Pel-Ebstein Fever

Pel-Ebstein ndeimwe yenzira dzakawanda dzefivha dzinozivikanwa navanachiremba

Pel-Ebstein ine feversi yepamusoro yakaramba ichikwira uye ichiwa mazuva manomwe kusvika ku10 kusvika ku10. Fivhiri inomuka pakarepo, inogara yakakwirira kwevhiki kana kupfuura uye zvino inowira pedyo nekugara zvakare zvakare, ichigara pasi kwevhiki. Zvadaro izvi zvinomuka uye muenzaniso wekuwa unodzokorora zvakare. Nokudaro, vanachiremba vanofanira kuziva kuti kutaridzika kwomunhu kwave kuitei kwevhiki dzinoverengeka kuitira kuti vaone Pel-Ebstein fever.

Haasi vese varwere vane chirwere cheHodgkin vane chirwere ichi. Zvechokwadi, vashomanana chete ndivo vane chimiro chaiyo. Zvisinei, kana iripo, inogona kuva chiyeuchidzo chakasimba chekutsvaga Hodgkin lymphoma inogona kunge yakakodzera.

Fever ndeimwe yezvimwe zviratidzo zvinokosha zveHodgkin lymphoma, inonziwo Hodgkin chirwere. Uyu muenzaniso wefivha yakatumidzwa zita rechiremba vaviri veEurope, Pieter Pel naWilhelm Ebstein, avo vakacherechedza uye vakaudza iyo muenzaniso kupfuura makore zana shure.

Zvimwe pamusoro pePel-Ebstein Fever

Chirwere chekare chinopinda mukati chinowanikwa munenge 35 muzana yevanhu vane Hodgkin lymphoma; asi Pel-Ebstein fever-high fever kwemavhiki maviri, akatevera pasina fivhiri kwemavhiki maviri-inoonekwa seashoma muHodgkin lymphoma.

William Ebstein aiva chiremba wechiGermany uye chipatara akatsanangura chimwe chinhu chinonzi "remittent pyrexia inowanikwa muLymphadenoma" muna 1887. Pieter Klazes Pel akatsanangura ichi chiitiko chinowanikwa neHodgkin lymphoma mwedzi mishomanana yapfuura mumagazini imwechete, saka zita rokuti Pel-Ebstein fever.

Kubvira panguva iyo, pane kukakavadzana kwakavapo pamusoro pokuti kazhinji Pel-Ebstein fever inowanikwa sei muHodgkin lymphoma. Vamwe vakataura kuti, nokuti zita refivha rinotarirwa munhau, vadzidzi vemishonga vanogona kunge vachiziva zvakawanda Pel-Ebstein's link kuHodgkin lymphoma kupfuura yakakodzera, zvichienderana nekushaya simba kwesangano.

Kunyange zvakadaro, nguva nenguva fever in lymphomas inonyatsoratidzwa mumabhuku ekurapa. Heino nyaya yakashandurwa kubva mumushumo we1995 mu "New England Journal of Medicine" iyo pakutanga yakaratidza girafu yekushisa kwemunhu uyu, iyo inokonzera kutonhora kwakanyanya uye normalizing mumagariro, kwemavhiki mashoma:

Case Report:

Mumwe murume ane makore makumi mashanu aiva nefivha, usiku hwekutuka, uye kukora kusingabatsiri kwevhiki gumi. Akatora mishonga yekurwisa fever panguva ye febrile nguva. Mudzimai wake akanyora kutonhora kwake pamusoro pemazuva 56 emashure makumi mana. Chirwere chekuwedzera kwechirwere chechiberekeri chinonzi lymph node chakabudiswa nodular kuongorora Hodgkin's lymphoma. Chirwere chemurwere nemamwe zviratidzo zvakanyangarika zvakanyangarika mushure mokutanga kwemakemikari.

Zvimwe pane Fever Patterns

Hondo mapepa anorondedzerwa mumhando dzose dzemitauro yakasiyana-siyana, iyo inogona kuva inokonzera kuvhiringidzika -iyo, mapepa epakatikati, fever remittent, fever inogadziriswa, fever fever, etc. Mune zviitiko zvakawanda, maitiro aya anogona kuva anongoratidzi asi haasi chaiwo kune chero kunyanya chirwere. Zvisinei, heano zvimwe zviito izvo vanachiremba dzimwe nguva vanofunga:

Kudzorera mafungu ane nguva iyo varwere vasina kupisa kwemazuva rimwe kana kupfuura pakati pefivha episodes zvinogona kuonekwa nemarariya , rakat-bite fever, Borrelia mawere - echirwere cheLyme chirwere , uye lymphoma.

Zvikamu zvekare zvemafivha pamusoro pemwedzi mitanhatu zvinogona kuratidza hutano hwakasiyana hwezvirwere, kusanganisira immunodeficiency states .

Kuwana chii chinokonzera kupisa kwemafivha mune dzimwe nguva mamiriro akaoma kwazvo. Iwe unogona kudzidza zvakawanda pamusoro pehurukuro iyi pane fevri yechiratidzo chisingazivikanwi, cheFUO .

> Sources:

> NCCN Clinical Practice Guidelines muOncology: Hodgkin Lymphoma. Version 2.2015. National Comprehensive Cancer Network.

> Eichenauer DA, Engert A, André M, Federico M, Illidge T, Hutchings M, et al. Hodgkin's lymphoma: ESMO Clinical Practice Guidelines yekuongorora, kurapa > uye > kutevera. Ann Oncol . 2014 Sep. 25 Kubatsira 3: iii70-5

> Schattner A, Keshet N. Pel-Ebstein cyclic fever: kwete kungoita lymphoma. Am J Med. 2010; 123 (7): e3.

> Racchi O, Rapezzi D, Ferraris AM, Gaetani GF. Kazhinji mapfupa emapfupa ekudzoka kwechirwere cheHodgkin nechimiro chePel-Ebstein fever. Ann Hematol . 1996; 73: 39-40.

> Zvakanaka G, DiNubile M. Cyclic Fever muHodgkin's Disease (Pel-Ebstein Fever). N Engl J Med . 1995; 332: 436.