Mumiriyoni Pashure Pokuziva
Kana iwe kana munhu waunoda akawanikwa ane amyotrophic lateral sclerosis (ALS), inonziwo chirwere chaLou Gehrig, imwe yemibvunzo yako ndiyo inofanirwa nehosha iyi. ALS inobatsira zvikuru pamutariro wehupenyu asi kune mishonga inogona kuderedza kurasikirwa kwenyama uye inogona kuwedzera hupenyu.
Chii Chinonzi ALS?
ALS chirwere chinonzi neurodegenerative chinokanganisa masero emagetsi muuropi uye musipinha.
Iyo chirwere chinopfuurira chinokanganisa majini neuroni anosvika kubva kubva muuropi kuenda kumutsipa wepelinha. Aya neuroni anodzora misumbu mumuviri wose. Nokufamba kwenguva, uropi hunorasikirwa nehutano hwekudzivirira hutundu hwemishumo nekuda kwekufa kweizvi motokari.
ALS Upenyu Husingatarisiri
Ivhareji inotarisirwa kurarama kwemunhu ane ALS makore maviri kusvika mashanu kubvira panguva yekuongororwa. Zvisinei, zvakasiyana zvikuru:
- Vanopfuura 50 muzana yevanhu vane ALS vanorarama makore anopfuura matatu.
- Makumi maviri kubva muzana anogara makore mashanu kana kupfuura.
- Tumi muzana vanogara makore gumi kana kupfuura.
- Vashanu muzana vanogara makore anopfuura makumi maviri.
Nzira Dzokuwedzera Hupenyu Husingatarisiri
Kunyange zvazvo pasina mushonga weAIDS kana nzira dzekumisa kufambira mberi kwechirwere zvachose, pane zvimwe zvaungaita kuti uvandudze kutarisira hupenyu. Izvi zvinosanganisira:
- Mishonga: Riluzole yave iri kushandiswa kubvira muna 1995 uye yakaratidzwa mumakiriniki emakiriniki akafuridzirwa maviri akashongedzwa kuti awedzere kutarisira kwemakore kwemwedzi miviri kusvika mitatu, kunyange zvazvo zvimwe, zvidzidzo zvishoma zvakanyanya zvakaratidza kuti mushonga wacho unobatsira zvikuru. Mukuwedzera, mamwe mishonga inoshandiswa mukuratidza zviratidzo zvinogona kubatsira kuvandudza hupenyu hwehupenyu nekuwedzerwa kushanda. Radicava (edaravone) yakagamuchirwa muna 2017. Mumakiriniki ekuedza, yakaderera kuderera mukushanda.
- Noninvasive Ventilation: Kushandiswa kwemhepo isina kuputika (NEV) yakaratidzwa kuti iwedzere kupona pakati pemwedzi manomwe ne11, zvichienderana nekushandiswa kwaiitwa zuva rega rega uye zvirwere zvakasiyana-siyana. Inonyanya kumira ye NEV yakanaka-kusvitsa mhepo, iyo inopfurikidza kufema kuburikidza nemasikisi inoenderana nemuromo nemhino.
- Percutaneous Endoscopic Gastronomy (PEG): Bhuku rekudya rinoiswa mudumbu uye rinotungamirira kunze kwemuviri kuburikidza nemadziro emimba. Kunyange zvazvo zvidzidzo zvakakundikana kuratidzira kusagadzikana kunokonzerwa nekupona nguva, American Academy of Neurology inokurudzira kuti PEG inoshandiswa kuvanhu vane ALS kuchengetedza uremu hwemuviri hwakasimba. Vanachiremba vakasiyana vane maonero akasiyana pane nguva yakanakisisa yekuita chirongwa chePGG uye vanotanga kudya nenzira iyi.
Shoko Rinobva
Kufambira mberi kwakaitwa mumakore achangopfuura mukutsigirwa uye kurapwa kweAIDS. Kuzvidzidzisa pane kurapwa uye kusarudzwa kweAIDS kunogona kukubatsira kunzwisisa izvi zvakaoma uye zvakaoma kuongororwa. Taura nechiremba wako pamusoro pezvaunogona kuitwa kuti ubatsire munhu ane ALS kurarama zvakanyanya kunyatsonaka kwenguva yakareba sezvinobvira.
Sources:
> Zvinhu Zvaunofanira Kuziva Nezve ALS. ALS Association. http://www.alsa.org/about-als/facts-you-should-know.html.
> Frequently Asked Questions About Radicava (Edaravone). ALS Association. http://www.alsa.org/research/radicava/radicava-kudaro-asked-questions.html.
> Miller RG, et. al. Practice Parameter update: Kutarisira kwomurwere neamyotrophic lateral sclerosis: Zvinodhaka, noutano uye kuporesa maitiro (kubvunzurudzwa kwakagadziriswa): Mushumo weMitemo yeBumbiro reMitemo yeAmerican Academy of Neurology. Neurology 2009; 73; 1218-1226.
> Pinto S, Carvalho MD. Kuita kuti hupenyu hutsva huve hutano hwekufema kunopera muAmyotrophic lateral sclerosis varwere. Neurodegenerative Disease Management . 2014; 4 (1): 83-102. doi: 10.2217 / nmt.13.74.