Mhedziso yeHereditary Hemochromatosis
Hereditary hemochromatosis chirwere chemazwi kana chizvarwa, chinowanzonzi sesimbi inoperesa chirwere. Inokonzerwa nokuwedzerwa kwesimbi yakawandisa mumatumbo ako (kubva pakudya) zvichiita kuti dare richengetwe mumitumbi, sechiropa chako, mwoyo, uye pancreas.
Iwe unogona kushamisika kuziva kuti utachiona hunoshaya hunogona kukonzerwa nehutano hemochromatosis . Izvi ndezvokuti dare rinogona kuiswa muhuturo hwepituitary yako, zvichikonzera central hypothyroidism, kana kuti zvishoma, kazhinji, thyroid thyland, zvichikonzera primary hypothyroidism.
Ngatinyatsocherechedza hemochromatosis, kusanganisira kuti izvi zvinowanikwa sei maitiro ezviratidzo uye zvinorapwa.
Risk Factors
Kune huwandu hunokonzera njodzi dzekusimudza hemochromatosis. Sezvo hemochromatosis inoshandiswa pakugadzirisa zvinhu, iwe unoda mapepa maviri eine genetic mutation kuti uite.
Uyezve, kuva Caucasian yeNorthern Europe kubva kune imwe nharaunda. Mukuwedzera, kuva murume kunowedzera mikana yako yekukura hemochromatosis, sezvo vakadzi vanorasikirwa nesimbi kuburikidza nekuenda kumwedzi, saka vanovaka simbi shoma kudarika. Mungozi yomudzimai inokwira, zvisinei, mushure mokunge apera , kana asisati ava kuenda kumwedzi.
Zviratidzo uye Zviratidzo
Zviratidzo zve hemochromatosis hazviwanzokudziridza kusvika pakukwegura, uye zvichienderana nhengo dzipi dzinobatwa, munhu anogona kuva nezviratidzo zvakasiyana. Vanhu vazhinji, chaizvoizvo, vanoongororwa ne hemochromatosis (zvichibva pane zvakaitika mumhuri kana kuti kuongororwa ropa kweropa) vasati vatanga zviratidzo.
Zvakakoshawo kuziva kuti iron inoshandiswa inogona kuitika mukati memutezo pasina chero zviratidzo zvekliniki. Semuenzaniso, zvidzidzo zve autopsy zvakaratidza dhidhi inowanikwa muhutano hwetroroid yevanhu vose vane hemochromatosis; asi, vanhu vakawanda vane hemochromatosis havasi kukura zvikuru hypothyroidism (inokosha inofanira kuchengeta mupfungwa).
Kwose, kunyange zvakadaro, zviratidzo zvinowanzoonekwa uye zviratidzo zve hemochromatosis zvinosanganisira:
- Kuramba kuneta
- Arthritis-kufanana nemarwadzo muzvibatanidzwa, kunyanya, pakati nepakati neminwe
- Kuchinja kweganda reganda, tsvuku, sharon, grey, muorivhi
- Kushaya simba
- Mavanga emimba (kurudyi kubva kune chiropa chakawedzerwa)
- Yakawedzerwa ropa sutu
- Abnormal thyroid function tests
- Zvisina kukodzera chiropa chekuedza
- High mazinga esimbi muropa
Sezvo mamiriro acho ezvinhu achiitika, kana asina kusiya, munhu angakura:
- Chirwere cheshuga
- Chiropa kukuvara
- Heart damage
- Utachiona husingaiti
- Kutadza
- Kutadza kana kusina nguva nguva yekuenda kumwedzi
Kuongororwa uye Kuedzwa
Kana uri kuona zviratidzo zvesimbi zvakanyanyisa uye chiremba wako anoona hutano hwakareba muropa rako, anokwanisa kurayira kuongororwa ropa kune hemochromatosis gene.
Uyezve, maererano neNational Institute of Diabetes uye Digestive uye Kidney Diseases, zvinotevera zvinotungamirirwa nemitemo zvinofanira kuteverwa:
- Vanun'una vevanhu vane hemochromatosis vanofanira kuva neropa ravo rekuongorora mutemo weC282Y (hemochromatosis gene).
- Vabereki, vana, uye hama dzepedyo dzevanhu vane hemochromatosis vanofanira kufunga nezvekuedza.
- Vanachiremba vanofanira kuedza vanhu nehutano hwakasimba uye hunoramba huripo, chirwere chisina kutsanangurwa chechiropa, marwadzo akabatana, zvinetso zvemwoyo, erectile dysfunction, kana chirwere cheshuga.
Pakupedzisira, kunyatsojekesa utachiona-gland kubatanidzwa mu hemochromatosis, MRI yehutachiona yakagadzika inogona kuona huni inogadziriswa.
Kurapa
Hemochromatosis inorapwa kuburikidza ne "ropaletting" kana phlebotomy-chaizvoizvo, nzira iri nyore yekupa ropa. Chiremba wako achaita purogiramu yenguva dzose yephlebotomy, semushonga we hemochromatosis.
Shoko Rinobva
Hemochromatosis ndiyo inowanzosangana nehutachiona muUnited States, uye nhau dzakanaka ndeyokuti kuratidzwa kwayo kwakakomba, kufanana nechiropa, mwoyo, uye chirwere chetachiona, chinogona kudziviswa nekuchengetedzwa kwakakodzera.
Kana iwe uine mhuri yakagadzirwa nesimbi yakawandisa kana zviratidzo zvisingatsanangurwi, zvinonzwisisika kutaura nachiremba wako pamusoro pekuedzwa.
> Sources:
> Schrier SL, Bacon BR. (2018). Kupiriniki kwezviratidzo uye kuongororwa kwenhaka yehemochromatosis. Mu: UpToDate, Mentzer WC (Ed), UpToDate, Waltham, MA.
> Tamagno G, De Carlo E, Murialdo G, Scandellari C. Zvingave zvakabatana pakati pe genetic hemochromatosis uye autoimmune thyroiditis. Minerva Med . 2007 Dec; 98 (6): 769-72.