Kennedy Disease

Zviratidzo uye Kurapa kweSBMA

Kennedy chirwere, chinonziwo spinal bulbar muscular atrophy kana SBMA, inokonzerwa neurological disorder. Chirwere cheKennedy chinokanganisa masero ehutano chaihwo anodzora misuli kufamba (kunyanya, motokari yemaputi neuroni), iyo inokonzerwa nekufamba kwemasimba akawanda emaoko nemakumbo. Icho chinokanganisawo mitsipa inodzora misoro yebhuru, iyo inodzora kufema, kumedza, uye kutaura.

Chirwere cheKennedy chinogonawo kutungamirira kune androgen (mashomoni evanhu) kusava nehanya kunokonzera mazamu akawedzerwa mumarume, kuderedza kubereka, uye testicular atrophy.

Kennedy chirwere chinokonzerwa nehutachiona hunokonzerwa ne X (vakadzi) chromosome. Sezvo varume vari chete vane X chromosome, ivo vanonyanya kunetseka nedambudziko. Madzimai, ane maviri e-chromosomes, anogona kutakura chirwere chisina kukwana pane imwe X chromosome, asi imwe chinyorwa chechi X chromosome inoderedza kana kuvanza zviratidzo zvechirwere. Kennedy chirwere inofungidzirwa kuitika kune 1 mu 40,000 vanhu pasi rose.

Zviratidzo zveKennedy Disease

Pavhareji, zviratidzo zvinotanga kune vanhu vane makore 40-60. Zviratidzo zvinouya zvishoma nezvishoma, uye zvinogona kusanganisira:

Kennedy chirwere chinogona kuva nemimwe migumisiro mumuviri, kusanganisira:

Kuongororwa kweChiitiko

Kune hutano hwakawanda hweeuromuscular ine zviratidzo zvakafanana neKennedy chirwere, saka kushaya mishonga kana kusazviongorora kungave kwakakurumbira.

Kakawanda, vanhu vane chirwere cheKennedy vanofungidzirwa nenzira isina kururama kuti vane amyotrophic lateral sclerosis (ALS, kana chirwere chaLou Gehrig). Zvisinei, ALS, pamwe nezvimwe zvinetso zvakafanana, hazvisanganisi matambudziko endocrine kana kurasikirwa kwekunzwa.

A genetic test inogona kusimbisa kana chirwere cheKennedy chiripo pane X chromosome. Kana kuenzaniswa kwemafuroki kwakanaka, hapana humwe huedzo hunofanira kuitika sekuongororwa hunoitwa kubva kumuviri wechipfuwo chete.

Kurapa kweSBMA

Chirwere cheKennedy kana kuti SBMA hachina kukanganisa kurarama kwehupenyu, saka kurapwa kunowedzera mukuchengetedza hutano hwemunhu hwakanaka muupenyu hwake hwose kuburikidza nedzimwe nzira dzinotevera dzehutano:

Aya maitiro ekurapa anokosha pakuchengetedza unyanzvi hwemunhu uye kugadzirisa kuenderera mberi kwechirwere chacho. Zvigadzirwa zvekugadzirisa zvakadai sekushandiswa kwezvikwata kana zvikwata zvemagetsi zvinogona kubatsira kuchengetedza kufamba uye kuzvimirira.

Genetic Counseling

Kennedy chirwere chinobatanidza neC (chikadzi) chromosome, saka kana mukadzi ari mutakuri wejini isina kukwana, vanakomana vake vane mukana we50% ane chirwere uye vanasikana vake vane mukana we50% wekutakura.

Vanababa havagoni kupfuura chirwere cheKennedy kuvana vavo. Asi vanasikana vavo, zvisinei, vachave vatakuri vejecha risina kukwana.

Sources:

Barkhaus, PE (2003). Kennedy chirwere.

Kennedy's Disease Association. "Chii Chinonzi Kennedy Disease?"