Iyo Yakanyanya Nervous System Disorder Kazhinji Inorasikirwa neChinsinson
Multiple system atrophy (MSA) chirwere chinokonzera kuti zvikamu zvakawanda zvehutano hwemagedha zvipere. MSA inosanganisira matatu syndromes: Shy-Drager syndrome, striatonigral degeneration, uye olivopontocerebellar atrophy. MSA chirwere chinopfuurira chinokanganisa utongi hwehutongi hwehutongi, chikamu chemuviri wako chinodzora zviito zvisingazivikanwi sekudya uye kufema.
MSA inokanganisa chero ipi zvayo kubva kune vanhu vaviri kusvika ku15 vanhu pa100 000. Zvinogona kutora nguva kuti uwane MSA kuongororwa nekuda kwekufananidzwa pakati peMSA nedzimwe mamiriro ezvinhu, zvakadai sehosha yaPasinson . MSA inowanzoongororwa inenge makore makumi mashanu emakore uye inoonekwa kuvanhu vemarudzi ose. Kana imwe zviratidzo zvatanga, chirwere ichi chinowedzera kufambira mberi nokukurumidza.
Zviratidzo zveMatongerwo Enyika Atrophy
MSA zviratidzo zvinobva mukurasikirwa kwemasero emagunha mumamiriro emagetsi. Chii chinokonzera kurasikirwa uku kwemasero emagetsi kusati kuchizivikanwa. Vanhu vazhinji vane MSA chiziviso chechi mptoms, sekunyanya kusagadzikana, erectile kushaya simba mukati mevarume, kudonha muropa yepamusoro apo vakamira (orthostatic hypotension), kupera simba, nekudzivirirwa. Sezvo zviratidzo zvinopfuurira, zvinowanzowa pasi pemumwe wemapoka maviri:
- Parkinsonian type (MSA-P): izvi zvinosanganisira zviratidzo zvakafanana nehosha yaPasinson yakafanana nokudengenyeka kwezororo, kusagadzikana kwemisungo, uye kunonoka kunonoka
- Cerebellar type (MSA-C): inosanganisira kuoma kufamba (ataxia), nyaya dzinochengetedza kuenzanisa, uye zvinetso kurongedza kufamba kwezvizvi.
Zvimwe zviratidzo zvinosanganiswa neMSA zvinosanganisira kuoma kutaura kana kumedza, kurara kweputi, uye kutonhora maoko. Vamwe vanhu vanogonawo kukura chirwere chehope, musuru uye tendon kupfupika, Pisa syndrome - apo mutumbi unoita seunoomerera kune rumwe rutivi, kugomera kusingabatsiri, uye antecollis - inoitika apo mutsipa unotama mberi uye musoro unoderera pasi.
MSA inozivikanwa sei
Zvinogona kuva zvakaoma kusiyanisa MSA kubva kuPalinson's disease . Imwe nzira yekusiyanisa pakati pezviviri ndeyokuona kuti nokukurumidza chirwere ichi chinowedzera sei. MSA inotanga kufambira mberi nokukurumidza kupfuura Parkinson's. Vanhu vazhinji vane MSA vachada chigadziro chekubatsira, sechigaro chevasimhudhudai kana kuti mumiti, mukati memakore akawanda ekuonekwa.
Imwe nzira yekusiyanisa pakati pezviviri ndeyekurapa Parkinson. MSA haina kupindura zvakanaka kune levodopa, mushonga unoshandiswa kurapa Parkinson. Zvinosuruvarisa, an autopsy ndiyo nzira chete yekugadzirisa kuongorora MSA. Kunyanya kuongororwa, kwakadai sePET scan (positron emission tomography), kunogona kutonga kune dzimwe mhando dzehutano husingawaniki neurological.
MSA Treatment
Parizvino, hapana mushonga weMSA, uye hapana marapirwo akangogadzirirwa kuchinja kana kumira zvirwere. Zvimwe zvikamu zvehutano zvinokanganisa uye zvakaoma kurapa. Zvinetso zveMovement zvinogona kurapwa ne levodopa uye carbidopa (Sinemet), asi izvi zvinowanzova nezvikamu zvishoma.
Mimwe mishonga yakadai se bromocriptine (Parlodel), trihexyphenidyl (Artane), benztropine mesylate (Cogentin), uye amantadine (Symmetrel), inogona kupawo mamwe mupiro wezviratidzo.
Kurapa kwepanyama, kusanganisira aqua therapy, kunogona kubatsira kuchengetedza mishonga, uye kutaura kwemazwi kunogona kubatsira kuwedzera chero matambudziko ekumedza kana kutaura.
Zvinotsvakurudzwa neUtsvakurudzo
Chinyanyozivikanwa nezvemichina yekushanda mune dzakawanda system atrophy. Vatsvakurudzi veNational Institute of Neurological Disorders uye Stroke (NINDS) vari kuedza kutsvaga kuti sei protini alpha-synuclein inowedzera mumagetsi emasero (masero anopa kudzivirirwa kweeurons mumutambo wekutya) wevanhu vane MSA uye neuronal (mitsipa) masero evanhu vane chirwere chePasinson. Chirwere chemakiriniki chakashandisa kushandisa drug drug rifampicin kuderedza chirwere chekuwedzera, asi kurapwa kwakanga kusingabatsiri.
Dhiyabhorosi kubva padzidzo iyi yava kushandiswa mune dzimwe dzidzo dzeMSA.
Sources
Diedrich, A., & Robertson, D. (2002). Multiple system atrophy. eMedicine, yakawanikwa pa http://www.emedicine.com/neuro/topic671.htm
National Institute of Neurological Disorders uye Stroke. Multiple System Atrophy Fact Sheet. November 2014.