VATER Syndrome (dzimwe nguva inonzi VATER kana kuti VACTERL sangano ) isarudzo yezvakaberekwa zvirema zvinowanzoitika pamwechete. Mavambo muVATER syndrome anotarisa munzvimbo shanu dzakasiyana umo mwana angave asina kukanganisa:
- V ertebrae
- A nus
- T rachea
- E sophagus
- R enal (itsvo)
Ikoko kunogonawo kuva nemoyo uye mamiriro ezvinhu, izvo zvinoshandura zita racho kuACTERL
Mwana anoonekwa ane imwe yeva syndromes haazove nechinetso munzvimbo dzose, asi kubata kwekuremara kwekuberekwa kunosanganisira nzvimbo dzakawanda.
VATER Syndrome Inoziva
HERE haisi chirwere chinonzi discrete kana zvirwere, saka hapana kuongororwa kwechiremba kwakafanana nekuongorora ropa kunogona kuongorora dambudziko racho. Kuti zviwanikwe neVATER Syndrome, mwana anofanira kunge ane zvinenge zvitatu zvinetso zvinotsanangurwa pamusoro apa.
Kunyange zvazvo chirwere chisina kujairika (chinokonzera mumwe mu10 000 kusvika ku40 000 vana), zviratidzo zvinogona kusiyana zvakasiyana kubva kumwana mumwe kune mumwe. Chimwe chinhu chinokosha cheVATER ndechokuti hazviiti sekuti zvinokonzera kukura kwepfungwa. Nokudaro, kana mwana ane zviratidzo zvepanyama zveVATER pamwe nekugadzirisa uye / kana kugadzirisa matambudziko, VATER kuongorora hakufaniri kukodzera.
Zvinokonzera VATER Syndrome
Sezvo VATER isiri chirwere chaiye, inonzi "sangano rekusava nehanya kwekuremara kwekuberekwa." Mune mamwe mazwi, nheyo chaiyo yezvakaberekwa zvinokanganisa izvo zvingava chikamu cheVATER kana VACTERL hachizivikanwe kuti chinoshamwaridzana.
Pane kudaro, zvinowanzoitika pamwechete kakawanda kuti zvive zviratidzo zvisinganzwisisiki zvezviratidzo.
Hakuchina chikonzero chaicho chinozivikanwa, asi chiremera chegene chinotendwa chinobatanidzwa. Kutsvakurudza kunoratidza kuti mamwe mararamiro anogona kuitika munguva pfupi kubva pamuviri. Uyewo, vakadzi vane chirwere cheshuga vanoita sevanowanzova nevana vane VATER.
Kurapa kweVATER Syndrome
Apo vamwe vana vane VATER / VACTERL vanogona kuva nezvinetso zvakadai zvokuti vanokundikana kubudirira sevana, vazhinji vanokura uye vanorarama hupenyu hwakakwana.
Nzira yekurapa inoenderana zvachose pane zvinodiwa zvomwana mumwe nomumwe. Somuenzaniso, zvimwe zvisingakanganisi muzvikamu nemakumbo zvinogona kubudirira kurapwa nekuvhiyiwa. Vamwe vangadikanwa kupindira kwemishonga, chirwere chepanyama , chirongwa chebasa, uye zvakadaro.
Sezvo vana vane VATER vachikura uye vanotanga kuenda kuchikoro, vangave vane zvimwe zvinhu zvinobudirira kana zvepanyama zvinofanira kutaridzirwa. Semuenzaniso, vangave vachinetseka kufamba, vachishanda nesimba, kana kuti zvakanaka motokari.
Zvakakosha kuziva, zvisinei, kuti VATER haisi chirwere cheuropi. Vana vazhinji vane VATER vanofanira kukwanisa kutarisira zvidzidzo zvepfungwa uye zvigumo zvechikoro pasina dambudziko rakawanda.
Vabereki vevana vane VATER / VACTERL vangave vachida kukumbira mazano ekugadzirisa mazita avo pavanenge vachifunga kuti vanogona kuva nevana vakawanda. Chirwere chacho chinonzi genetic uye, saka, njodzi yako yokuva nemumwe mwana ane zvimwe zvakafanana kana zvakakonzerwa nehutachiona hwepabonde zvakakwirira.
VATER Syndrome Resources
Mukuwedzera pakubvunza chiremba wako mibvunzo, izvi zvigaro zvingabatsira mukuwedzera kunzwisisa chirwere.
- National Center ye Biotechnology Information
- Genetics Home Reference
Zvipatara zvakawanda zvevana munyika yose zvinoshanda pamishonga yeVATER. Vamwe vari nyanzvi pane imwe nzvimbo yechirwere ichi chakaoma zvikuru.
- Cincinnati Children's Hospital