Kutamba Maziso Kutamba Maputso
Opsoclonus-myoclonus syndrome (OMS) chirwere chinoputika neurological disorder. Inokonzera matambudziko makuru nemagetsi emagetsi, kufamba kweziso, maitiro, kukanganiswa kwemitauro uye zvinetso zvekurara. Inowanzouya pakarepo uye inowanzosingaperi; kana wakamboonekwa kuti une opsoclonus-myoclonus syndrome, inogona kunge yakagara muupenyu hwako hwose.
Zita rayo rinotsanangura zviratidzo zvaro: opsoclonus inofambisa maziso uye mayoclonus zvinoreva kusagadzikana kwemafupa. Inonziwo "Kinsbourne syndrome" kana kuti "kutamba-meso-kutamba-tsoka."
Ndiani ari pangozi
Mune chirwere chekudzivirira , muviri unorwisa masero awo ane utano. Opsoclonus-myoclonus syndrome inokonzerwa nehutachiona hwemotokari umo muviri wezvirwere zvemuviri zvinopindura kune utachiona hwehutachiona kana tumarara inonzi neuroblastoma. Chero zvazvingaitika, zvirwere zvinopedzisira zvichirwisa masero europi zvakare, uye izvi zvinokonzera kukanganisa kunounza zviratidzo.
Opsoclonus-myoclonus syndrome inowanikwa kakawanda muvana. Vana vaduku ndivo boka rezera umo inonzi neuroblastoma inowanzowedzera; vanenge makumi mana muzana yevana ava vachakudziridza OMS. Chero mwana chero upi zvake ane OMS achaongororwa kuti aone kana iye kana ane chiremera, kunyange kana akarwara nehutachiwana hwehutachiona kubva kaviri kazhinji kacho kuenda pamwe chete.
Kurapa
Kunyanya kunetseka ne opsoclonus-myoclonus syndrome kunotanga kuongororwa uye kurapwa kuitira kuti kuve nokuregererwa kwemaurological uye kugadzirisa. Kana mwana ane opsoclonus-myoclonus syndrome uye ane chirwere, chirwere chacho chinowanzobviswa chirwere. Kazhinji, matumire ari mumatangiro ekutanga uye chemotherapy kana remishonga yehutachiona haifaniri.
Dzimwe nguva izvi zvinovandudza kana kubvisa zviratidzo. Muvanhu vakuru, kushambadzira kwepamuviri kazhinji hakubatsiri uye zviratidzo zvingatowedzera kuipa.
Mimwe mishonga inosanganisira:
- Adrenocorticotrophic hormone (ACTH) injections
- Intravenous immunoglobulins - kugadzirwa kwezvokutengesera kwezvirwere kubva kune vanopa ropa rakanaka
- Azathioprine (Imuran) - inoderedza hutachiona hwehutachiona, hunoita kuti zvishoma nezvishoma kugadzirwa kwezvirwere
- Nyuchi uye intravenous steroids, dzakadai sa prednisone, dexamethasone, uye hydrocortisone
- Chemotherapy yakadai se cyclophosphamide uye methotrexate, kune vana vane neuroblastoma
- Therapeutic apheresis - kuchinjana plasma yeropa
- Immunoadsorption - kuchenesa ma antibodies kubva muropa yakaedzwa kune vanhu vakuru neOMS.
Kurapa kunowanzoitwa pamwe chete kunowanzodiwa kuti urambe uchigadzirisa zviratidzo uye kuderedza dambudziko rekuora kwechirwere.
Prognosis
Vanhu vane mikana yakakura yekudzoka kune yakasununguka mushure mekurapa ndevaya vane zviratidzo zvinyoro. Vaya vane zviratidzo zvinorema zvinogona kuve nekugadzikana kwemafupa avo kushungurudza (myoclonus) asi vane dambudziko nekubatanidza. Zvimwe zvinetso zvinobva mukukuvara kweuropi, zvakadai sekudzidzira uye zvinetso zvehutano, kukanganisa-kukanganisa kusagadzikana kwehutano (ADHD) uye kusagadzikana-kusagadzikana kwepfungwa, kunogona kuitika, uye izvi zvinogona kudiwa zvirongwa zvavo.
Vana vane zvirwere zvakaoma zvikuru zveOMS vangave nekukuvara kwehupi zvekusingaperi izvo zvinogona kukonzera kukanganisa mumuviri nepfungwa.
Kuwanda
Opsoclonus-Myoclonus Syndrome haigoni kwazvo; Vanhu vanosvika mamiriyoni chete vanotenda kuti vane dambudziko munyika. Inowanzoonekwa muvana nevakuru, asi inogona kukanganisa vanhu vakuru zvakare. Inowanzoitika kazhinji pane vasikana kupfuura vakomana uye inowanzoongororwa pashure pemwedzi mitanhatu yemakore.
Sources:
Pranzatelli, M. "Vital Signs: Shamwari Inofisa." Discove r, 2000.
Pranzatelli, M. "Opsoclonus-Myoclonus Syndrome". National Organisation for Rare Disorders, 2016.