Dystonia inosanganisira kuvhiringidza kusingabvumirwi kwemisungo iyo inowanzoshanda pamwe nekubatana, kuitira kuti chikamu chemuviri chiitwe munzvimbo isina kujairika uye inowanzorwadza semugumisiro. Dystonia inogona kukanganisa chero chikamu chemuviri, uye inogona kukonzera kunyadziswa uye kusakwanisa kuita mabasa ezuva nezuva. Nenzira yakanaka, pane nzira dzakasiyana-siyana idzo dystonia inogona kuvandudzwa.
Physical and Occupational Therapy
Kuona mutachiona wepanyama kana webasa kunogona kubatsira vanhu vane dystonia kudzidza kushanda zvakakomberedza dambudziko ravo, kunyange zvazvo risingabatanidzi zvakananga dambudziko racho. Vanhu vazhinji vane dystonia vanoonawo kuti vanogona kubvisa zviratidzo zvavo kwekanguva nekubata chikamu chemuviri wavo neimwe nzira. Izvi zvinozivikanwa sevane simba, uye ndeimwe yezvinhu zvisingazivikanwi zve dystonia.
Oral Mishonga
Nhamo, vashoma mishonga inoshanda zvakakwana pakurapa dystonia. Kusiyana nemutemo uyu kunosanganisira kushandiswa kweBenadryl kubata chirwere chakakosha-induced dystonia uye kushandiswa kwedopamine kubata mamwe maitiro echizvarwa cheDystonia, seSegawa syndrome. Nokuda kwechikonzero ichi, vana vose kana vari kuyaruka vane dystonia vanofanira kupiwa muedzo we dopamine.
Artane (trihexyphenidyl) ndeimwe yemishonga inonyatsodzidza yeDystonia. Iyi mishonga inobva kumhuri ye anticholinergics.
Vachiri vaduku vanowanzobatsirwa zvikuru nemishonga iyi. Vakuru vangave vanonyanya kufunga nezvemigumisiro yeAnchocholinergics, kusanganisira muromo wakaoma, kuvhiringidzika, kushungurudzwa, kurangarirwa kwepfungwa nekufungidzira.
Benzodiazepines, kufanana nekolonazepam , inogonawo kushandiswa, kazhinji pamwe chete nemumwe mushonga pamwe chete.
Baclofen, musumbu unozorodza, kazhinji haisi kubatsira zvikuru mukurapa dystonia, asi inogona kubatsira mukurapa jem dystonia, kunyanya pakati pevana. Icho chinonyanya kukosha kwemishonga iyi sedation.
Dopamine-depleting agents vakaita se tetrabenazine ndiwo akanyatsopesana nekupa dopamine, asi inogonawo kuva nenzvimbo mukurapa dystonia. Zvimwe zvikanganiso zvinosanganisira kuora mwoyo uye dysphoria, pamwe neparinsinsonism. Kana iyi mishonga inoshandiswa, madhizi anofanira kungowedzerwa zvishoma nezvishoma.
Injected Mishonga
Muchikamu chikuru chinonzi dystonia chinokanganisa chikamu chimwechete chemuviri, majekiseni e-botulinum toxin angabatsira. Ichokwadi, mune mamwe marudzi eDystonia, akadai se blepharospasm (kunyanya kuisa maziso) uye cervical torticollis (neck dystonia), injulinum inxin injection inofanirwa kuve yeropa rekutanga. MuTatticollis, 70-90% yevarwere vakarondedzera vamwe kubatsirwa. Injection inodzokororwa masvondo gumi nemaviri kusvika ku16. Pasi purogiramu iyi yekurapa, migumisiro inogona kuramba yakasimba uye yakachengeteka kwemakore mazhinji.
Botulinum injections inoshanda nokuvhara kusunungurwa kweacetylcholine, neurotransmitter inoratidza pakati pechirwere chemitsipa nemisumbu. Izvo zvinotungamirira ku kuora simba kwemuviri. Zvimwe zvinokonzerwa nehutachiona hwepinyikisi inokonzera kusakwana zvakanyanya, izvo zvinogona kunyanya kunetseka kana kuvhara kumeso kwe blepharospasm, kana kuti kupoteredza mutsipa nehuro, sezvo izvi zvinogona kutungamirira kumedza zvinetso.
Ijojekiti inofanira kuve yakarongedzwa zvakajeka kuitira kuti iwedzere kubatsirwa apo ichideredza dambudziko remigumisiro.
Zvokuvhiya
Kana nzira dzokurapa dzisingakwanisi uye kana dystonia ichikuvadza zvechokwadi humwe hupenyu hwehumwe, zvingasarudzwa zvinogona kuonekwa.
Munguva yakapfuura, kurapwa uku kwakabatanidza nekuzvivhiringidza kuipa kwehutachiona hunobuda kubva muuropi kusvika kune hutachiona hwakavhiringidzika (zvichiita kuti kuderedza mitsipa uye kubvisa dystonia) kana kuti kubvisa chikamu cheropi. Iye zvino, vanhu vakawanda vanosarudza sarudzo isingagadziriswi mumamiriro ehupamhi hwekurovedza ( DBS ).
Uropi hwepfungwa hunokurudzira hwakawanda hunoratidzirwa kuratidzira kugadzirisa hutano hukuru hwedysonia.
Vanhu vanotambura nemhando iyi yedystonia vanowanzove vaduku, kusanganisira vana. Mhinduro kumunhu wakadzika kukurudzira zvinogona kusiyana zvakasiyana. Nenzira yakawanda, mhinduro yeDystonia kune DBS haina kutarisirwa kudarika kupindura kwechirwere chePasinson uye kudengenyeka kunokosha, uye kuvandudzwa kunongowanikwa mwedzi yakawanda mushure mekurapa.
Inenge mwedzi gumi nemaviri mushure meDBS, varwere vazhinji vane dystonia vanoratidzira kubudirira mukufambisa nevana makumi mashanu. Vana uye vanhu vane dystonia kwenguva shomanana vanowanzoita zviri nani kudarika zviyero. Sekondari dystonia haifaniri kupindura sezvinofanotaurwa nehupamhi hwepfungwa yekukurudzira. Saizvozvowo, kana dystonia yakatungamirira kugadziriro yakasarudzwa panzvimbo yekuchinja-chinja mune zvakasimba, dystonia haigoni kupindura kubhudzi hwepfungwa dzakadzika.
Sources:
Kathleen Poston, Hurongwa Hwenhengo Yowakasiyana-siyana Matambudziko, Continuum: Matambudziko Anokonzera Mubhuku 16, Nhamba 1, February 2010
Mustafa Saad Siddiqui, Ihstsham Ul Haq, Michael S Okun, Deep Brain Kukurudzirwa MuMatambudziko Matambudziko, Continuum: Kutambudza Kwemagwaro Mubhuku 16, Nhamba 1, February 2010