Dzidza Nezve ALD Treatment Yakafuridzirwa naLorenzo Odone
Lorenzo mafuta ndeyekurapa kwakagadzirwa nokuda kwehucheche hutachiona adrenoleukodystrophy (ALD) , isingawanzoitiki uye inowanzofa inouraya myelin disorder. Mumakore ose aya, kurapwa kwave kwakagamuchirwa zvikuru kuburikidza nekutsvakurudza kwezvesayenzi, Myelin Project, uye firimu re 1992, Lorenzo's Oil.
Kutanga kuAdrenoleukodystrophy (ALD)
Adrenoleukodystrophy (ALD) chirwere chinokonzerwa nehutachiona chinokonzera kuumbwa kwemafuro akareba-mafuta acids anoparadza myelin, chifukidzo chekudzivirira pamusoro peeuroni muuropi.
Pasina izvi zvidziviriro zvinodzivirira, zviratidzo zvinokanganisa upofu, matsi, kugunun'una, kurasikirwa kwemasimba, uye kukanganisa kwemaitiro kunogona kuitika.
Zviratidzo zve ALD zvinowanzoonekwa pakati pemakore mana uye gumi. Chirwere chacho chinokurumidza kukurumidza uye kazhinji chinouraya mukati memakore maviri kusvika mashanu echiratidzo chinotanga. Nemhaka yenzira iyo ALD inotora nhaka, kuburikidza ne X chromosome, mamiriro akaoma kwazvo emamiriro ezvinhu anokanganisa chete vakomana. Iyo adrenal gland inosanganiswawo, inozivikanwa seAjouterison's disease, mune 90-muzana yematambudziko.
Chii Chinonzi Lorenzo Mafuta?
Maererano neThe Myelin Project, Mafuta aLornzo anowanzobatanidzwa 4 kusvika ku 1 musanganiswa we erucic acid uye oleic acid, yakabviswa kubva mumafuta ekuputika uye maorivhi, zvichienderana. Mafuta ekurapa, kana akangotanga kuonekwa nevana vakomana neAIDS, kana vakomana vasati vasati varatidze zviratidzo, zvakaratidza kuderedza kuwanda kwemaketani akawanda kwenguva yakareba apo inonwa zuva rega rega, iyo inogona kuderedza kutanga kwechirwere.
Zvisinei, zvidzidzo hazvina kukwanisa kuratidza kuti mafuta anodzivisa kufambira mberi kwechirwere uye inozivikanwa kuti haigadziri kana kugadzirisa kukanganisa myelin. Mushonga wakanakisisa iye zvino unowanikwa kune ALD ndeyemapfupa ekucherwa kwemafuta paanenge achiri kuchinja. Zvisinei, kutapisa kwemapfupa emapfupa kune ngozi zvikuru kuvarwere vaduku nekuda kwezvipingamupinyi zvehutachiona uye kurambwa.
Mukomana Akafuridzira Murapa
Mushonga unonzi "Lorenzo mafuta" mushure meL Lorenzo Odone, mukomana ane ALD ane vabereki vake, Michaela naAugusto, vakaramba kubvuma kuti pakanga kusina kurapwa kweAlD uye kuti Lorenzo aizofa nokukurumidza pashure pokunge aongororwa muna 1984. Nokutsvakurudza kwakasimba uye kushivirira , Vabereki vaRennzo vakabatsira kutanga mafuta.
Mushure mokutora mafuta zuva roga roga kubva pakuchirwa kwacho, Lorenzo akazopedzisira apera maitiro echiremba kwemakore anodarika makumi maviri. Akafa zuva rimwe mushure mekuberekwa kwake kwemazuva makumi matatu kubva pamatambudziko echirwere. Nyaya yemhuri yakaratidzirwa mufirimu ye 1992, Lorenzo's Oil , yakasangana naSusan Sarandon naNick Nolte.
Kuwanikwa kwe Lorenzo's Oil
Lorenzo's oil ikozvino inongowanikwa kune varwere vari muUnited States avo vanyoresa kuchipatara chirongwa sezvo ichiri kuonekwa sechirwere chekuedza. Mafuta haana kubvumirwa neU.S. Food and Drug Administration (FDA) yekutsvaga. Izvozvo zvakati, dzimwe shandisheni inogona kuvhara mari yekuedza kurapwa. Mafuta anobatanidzwa pamwe chete neCroda International yeBritain uye SHS International. SHS International ndiyo inoparadzira munyika yose yemafuta.
Zvimwe Zvakasanganisira Zvokuverengera Zvimwe
Unoda kudzidza zvakawanda nezve ALD, Lorenzo Odone, nezvimwe zvisingawanzovhiringidzi zvemagenene?
Tsvaga mamwe magwaro apa:
- Zvimwe Nezve ALD naLornzo Odone
- Zvimwe Zvirwere Zvirwere Zvinobata Vanhu
Kunobva:
"Mazano Pamusoro peLornzo Mafuta." The Myelin Project. 13 Feb 2009