Ita Zano Rakanaka kune Hypertrophic Cardiomyopathy

Hypertrophic cardiomyopathy (HCM) imwe yemamiriro emwoyo inobatanidza nekufa kamwe kamwe mune vatambi vechidiki. Kutaura zvazviri, HCM ndechimwe chezvinhu zvinowanzojairika zvepabonde, zvinokanganisa mumwe kune vanhu 500. MuUnited States, HCM inokwana 36% yematambudziko anouraya kamwe-kamwe anowanikwa mumitambo miduku. Uyezve, inopfuura hafu yematambudziko akangoerekana aitwa neHCM inoitika muAfrica America.

Vanhu vane HCM kazhinji havasabvumirwi kubva kumabasa ose emitambo, kunyange zvazvo vakaderedzwa.

Chero ani ane HCM anofanira kuziva nezvekuda kwekufa kamwe kamwe, uye anofanira kuziva nezvesangano rinokurudzira nyanzvi dzinobvumirana zvinofanira kuteverwa nevanhu vane chirwere ichi.

Chii Chaizvoizvo Chirwere cheCardiomyopathy?

HCM chirwere chemwoyo chinoratidzirwa nekunyanya kusina kuchena kwemutsipa wemwoyo, chirwere chinonzi hypertrophy. Iyo hypertrophy inogona kukonzera matambudziko akawanda. Inobereka "kuoma" kwakanyanyisa mumhepo yakasara ye ventricle yemwoyo. Inogonawo kukonzera kudzivirira kunokonzerwa neropa kunopera mu ventricle kuruboshwe, zvichiita mamiriro akafanana neaortic stenosis . HCM inobatanidzawo nekusaita basa rema mitral valve .

Izvi zvikamu zveHCM zvinogona kutungamirira ku diastolic kudzvinyirira uye diastolic mwoyo kusakundikana , kana kuti kuwedzera kurwara kwemoyo uye zvimwe "zvinowanzo" zvakasiyana-siyana zvekushaya mwoyo .

Inogonawo kukonzera mitral kudzoka , iyo inogona kukonzera kana kuipa mwoyo kusakundikana.

Asi mhedzisiro inotyisa yeHCM ndeyokuti inogona kuita kuti mwoyo mushure uwedzere kuwedzera ventricular tachycardia uye ventricular fibrillation, arrhythmias inogona kubudisa kufa kamwe kamwe. Kunyange zvazvo aya arrhythmias angaitika panguva ipi zvayo, iyo inowanzoitika panguva dzekushanda nesimba.

Zvinosuruvarisa, rufu rwechimbichimbi runogona kunge rwuri kuratidzwa kwekutanga kweHCM, kunyanya mumitambo miduku. Nguva dzose kuongororwa neEECG , kana zviri nani zvakadaro, echocardiogram, inogona kuzarura dambudziko muvatambi vakawanda vasati vatarisa upenyu - asi kuongororwa kwemaitiro kwakamboonekwa mari inorambidzwa.

Kunyange zvakadaro, chero mutambi wechidiki uyo ane imwe nhengo yemhuri akafa kamwe, kana kuti ane nhoroondo yemhuri yeHCM, inofanira kuongororwa nekuda kwechiitiko ichi. Uye kana HCM ichionekwa, inofanira kutevera maitiro ekubvuma anokurudzirwa nevatambi vechidiki vane HCM.

Ndeapi Mazano Okugadzirisa Maitiro Kune Vechidiki Vechidiki NeHCM?

Maererano nesangano reBethesda re 366 reBhithesda reEgligility Recommendations yeVakwikwi Vakatambira neCardiovascular Abnormalities, vatambi vane HCM havafanirwi kupinda mumitambo yakakwikwidzana, pamwe chete nemitambo yakaderera (yakadai se bowling kana gorofu).

Vaya vane HCM vasati vari muboka rakarongeka asi vanoita zvemitambo nguva nenguva vanofanirwawo kudzivisa mitambo yakawanda yepamusoro-soro yakadai seHockey, basketball, uye singles tennis.

Mimwe yemitambo inosanganisira kusimba kwakanyanyisa, uye mitambo yakadzika-yakasimba, inogona kuwanika mukuenzanisa.

Izvi zvinosanganisira gorofu, kaviri tennis, kusvetuka uye kutamba.

Sources:

Maron, BJ, Ackerman, MJ, Nishimura, RA, et al. Task Force 4: HCM uye Dzimwe Cardiomyopathies, Mitral Valve Prolapse, Myocarditis, uye Marfan Syndrome. J Am Coll Cardiol 2005; 45: 1340.