Chirongwa cheHemoglobin uye Chine Chizvarwa Chekuedzwa Kuedzwa
Kunzwa mwana wako ane hemoglobin isina kukanganisa pachirwere chitsva chinogona kutyisa. Tora kufema kwakadzika uye ngatitorei zvakanyanya kuti zvinorevei iwe nemwana wako.
Kuonekwa patsva kwekuzvarwa patsva kwakavandudza upenyu hwevana vakawanda nekuratidza hupenyu hunotyisa zvirwere sevana vacheche kuitira kuti kurapwa kunogona kutangwa musati matambudziko.
Izvi zvave zvichibudirira kuburikidza nekuenderera mberi nekuvandudza kuongorora kuongorora kunosanganisira. Mukuwedzera pakucherechedza maitiro ekurapa anokosha, dzimwe nguva, izvi zvinongororwa zvinoratidza vana sevatakuri vemamiriro ezvinhu.
Kunyatsoenderana nezvinetso zveropa, kuonekwa patsva kunoshandiswa kureva vana vane sickle cell chirwere uye thalassemia (alpha uye beta). Iyi nharaunda yechinyorwa chitsva chingave chakanyorwa mahemoglobinopathies, zvinetso zve hemoglobin. Kuziva maitiro aya kunobvumira kutanga kutumirwa kune anonzi hematologist uye kukwanisa kutanga chirwere chinoponesa upenyu zvisati zvaitika. Kuedzwa kunoitwa, zvisinei, haisi yakananga kune zvinetso izvi chete.
Chii Chinonzi Hemoglobin?
Hemoglobin ipuroteni yakagara mukati memusero weropa tsvuku. Iyo hemoglobin inotakura oksijeni mune imwe tsvuku yeropa kusvika kumatumbu ose mumuviri. Kana pasina hemoglobin yakakwana iripo, iwe unonzi une hoemia . Kune maviri maitiro akawandisa ematambudziko e hemoglobin.
Hemoglobinopathies inokonzerwa nezvinokonzerwa nekushanduka kwemasimba mu hemoglobin. Chirwere chetachiona chirwere ndiyo inowanzozivikanwa nehemoglobinopathy. Kunewo thalassemia, zvinetso nekuda kwekusava nekushanda kwekubudisa hemoglobin. Idzi mbiri dzakanyanya pane idzi ndiAra thalassemia uye beta thalassemia .
Svondo Rakaberekwa Rinotaridzirei?
Nguva pfupi mushure mekuberekwa, vacheche vanofanira kuita mapoka maviri ehemoglobin, hemoglobin F (fetal) uye hemoglobin A (munhu mukuru).
Pakuberekwa, mutumbi unofanirwa kuve uchitora hemoglobin F kupfuura hemoglobin A. Pamusoro pechinyorwa chinoberekwa checheche asina hemoglobinopathy, chigumisiro chichaverenga FA inoratidza kuti izvi zviviri zvinonzi hemoglobins zvakaonekwa. Zvimwe zvinogadzirirwa kunze kweFA zvinonzi hazvisi zvisiri izvo asi hazvirevi kuti mwana wako ane hemoglobinopathy. Chirongwa chitsva chingazvarwa chinogonawo kuziva vatakuri vematambudziko aya, anonziwo mamiriro ezvinhu.
Ndezvipi Zviitiko Zvinobvira zveNewborn Screening?
Kune ronguva refu rungagona. Nyaya dzakanyanya kunyorwa dzakanyorwa pasi apa dzakakanganiswa ne hemoglobin.
Hemoglobin S (chirwere chinonzi hegoglobin)
- FAS inoratidzira chikwereti chekare.
- FS inoratidzira chirwere chechirwere chetachiona, kana hemoglobin SS kana sickle beta zero thalassemia.
- FSA inoratidzira sickle beta pamwe ne-thalassemia, iyo inowanzo yakaoma yevirle cell cell.
- FSC inoratidza rudzi rwe sickle cell chirwere chinonzi hemoglobin SC.
Hemoglobin C - Hemoglobin C inoita sokuti yakatanga kuWest Africa.
- FAC inoratidza hemoglobin C muitiro kana mutakuri.
- FC inoratidza chirwere cheHemoglobin CC kana hemoglobin C beta zero thalassemia. Izvi zvinowanzokonzera unyoro kusvika pakuenzanisa chirwere chemahyamu chinonyatsotsungirira.
- FCA inoratidza hemoglobin C beta pamwe thalassemia. Izvi zvinogona kukonzera chirwere chemafupa.
Hemoglobin E-Hemoglobin E inowanikwa muSoutheast Asia
- FAE inoratidza hemoglobin E trait kana carrier.
- FE inoratidza hemoglobin EE zvirwere kana hemoglobin E beta zero thalassemia. Hemoglobin EE yakanyanyisa uye haina zvishoma kudarika ropa rinopera. Masero matsvuku eropa mu hemoglobin EE maduku zvikuru (pasi-pasi MCV). Hemoglobin E beta zero thalassemia inogona kusiyanisa kubva pakuyerera kwemaanti kusvika pakuwedzerwa ropa. Nemhaka yekusiyana kukuru pakati pezvinetso zviviri izvi mwana wako angangoona nyanzvi yehutemikari kuti asarudze kuguma kutsvaga.
- HERE inoratidza hemoglobin E beta pamwe thalassemia. Izvi zvinogona kusiyana zvikuru. Mwana wako angangodaro akatumirwa kune hematologist kuti arambe achiita basa.
Mamwe mahemoglobin vari
- FAOther inoratidza chimiro chakasiyana-siyana che hemoglobin. Kune misiyamu inopfuura 1000 hemoglobin uye vashomanana vavo vanoita kuti pave nedambudziko. Zvizhinji zvezvo zvidiki zvishanduko zvisingagadziri basa re hemoglobin. Mamiriro ezvinhu aya, zvinowanzokurudzirwa kuti uwane mamwe mabhii emabasa mushure memazera matanhatu ekuberekwa kuti uone kana ichi chinokonzera hemoglobin chichava dambudziko. Hemoglobin variants dzinodanwa nezvenzvimbo yavakatanga kurondedzerwa. Mienzaniso inosanganisira hemoglobin Austin, hemoglobin New York, uye Philly hemoglobin.
Thalassemia
- F inongoratidzira kuvapo kwe beta thalassemia, zvichida zvikuru.
- FABarts kazhinji inoratidza chiito che alpha thalassemia, nyika inotakura. Vamwe vana vane alpha thalassemia trait havazozivikanwi pachirwere chitsva uye vanogona kuonekwa munguva pfupi muupenyu.
- FA + Barts yakakwirira inoratidza chirwere cheHemoglobin H, chimiro che alpha thalassemia.
Iri haisi rondedzero yakakwana sekunge kune dzakawanda zvinogoneka zvinowanikwa pakuzvarwa patsva kuongorora. Kana uine mibvunzo kana zvinetseka pamusoro peganda rechecheche rawakaberekwa, taura nevana vevana vako.