Inherited blood disorder inokonzera anemia uye kurwadziwa
Overview
Sickle-cell anemia inokonzerwa neropa redambudziko. Zviratidzo zvaro zvekare ndezvenguva refu (isingaperi) chirwere chemvura uye zvikamu zvekutambudzika. Mune chirwere, hemoglobin molecules mumasero matsvuku eropa, anotakura okisijeni mumuviri wose, haana kukwana. Aya maemorokisi asina kukwana anokonzera mamwe masero matsvuku eropa kuti achinje uye agadzire chimiro chekokwe. Aya masero eropa asina kufanana anokonzerwa nekushaya ropa nekurwadziwa.
Kuwanda
Sickle-cell anemia inowanzozivikanwa pakati pevanhu vane madzitateguru anobva kuSouth Sahara, nzvimbo dzeSpanish-inotaura nyika (South America, Cuba, neCentral America), Saudi Arabia, India, uye nyika dzeMediterranean dzakadai seTurkey, Sicily, Greece , uye Italy.
Pane imwe nguva yaifungidzirwa kuva chirwere chisinganzwisisiki , tsvakurudzo ikozvino inoratidza kuti muUnited States, chikwangwani-cell anemia inowanikwa munenge 1 muvana 500 veAfrica -America vana vanoberekwa uye mune 1 mumarudzi ose 900 eAmerican America vana vanozvarwa.
Vanenge mamiriyoni maviri veAmerica vane chirwere chisina kusimba chekukwezva-cell anemia asi ivo pachavo havana chirwere chacho. Zvisinei, kana vanhu vaviri vane chirwere chisina kukwana vachiroorwa, pane imwe mukana wechina kuti chero mwana wavo waanove aine chirwere-cell anemia.
Kuziva
Zvizhinji zvehurumende muUnited States vanoita kuongororwa kweropa nyore kune vose vacheche vanoberekwa kuti vaone chikoro-cell anemia. Kana chiratidzo chichiratidza kuti haemoglobin isiripo iripo, chiratidzo chechipiri cheropa chinoitwa kuti chisimbise kuongororwa.
Zviratidzo
- Marwadzo: Masero matsvuku eropa-akafanana akaomeswa anononoka uye anotambudza kudarika nemidziyo midzi yeropa mumuviri. Masero acho anonamatira, akabatana, uye anovhara kubuda kweropa. Kuvhara kure ropa kunokonzera marwadzo. Izvi zvinonzi chirwere-cell cell.
- Anemia: Masero matsvuku eropa ane mavara akafa nokukurumidza. Iko kusina masero matsvuku eropa kuti atakure okisijeni mumuviri wose. Chigumisiro ndechokuneta, kutadza, uye kupererwa kwekupema .
- Kukurira kuderera: Anemia inopedza kuwedzera kwekukura nokuti masero emumuviri haatore okisijeni yavanoda kuti akure. Vana nevakuru vane chirwere che-sickle-cell anemia vanowanzova nekuvaka kuduku kudarika vamwe vanhu vezera rimwechete.
- Dambudziko reziso : Ziso rinogona kukuvadzwa nekushayikwa kweokisijeni; zvinogona kunge zvakakomba zvakakwana kukonzera bofu.
- Zvirwere: Vanhu vane chirwere che-sickle-cell anemia vanowanzoomerwa nehutachiwana nekuda kwekukuvara kwemasimba avo ezvirwere kubva pachirwere.
- Stroke: Kana ropa richiyerera kune chikamu cheuropi rakadzivirirwa nemasero akarwara, chirwere chinogona kuitika.
- Acute chest syndrome: kurwadziwa kwepachifu uye fevri inokonzerwa ne-sickle-cell anemia inogona kuva chinetso chinouraya upenyu.
Kurapa
Nhamo kubva kune-sickle-cell anemia inobatwa nemarwadzo-kuuraya zvinodhaka uye inopisa mvura. Zvipingamupinyi zvizhinji zvinorapwa sezvinoitika. Anticancer drug hydroxyurea inogona kuderedza nguva inoshungurudza inorwarisa chikoro chemajeri uye yemapfupa akaoma chechifu.
Vana vaduku, kusvika kune makore mashanu, vanowanzopiwa penicillin muromo kaviri pazuva kuti vadzivirire pneumonia. Kuwedzerwa ropa kunogona kugadzirisa anemia, kubatsira kudzivirira maitiro, uye kubata chirwere chepleen. Iko kune, zvisinei, zvakakomba nemigumisiro yakakura yekuve nekuwedzerwa ropa.
Kuchengetwa kwechiremba kunokosha kune vanhu vane maronda-cell anemia.
Nekutarisira utano hwakanaka, vanhu vane chirwere vanogona kunge vane hutano hwakanaka uye vanogara mukati mavo makumi maviri nemazana uye mberi.
Kutsvakurudza
Kutsvakurudza kunoenderera mberi kutsvaka mishonga yekurapa sickle-cell anemia. Masayendisiti akagadzira ma laboratory maitiro ane chirwere-sechirwere chirwere chakafanana nevanhu kuitira kuti mushonga mutsva unogona kuongororwa. Boroora marora kupera rinogona kuporesa chirwere chacho, asi marrow anofanira kubva kune akaenzana akafananidza kupa hama, uye iyo nzira ine njodzi dzakawanda .
Kunobva:
"FAQs." 2007. American Sickle Cell Anemia Association. 27 Jul 2009.