Chirwere-sechirwere chirwere (SCD) inokonzerwa nehutachiwana hwemaemia apo masero matsvuku eropa anochinja kubva kumativi ose akaenzana (akafanana nehupi) maitiro kune imwe nguva yakareba yakafanana nekoko kana bhanana. Aya masero matsvuku eropa ane dambudziko ruchiyerera mumidziyo yeropa uye rinogona kubatwa. Mutumbi unoona masero matsvuku eropa seasina kujairika uye anoaparadza nokukurumidza kupfuura nguva dzose zvichikonzera kushaya ropa.
Mumwe Munhu Anowana Sei Dhiyabhorosi?
Kurwara-sechirwere chirwere chinotora nhaka, naizvozvo munhu anoberekwa nacho. Kuti munhu agare nhaka yeCSD, vabereki vose vanofanira kunge vane chirwere chekuita. Mune mhando dzakasiyana dzeSDD, mumwe mubereki ane chirwere chechiremba uye mumwe mubereki ane hemoglobin C mitiro kana beta thalassemia trait. Kana vabereki vose vane chirwere (kana chimwe chimiro), vane mukana wechina wekuva nemwana ane SCD. Iyi njodzi inoitika pese pamuviri.
Mhando dzeSickle-Cell Disease
Iyo iyo yakajairika yakawanda yekoko-sechirwere chirwere chinonzi hemoglobin SS. Mimwe mikuru mikuru ndeyi: hemoglobin SC, sickle beta zero thalassemia, uye sickle beta pamwe thalassemia. Hemoglobin SS uye sickle beta zero thalassemia ndiyo maitiro akaoma zvikuru ekurapa-cell uye dzimwe nguva anonzi sickle cell anemia. Hemoglobin SC chirwere inofungidzirwa kuti inonzwisisika uye inowanzo, sickle beta pamwe ne thalassemia ndiyo inonyanya kukurudzira yearele-cell.
Vanhu Vanozivikanwa Sei Nokurwara-Chirwere Chetachiona?
MuUnited States, vose vacheche vanoongororwa kuCSD mushure mekunge vaberekwa sechikamu chepurogiramu yekuongorora . Kana zvakaguma zvakanaka kune SCD, chiremba wevana kana mwana wechirwere chenguva yechipatara chinonyatsozivikanwa nemigumisiro kuitira kuti murwere aonekwe mune chikwereti chekliniki kliniki.
Munyika dzisingasviki kuongorora kuongororwa, vanhu vanowanzoongororwa vane SCD sevana pavanotanga kuona zviratidzo.
Zviratidzo zveSCD
Nokuti SCD chirwere chemasero matsvuku eropa muviri wose unogona kuchinjwa.
Marwadzo: Apo masero matsvuku eropa anorwara akabatwa muropa remudziyo, ropa harigoni kufamba kumativi eropa. Izvi zvinoguma nekushayikwa kweokisijeni kune ino uye kurwadziwa.
Zvirwere : Sezvo chirwere (nhengo mumuviri wechirwere chemuviri) hachina kushanda zvakanaka, vanhu vane chirwere chechiremba-chetachiona vari pangozi yekutapukirwa kwakanyanya kwebhakitiriya. Ichi ndicho chikonzero vana vaduku vane chirwere chechiremba-cell vanotora penicillin kaviri zuva rimwe nerimwe.
Sitiroko : Kana mirefu matsvuku eropa akabatwa mune muropa yeropa muuropi, chikamu cheuropi hachiwani okisijeni chinokonzera chirwere. Izvi zvinogona kuunza seshizha chemaziso, kusimba kwemaoko kana makumbo, kana kuoma nekutaura. Kurohwa kunogona kuitika kune vana vane chirwere-cell-cell uye yakafanana nevakuru vane chirwere, ichi ndicho chirwere chekurapa.
Kuneta (kana kukaneta): Nokuti vanhu vane chirwere-chetachiona vane chirwere chekushaya ropa, vangave vachinge vasisina simba kana kuti kuneta.
Zvipfeko : Apo masero matsvuku eropa anoputsika (anonzi hemolysis) mu sickle-cell chirwere, anosunungura bilirubin. Izvo zvinovaka zve bilirubin zvinogona kutungamirira kukurudzirwa kwemakumbo.
Priapism : Kana zvikwereti zvinorwara zvikabatwa mupenisi, izvi zvinoguma nekumwadza, kusingadikanwi kukwegura kunonzi priapism.
Kurapa kweSDD
Penicillin : Kaviri pazuva, penicillin inotangwa nguva pfupi mushure mekunge uongorororwa (kazhinji usati wapera mwedzi miviri). Kutora penicillin kaviri zuva rega rega kusvikira makore mashanu apupurirwa kuderedza dambudziko rekukuvara kwebhakitiriya.
Majekiseni : Mishonga inogonawo kuderedza njodzi yehutachiona hwehutachiona hwakanyanya.
Kuwedzerwa ropa : Kuwedzerwa ropa kunogona kushandiswa kurapa zvinetso zvakananga zvekwekwe-sechirwere chirwere sehosha yakaoma kana chirwere chemapfupa, chirwere chemapapu. Uyezve, varwere vane chirwere chechiremba-chetachiona vane chirwere chepachirwere kana vari pangozi yakakura yekurohwa ropa vanogamuchira kuwedzerwa ropa pamwedzi wegore negore kuti vadzivise mamwe matambudziko.
Hydroxyurea : Hydroxyurea ndiyo chete mishonga inogamuchirwa neDAA inobata chirwere-cell. Hydroxyurea yakaratidza kuti inoderedza kucherecheka kwehutano hwehutachiona uye zvinetso zve sickle-cell chirwere sekurwadziwa uye chirwere chepachifu chechipfuva.
Bhuna marora kuendeswa : Bone marrow kupemha ndiyo chete chirwere chegwerere-cell. Kubudirira kwakanakisisa kwechirapa ichi kunouya apo mumwe akafananidzwa mukoma wako anokwanisa kupa masero emadzimai.