedzera kuwedzerwa ropa.
Chero chii chingaitwa kurapwa kwako, boka rako rezvechiremba richakufamba nematanho ose aunoda kutora kuti uve mukutarisira hutano hwako. Usanonoka kuudza pfungwa dzako, mibvunzo, uye manzwiro navo.