Kufambira mberi mukutsvakurudza kweBioogenetic Kunowedzera Upenyu Hupenyu
Cystic fibrosis (CF) chirwere chinopfuurira chinokanganisa zvose hupenyu hwehupenyu uye nguva yeupenyu kune avo vanorarama nechirwere. Kunyange zvazvo inyanzvi chirwere chisingawanzo (chinongoda vanhu vanenge 30 000 vari muUnited States), ichiri kuonekwa seimwe yemapararira akapararira, mararamiro ekugadzirisa mararamiro.
Kunyange zvazvo tarisiro yehupenyu yevanhu vane CF inoramba iri pasi peiyo yevanhu vakawanda, kuwedzera kunzwisisa nezvechirwere, pamwe chete nemishonga inobatsira , yatanga kuchinja zvinhu.
Upenyu Husingatarisiri Kuwana Muvanhu NaCystic Fibrosis
Muna 1938, apo CF yakatanga kuzivikanwa sehosha, vana vakawanda vakawana chirwere chacho vakafa vasati vaberekwa kwekutanga. Pakazosvika makore makumi mashanu, vanhu vane CF vairarama kwenguva yakareba asi kazhinji havana kuita kuti vafambe vachiri vaduku. Apo zvinhu zvakatanga kuvandudzwa nema1980, apo vanhu vava kurarama kusvika pakati pekupera kwema makumi maviri, hazvina kusvika kusvikira kuwanikwa kweCFTR gene muna 1989 kuti takatanga kuona kuchinja.
Mazuva ano, ane zvombo zvakanyatsonzwisisika nezvemaitiro eCF, tine nzira dzekutarisa zviri nani chirwere, kudzivirira utachiona, uye kuvandudza mapapu mukati meavo vanorarama nedambudziko.
Somugumisiro, chiyero chekurarama kwehupenyu kwevanhu vanogara neCF nhasi nderamakore 37.5. Munyika yakagadzirwa, chiyero ichocho chakanyanya kunyanya nekufungidzirwa kubva kune chero 42 kubva kune makore makumi mashanu.
Nekufambira mberi mukurapa uye inyanzvi yehupenyu, vatsvakurudzi vanofanotaura kuti vana vanozvarwa nhasi vanogona kurarama zvakanaka kunze kwekuzvarwa kwavo kwema50.
Upenyu Huri Kuwedzera Hwokubatanidza Uchibatanidza Kumushonga WeAnbiotiki
Vanenge 80 kubva muzana yevanhu vane cystic fibrosis vachawana hutachiwana nePseudomonas aeruginosa , bhakitiriya rinowanzoonekwa sekupararira kwose kwose kwepasi.
Vanhu vane CF vari pangozi yakakura yeP. aeruginosa , hutachiona hwehwo hunogona kutungamirira mukushaya kuputika uye kunyange rufu.
Kutaura zvazviri, 50 muzana yevanhu vane CF avo vari muchipatara cheP. aeruginosa vachafa nekuda kwehutachiona.
Nenzira, kune mamwe akawanda mishonga nhasi ayo anogona kubata nekudzivirira P. aeruginosa chirwere. Izvi zvinosanganisira antibiotics tobramycin, levofloxacin, ciprofloxacin, azithromycin, uye yakareba-spectrum cephalosporins. Kusarudzwa kwezvinodhaka kunowanzotarisirwa kuongororwa kuongorora kusvibiswa kwesimba rePseudomonas kumasarudzo akasiyana-siyana emishonga inorwisa mabhakitiriya.
Kutarisira kunopesana nemhando uye chikwata chekutapukirwa. Inhaled tobramycin kana levofloxacin inowanzopiwa kwemwedzi panguva imwe kudzivirira kubhakitiriya kukura. Nyaya ciprofloxacin uye azithromycin inogona kushandiswa kudzivirira utachiona kana kubata chirwere chakapo.
P. aeruginosa inogonawo kurapwa nemhando ye penicillin inonzi ureidopenicillin.
Zvimwe Kufambira Mberi Mukurapa kweCystic Fibrosis
Mukuwedzera kune mamwe maitiro ekurapa maantibhakitiriya, mamwe hufambiro akaitwa mukurapa kwemapfupa maviri nemapapu ane chokuita neCF. Dzinosanganisira:
- pancreatic enzyme supplementation kuti ikunde zvinetso zvekudya nemhaka yekuvakwa kwekamu mumugwagwa wezvokudya
- Pulmozyme (dornase alfa) iyo inoputira rukato runodzivirira kufamba kwemhepo
- bronchodilators (inhalants dzinofamba nzvimbo dzomugwagwa dzakashama)
- yakagadziriswa anti-inflammatory medication
- inhaled hypertonic saline kuwedzera muwandu weasarasi yakarasika mumhepo
Zvose izvi zvinobatsira pakuwedzera kwehupenyu hwevanhu vane CF.
Shoko Rinobva
Cystic fibrosis chirwere chakasiyana kwazvo kupfuura chaiva makore makumi maviri kana makumi matatu adarika. Nhasi, vanhu vane CF vanogona kurarama hupenyu hwakasimba uye hunogutsa, kuenda kuchikoroji, kuwana mabasa, uye kuronga mhuri. Zvose zvinonyanya kutora matanho matanhatu ekuvimbisa hupenyu hurefu uye hupenyu:
- kunzwisisa zvirwere zvako uye kuitora sezvinorayirwa
- kuvimbisa kudya kwakanaka, kwakaringana ne50 muzana yekoriyori munhu wepakati
- kunwa mvura yakawandisa kuti ugare wakachengetwa zvakanaka
- kusika chirongwa chepfungwa chakakonzerwa nekudzivisa uye cardio kudzidziswa
- kudzivisa utachiona nekushamba maoko ako nguva dzose, kuwana zvirwere zvako, nekudzivirira vamwe vanorwara
- kuona chiremba wako nguva dzose kuti ave nechokwadi chekuenderera mberi kwekutarisira
Pakupedzisira, cystic fibrosis haisi chirango chekufa chaiwanzove, uye, nekuchengetwa kwakanaka uye kurapwa, hapana chikonzero nei iwe usingakwanise kudarika zvinotarisirwa mune zvose uye huwandu hwehupenyu.
> Kwakabva:
> O'Sullivan, B. uye Freedman, S. "Cystic fibrosis." Lancet . 2009; 373 (9678): 1891-1904.