Pulmonary arterial hypertension chirwere chakakomba kune zvirapa asi hapana mushonga, maererano neNational Heart, Lung, uye Blood Institute. Secondary pulmonary arterial hypertension inogona kukonzerwa kana kuti inoitika nekuda kweimwe chikamu chechipiri.
Pulmonary Hypertension Causes
Pulmonary arterial hypertension (kana kukwirira kweropa mukati mumapapu) chinhu chisingawanzoitiki asi chirwere chakakomba zvikuru.
Dambudziko iri, risingaenderani nekuwedzera systemic ropa (hypertension), inokonzerwa nekurasikirwa kwemapapu yevhesi uye kurasikirwa kwechimiro (elasticity) yemapurmonary arteri iyo basa rekudzorera ropa kumapapu eoksijeni.
Rheumatic Diseases Associated With Pulmonary Hypertension
Pulmonary hypertension inosanganiswa nemitemo yakawanda. Mune varwere vane chirwere chakakura chemapapu (fibrosis sezvinoonekwa mu scleroderma uye dzimwe nguva rheumatoid arthritis ), pane hutaputi hwemapapu hunoita kuti mwoyo uwedzere kuwedzera kudiwa kunosundira ropa kuburikidza nemapurmita arteri kumapapu. Vamwe varwere vanowedzera huwandu hwemishonga inokonzerwa nemishonga inokonzerwa nekuderedza mishonga. Izvi zvinogona kuonekwa mumamiriro ezvinhu akadai se scleroderma (kazhinji mumutauro wakadana unonzi CREST) kana kuti zvisiri nyore lupus (systemic lupus erythematosus). Munguva pfupi iyi chirwere chepachimona chepachimona chakawanikwa chichibatanidzwa nekudya zvinodhaka zvisingawani pamusika.
Zviratidzo
Zviratidzo zvechiitiko ichi zvinosanganisira kukurumidza kufema uye kurwadziwa kwepfuva. Kuongororwa kunogona kuratidzirwa ne-non-invasive ultrasound yemwoyo (echocardiogram). Cardiac catheterization (mwoyo catheterization) iyo ine zvimwe zvinetso zvehutano inowanzoitwa kugadzirisa kuongororwa.
Kurapa
Munguva yakapfuura, pakanga pasina mushonga muduku waiwanika kune dambudziko iri raitakura kurasika kwakashata.
Nenzira yakanaka, pane mishonga mitsva inowanikwa kubatsira varwere vane chirwere chavo kusanganisira:
- epoprostenol (pfupi-inodhaka zvinodhaka zvinoda kuramba zvichiri kuvharwa neV IV)
- treprostinil (inoshandiswa nekuenderera mberi kwechikamu chemukatikati)
- bosentan (akapiwa muromo)
- sildenafil (yakapiwa nomuromo)
- iloprost (inhaled)
Zvimwe zvipatara zvinosanganisira oxygen, ropa thinners, diuretics uye cardiopulmonary rehabilitation. Kana akawanikwa ane dambudziko iri, zvakanakisisa kuona chiremba wemapapu ane unyanzvi mune chirwere ichi.
Mhinduro yakapiwa naScott J. Zashin, MD, purofesa mupurezidhendi mudzidzisi paYunivhesiti yeTexas Southwestern Medical School, Division of Rheumatology, muDallas, Texas. Dr. Zashin zvakare ari kuenda kuchiremba muPresbyterian Hospitals yeDallas uye Plano. Iye ishamwari yeAmerican College of Physicians uye American College of Rheumatology uye nhengo yeAmerican Medical Association. Dr. Zashin munyori weArthritis Pas Pain - Mirairo yeAnti-TNF Blockers uye mubati wenhengo yeAtmal Arthritis Treatment .