Platelet function disorders iboka rematambudziko ekubuda ropa apo maplatelet haashande zvakakodzera, zvichiita kuti kubuda ropa. Kukanganisa uku kunogona kupiwa nhaka (kudarika mumhuri) kana kuwanikwa (yakagadzirwa panguva inotevera).
Ndezvipi zviratidzo zvePlatelet Function Disorder?
Platelets ndeimwe chikamu chekuvhara, system iyo inotibatsira kusamira ropa.
Kana maplatelet ako asingashande zvakanaka, iwe unowedzera ngozi yekubuda ropa. Zviratidzo zvinogona kusanganisira:
- Kuwedzera kuputika
- Nosebleeds
- Gum ropa
- Menorrhagia (kunyanya kubuda kumwedzi kunopa ropa)
- Kubuda ropa kwenguva refu mushure mekucheka kana kumwe kukuvara
- Kubuda ropa kwenguva refu nekuvhiya
Chii chinokonzera Platelet Function Disorders?
Platelet function disorders inogona kugoverwa muzvikamu zviviri zvakakura: congenital (nhaka) kana kuwanikwa. Ruzhinji rwevhiringidzi urwu huri kuberekwa, kusanganisira:
- Glanzmann's thrombasthenia
- Bernard-Soulier syndrome
- Grey platelet syndrome
- Matambudziko anokonzerwa neHIMH9: May-Hegglin anorwara, Epstein syndrome, Fechtner syndrome, uye Sebastian syndrome
- Wiskott-Aldrich syndrome: Ichi chirwere chema immunodeficiency uye hachina basa maplatelet. Iyo inoratidzirwa nediki duku maplatelets (akawanda eplatelet function disorders ane ruzha kune maplatelet makuru).
- Chediak-Higashi syndrome
- Hermansky-Pudlak chirwere
Zvinokonzerwa zvinokonzera zvinosanganisira:
- Mishonga: Mishonga yakafanana ne aspirin, dipyridamole (Persantine), uye clopidgrel (Plavix) yakagadzirirwa kuderedza basa remaplatelet. Ibuprofen inoderedzawo kubudirira kweplatelet asi pasi pe aspirin.
- Chiropa chechiropa
- Uremia (chirwere chakanyanya renal)
- Zvinetso zveMyeloproliferative sehutano hunokosha hunokosha
Ndeapi Platelet Function Disorders Inozivikanwa?
Akarwisana nedzimwe mararamiro eplatelet, ayo anowanzotarisana nenhamba eplatelet (yakakwirira kana kuti yakaderera), zvinokonzera mapeletlet function zvinogona kuva nemavara eplatelet anoverengeka.
Dzimwe mhando dzeplatelet function disorders dzinogona kuva ne- thrombocytopenia , kana kuti pasi petelet count. Maplatelets anofanira kuongororwa pasi pe microscope pane imwe ropa rega smear. Mamwe mazana e congenital platelet matambudziko anoshanda anokonzera maplatelets ari makuru kudarika. Zvimwe zvinoshaikwa zvinokosha zveplatelets, inonzi granules, inogona kuonekwa. Dzimwe nguva maplatelets anowanzoonekwa mukuonekwa uye kukura.
Basa rakasara-rinotanga zvakafanana kune mamwe matambudziko ekubuda ropa. Akarwisana nehemophilia (chirwere chekugadzirisa zvinhu), kuongorora maitiro seprothrombin nguva (PT) uye chikamu chepromboplastin nguva (PTT) yakajairika. Kuongororwa kweplatelet function disorders kunoda kuongororwa kuongororwa. Pasi pane pfupi pfupi mazita ezvidzidzo zvinowanzoshandiswa.
- Nguva yokubvisa: Uyu muedzo hauna kufungidzirwa zvakananga kune mapapletlet function disorders uye nekuda kwekugadzirisa kuedza hakusi kuongororwa kwakajeka kwekuvhara maitiro.
- Platelet function assay: Izvi zvinofungidzirwa nevakawanda kuti vanyatsoongorora kuongorora kweplatelet disorders. Uyu muedzo unoshungurudzwa ne platelet count uye inogona kunge isina kururama kana uine pasi peplatelet zvinyorwa.
- Platelet aggregation test: Uyu muedzo unotarisa kuti maplatelet anonamatira sei kune vamwe (aggregation) mukupindura zvakasiyana siyana. Uyu muedzo unogona kushandiswa kuyera kubudirira kweAspirin kana clopidogrel (Plavix) therapy.
- Platelet electron microscopy: Iyi inzira yakanakisisa yekuona maplatelet ane microscope inokosha iyo inogona kuona chikamu chimwe nechimwe cheplatelet.
Ndeapi Mishonga?
Kurapa kunobva pane mumwe munhu platelet function disorder iwe unayo. Zvimwe zvinetso zveplatelet function hazviwanzodi kurapwa kunze kwekuti iwe wakakuvadzwa kana kuti unoda kuvhiyiwa.
- Aspirin uye NSAIDs: Dzivisa aspirin kana kuti kwete-steroidal anti-inflammatory (NSAIDs) kufanana ne ibuprofen. Iyi mishonga inoderedza basa remaplatelet zvinogona kukuvadza kubuda ropa.
- Utachiona hweHormonal: Kufanana nezvimwe zvikonzero zvinokonzera kubuda kwemwedzi kunonoka, zvirwere zvekuberekwa kwehomoni zvinogona kushandiswa kuchengetedza kumwedzi kunopa kusvika kudiki.
- Anti-fibrinolytic mishonga: Nokuti zvinogona kuva zvakaoma kuti muviri uite mazamu akachengeteka, kunyanya panzvimbo yepamusoro yemucosa (muromo, mhino, nezvimwewo), mishonga inofibrinolytic yakadai seAmicar kana Lysteda inogona kushandiswa kurega kubuda ropa. Iyi mishonga inowanzoshandiswa mumamiriro ezvinhu aya e nosebleeds, gum ropa, uye menorrhagia. Inogonawo kushandiswa mushure mekuvhiya (zvikurukuru, muromo, mhuno, uye nehuro) kuitira kudzivirira kubuda ropa.
- Platelet kuwedzerwa: Kunyange muplatelet function zvinetso nemaitiro akazara eplatelet, kuwedzerwa kweplatelet kunogona kushandiswa pakubuda ropa kana kuti kana uchida kuenda kuvhiya.
- Chinhu VIIa (NovoSevenRT) kuvharwa: Ichi chinhu chinogadziriswa chigadzirwa chinogona kushandiswa kune vamwe varwere vane mapepa ekushanda kweplatelet. Izvi zvinoshandiswa kunyanya mune varwere vasingakwanisi kugamuchira kuwedzerwa kweplatelet sekusarudzwa kwoutano.